Q79.61 ICD-10-CM Code: Classical Ehlers-Danlos syndrome
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Inpatient Payment Groups (MS-DRG)
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0, Appendix B.
- MS-DRG 564 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC (MDC 08)
- MS-DRG 565 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC (MDC 08)
- MS-DRG 566 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC (MDC 08)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Official Registry Overview & Definition
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for Q79.61 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Classical EDS (cEDS)
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- congenital (sternomastoid) torticollis (Q68.0) Compare Q79.61 vs Q68.0 →
Change history
- FY2020 — 2019-10-01Added to the code setClassical Ehlers-Danlos syndromeFY2020 changes
Verify Before Coding
- Billable — reportable as written.
- CC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim.
Referenced by Other Codes
Clinical classification (AHRQ CCSR):MAL008 — Musculoskeletal congenital conditions (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Potential MS-DRG Relationships (FY2026)
CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 5 clinically related codes on its CMS exclusion list.
Named in the grouper logic of 3 MS-DRGs: DRG 564 (MDC 08), DRG 565 (MDC 08), DRG 566 (MDC 08).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Official ICD-10-CM tabular notes on other codes that name Q79.61 or its code family.
1 Excludes1 notes: Q82.8 (via Q79.6.-).
19 Excludes2 notes across 2 chapters: E70 (via Q79.6.-), E70-E88 (via Q79.6.-), E71 (via Q79.6.-), E72 (via Q79.6.-), E73 (via Q79.6.-), E74 (via Q79.6.-), E75 (via Q79.6.-), E76 (via Q79.6.-), E77 (via Q79.6.-), E78 (via Q79.6.-) and 9 more.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q79.61 in its code family, with their registry titles.
- Q79.5 — Other congenital malformations of abdominal wall
- Q79.51 — Congenital hernia of bladder
- Q79.59 — Other congenital malformations of abdominal wall
- Q79.6 — Ehlers-Danlos syndromes
- Q79.60 — Ehlers-Danlos syndrome, unspecified
- Q79.62 — Hypermobile Ehlers-Danlos syndrome
- Q79.63 — Vascular Ehlers-Danlos syndrome
- Q79.69 — Other Ehlers-Danlos syndromes
- Q79.8 — Other congenital malformations of musculoskeletal system
- Q79.9 — Congenital malformation of musculoskeletal system, unspecified
Indexed Clinical Terms (1)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Syndrome, Ehlers-Danlos, classical (cEDS) (classical EDS)