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Q79.61 ICD-10-CM Code: Classical Ehlers-Danlos syndrome

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
1 inclusion term · 1 Excludes2
Risk adjustment
RxHCC V08 category 84

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v44, Appendix B.

  • MS-DRG 564 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC (MDC 08)
  • MS-DRG 565 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC (MDC 08)
  • MS-DRG 566 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC (MDC 08)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q79.61 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2027Effective: October 1, 2026

Notes without a marker are published on Q79.61 itself; “inherited from” names the category or block whose note applies here.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Classical EDS (cEDS)

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

Source: inherited from Q79

Coder workflow for Q79.61

MedCoder structured workflow — derived from this code’s own official record

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).

Official instructions as workflow

  • Excludes2 — not part of Q79.61(1 note)

    Coding workflow: The conditions named in this note are not included in Q79.61. When the record documents both, both may be reported; the note is a boundary, not a prohibition.

    CompareQ68.0

    See the official tabular notes · Guidelines I.A.12.b

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Code Overview

Classical Ehlers-Danlos syndrome is a billable ICD-10-CM diagnosis code (Q79.61).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (1)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Verify Before Coding

  • CC as a secondary diagnosis (FY2027). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name Q79.61 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 2 Excludes1 notes across 2 chapters: M24.3 — Pathological dislocation of joint, not elsewhere classified (via Q79.-), Q82.8 — Other specified congenital malformations of skin (via Q79.6.-).

These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.

Referenced by 20 Excludes2 notes across 2 chapters: E70 — Disorders of aromatic amino-acid metabolism (via Q79.6.-), E70-E88 — Metabolic disorders (E70-E88) (via Q79.6.-), E71 — Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism (via Q79.6.-), E72 — Other disorders of amino-acid metabolism (via Q79.6.-), E73 — Lactose intolerance (via Q79.6.-), E74 — Other disorders of carbohydrate metabolism (via Q79.6.-), E75 — Disorders of sphingolipid metabolism and other lipid storage disorders (via Q79.6.-), E76 — Disorders of glycosaminoglycan metabolism (via Q79.6.-), E77 — Disorders of glycoprotein metabolism (via Q79.6.-), E78 — Disorders of lipoprotein metabolism and other lipidemias (via Q79.6.-), E79 — Disorders of purine and pyrimidine metabolism (via Q79.6.-), E80 — Disorders of porphyrin and bilirubin metabolism (via Q79.6.-), E83 — Disorders of mineral metabolism (via Q79.6.-), E84 — Cystic fibrosis (via Q79.6.-), E85 — Amyloidosis (via Q79.6.-), E86 — Volume depletion (via Q79.6.-), E87 — Other disorders of fluid, electrolyte and acid-base balance (via Q79.6.-), E88 — Other and unspecified metabolic disorders (via Q79.6.-), M35.7 — Hypermobility syndrome (via Q79.6.-), M95 — Other acquired deformities of musculoskeletal system and connective tissue (via Q79.-).

These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.

MS-DRG Grouper Relationships (FY2027)

Potential MS-DRG participation — not a DRG assignment.

FY2027 MS-DRG: CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 5 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 3 MS-DRGs: DRG 564 (MDC 08), DRG 565 (MDC 08), DRG 566 (MDC 08).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MAL008 — Musculoskeletal congenital conditions (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical process (MS-DRG)

Acts as CC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

Q79.60 — Ehlers-Danlos syndrome, unspecified, Q79.62 — Hypermobile Ehlers-Danlos syndrome, Q79.63 — Vascular Ehlers-Danlos syndrome, Q79.69 — Other Ehlers-Danlos syndromes

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Musculoskeletal congenital conditions).

Q78.3 — Progressive diaphyseal dysplasia, Q78.4 — Enchondromatosis, Q78.5 — Metaphyseal dysplasia, Q78.6 — Multiple congenital exostoses, Q78.8 — Other specified osteochondrodysplasias, Q78.9 — Osteochondrodysplasia, unspecified, Q79.0 — Congenital diaphragmatic hernia, Q79.1 — Other congenital malformations of diaphragm, Q79.2 — Exomphalos, Q79.3 — Gastroschisis, Q79.4 — Prune belly syndrome, Q79.51 — Congenital hernia of bladder, Q79.59 — Other congenital malformations of abdominal wall, Q79.6 — Ehlers-Danlos syndromes, Q79.60 — Ehlers-Danlos syndrome, unspecified, Q79.62 — Hypermobile Ehlers-Danlos syndrome, Q79.63 — Vascular Ehlers-Danlos syndrome, Q79.69 — Other Ehlers-Danlos syndromes, Q79.8 — Other congenital malformations of musculoskeletal system, Q79.9 — Congenital malformation of musculoskeletal system, unspecified, +245 more

Contextual Map

Every relationship of Q79.61 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run Q79.61 with these 10 related codes in Claim Check

Hierarchy

Referenced by Excludes1 notes

Referenced by Excludes2 notes (20)

Clinical classification (CCSR)

MS-DRG Grouper

MDC crossing

  • MDC 08 — Diseases and Disorders of the Musculoskeletal System and Connective Tissue[MDC crossing]: “Diseases and Disorders of the Musculoskeletal System and Connective Tissue — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 18,439 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2027

Index entries

  • Syndrome, Ehlers-Danlos, classical (cEDS) (classical EDS)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026

Nearest codes (16)

Change history

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v44 Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "Q79.61 — Classical Ehlers-Danlos syndrome." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/q79.61-classical-ehlers-danlos-syndrome

Change history

  • FY2020 — October 1, 2019
    Added to the code set
    Classical Ehlers-Danlos syndrome
    FY2020 changes

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q79.61 in its code family, with their registry titles.

View all codes in the Q79 family