Q79.4 ICD-10-CM Code: Prune belly syndrome

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q79.4 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on Q79.4 itself; “inherited from” names the category or block whose note applies here.

Coder workflow for Q79.4

MedCoder structured workflow — derived from this code’s own official record

Documentation check

The provider’s diagnostic statement

Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).

Official instructions as workflow

• Excludes2 — not part of Q79.4(1 note)

  Coding workflow: The conditions named in this note are not included in Q79.4. When the record documents both, both may be reported; the note is a boundary, not a prohibition.

  CompareQ68.0

  See the official tabular notes · Guidelines I.A.12.b

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Indexed Clinical Terms (8)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

• Abdomen, abdominal, muscle deficiency syndrome
• Aplasia, abdominal muscle syndrome
• Deficiency, deficient, abdominal muscle syndrome
• Prolapse, prolapsed, bladder (mucosa) (sphincter) (acquired), congenital
• Prune belly (syndrome)
• Syndrome, abdominal, muscle deficiency
• Syndrome, Eagle-Barrett
• Syndrome, prune belly

Don’t confuse Q79.4 with…

MedCoder analysis — pairs from this code’s official notes, distinctions written by MedCoder

The codes most likely to be picked instead of Q79.4 — named in its own official notes, or sharing its laterality or encounter family — with what separates them and which documentation moves the case. Each links to the full comparison.

• Q79.9— Specificity relationship (Review)

  Overlapping diagnoses in the same category.

  Overlapping codes in the same category — the documentation decides which is the more specific fit.

  What moves you there: A record that documents no more than “Congenital malformation of musculoskeletal system, unspecified” takes Q79.9; specificity in the record moves it back here.

  Full comparison: Q79.4 vs Q79.9 →

• Q68.0— Excludes2 relationship (Informational)

  Distinct conditions — both may be reported.

  A distinct condition — both may be reported when both are documented.

  What moves you there: Documentation of congenital (sternomastoid) torticollis adds Q68.0; it is not part of this code and both may be reported when both are documented.

  Full comparison: Q79.4 vs Q68.0 →

Relationships are read from this code's own official notes, its laterality siblings and its encounter family; the wording of each distinction is MedCoder editorial, and the documentation named in each “what moves you there” line is the official note phrase or sibling title itself. Source: CMS ICD-10-CM tabular instructional notes; ICD-10-CM Official Guidelines, Section I.A.12.a.

Verify Before Coding

• MCC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name Q79.4 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 2 Excludes1 notes across 2 chapters: M24.3 — Pathological dislocation of joint, not elsewhere classified (via Q79.-), Q64.7 — Other and unspecified congenital malformations of bladder and urethra.

These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.

Referenced by 1 Excludes2 note: M95 — Other acquired deformities of musculoskeletal system and connective tissue (via Q79.-).

These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: MCC — Major Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 5 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 3 MS-DRGs: DRG 393 (MDC 06), DRG 394 (MDC 06), DRG 395 (MDC 06).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MAL008 — Musculoskeletal congenital conditions (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical process (MS-DRG)

Acts as MCC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

Q79.2 — Exomphalos, Q79.3 — Gastroschisis, Q79.51 — Congenital hernia of bladder, Q79.59 — Other congenital malformations of abdominal wall

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Musculoskeletal congenital conditions).

Q78.3 — Progressive diaphyseal dysplasia, Q78.4 — Enchondromatosis, Q78.5 — Metaphyseal dysplasia, Q78.6 — Multiple congenital exostoses, Q78.8 — Other specified osteochondrodysplasias, Q78.9 — Osteochondrodysplasia, unspecified, Q79.0 — Congenital diaphragmatic hernia, Q79.1 — Other congenital malformations of diaphragm, Q79.2 — Exomphalos, Q79.3 — Gastroschisis, Q79.51 — Congenital hernia of bladder, Q79.59 — Other congenital malformations of abdominal wall, Q79.6 — Ehlers-Danlos syndromes, Q79.60 — Ehlers-Danlos syndrome, unspecified, Q79.61 — Classical Ehlers-Danlos syndrome, Q79.62 — Hypermobile Ehlers-Danlos syndrome, Q79.63 — Vascular Ehlers-Danlos syndrome, Q79.69 — Other Ehlers-Danlos syndromes, Q79.8 — Other congenital malformations of musculoskeletal system, Q79.9 — Congenital malformation of musculoskeletal system, unspecified, +245 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Aplasia”, “Deficiency, deficient”, “Abdomen, abdominal”, …; these codes share that main term but sit in a different category of the Tabular List.

Q51.828 — Other congenital malformations of cervix (cervix, cervical, congenital), Q52.8 — Other specified congenital malformations of female genitalia (round ligament), Q55.0 — Absence and aplasia of testis (testicle), Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate (prostate), Q55.5 — Congenital absence and aplasia of penis (penis), Q63.2 — Ectopic kidney (kidney, congenital), Q64.4 — Malformation of urachus (urachus, congenital), Q64.71 — Congenital prolapse of urethra (urethra, congenital), Q64.72 — Congenital prolapse of urinary meatus (urinary meatus, congenital), Q73.8 — Other reduction defects of unspecified limb(s) (limb), Q75.009 — Craniosynostosis, unspecified (craniofacial axis), Q78.8 — Other specified osteochondrodysplasias (short stature homeobox gene, with, dyschondrosteosis), Q84.8 — Other specified congenital malformations of integument (skin), Q89.01 — Asplenia (congenital) (spleen), Q96.9 — Turner's syndrome, unspecified (short stature homeobox gene, with, Turner's syndrome), QA0.0131 — SLC6A1-related disorder (GABA transporter 1), R10.0 — Acute abdomen (acute), R34 — Anuria and oliguria (secretion, urine), T85.398 — Other mechanical complication of other ocular prosthetic devices, implants and grafts (eye implant), T85.49 — Other mechanical complication of breast prosthesis and implant (breast implant), +249 more

Contextual Map

Every relationship of Q79.4 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run Q79.4 with these 3 related codes in Claim Check

Hierarchy

• Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q65-Q79 — Congenital malformations and deformations of the musculoskeletal system[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026

Referenced by Excludes1 notes

• M24.3 — Pathological dislocation of joint, not elsewhere classified[Excludes1](via Q79.-): “congenital dislocation or displacement of joint- see congenital malformations and deformations of the musculoskeletal system (Q65-Q79)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
• Q64.7 — Other and unspecified congenital malformations of bladder and urethra[Excludes1]: “congenital prolapse of bladder (mucosa) (Q79.4)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026

Referenced by Excludes2 notes

• M95 — Other acquired deformities of musculoskeletal system and connective tissue[Excludes2](via Q79.-): “congenital malformations and deformations of the musculoskeletal system (Q65-Q79)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026

Clinical classification (CCSR)

• MAL008 — Musculoskeletal congenital conditions[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)

MS-DRG Grouper

• MCC — Major Complication or Comorbidity [MS-DRG severity]: “As a secondary diagnosis this code can raise the stay's MS-DRG severity tier (MCC).”— CMS MS-DRG Definitions Manual (Appendix C) · FY2026
• DRG 393 — OTHER DIGESTIVE SYSTEM DIAGNOSES WITH MCC[MS-DRG]: “OTHER DIGESTIVE SYSTEM DIAGNOSES WITH MCC (MDC 06)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
• DRG 394 — OTHER DIGESTIVE SYSTEM DIAGNOSES WITH CC[MS-DRG]: “OTHER DIGESTIVE SYSTEM DIAGNOSES WITH CC (MDC 06)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
• DRG 395 — OTHER DIGESTIVE SYSTEM DIAGNOSES WITHOUT CC/MCC[MS-DRG]: “OTHER DIGESTIVE SYSTEM DIAGNOSES WITHOUT CC/MCC (MDC 06)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026

MDC crossing

• MDC 06 — Diseases and Disorders of the Digestive System[MDC crossing]: “Diseases and Disorders of the Digestive System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 5,744 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries

• Abdomen, abdominal, muscle deficiency syndrome[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Aplasia, abdominal muscle syndrome[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Deficiency, deficient, abdominal muscle syndrome[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Prolapse, prolapsed, bladder (mucosa) (sphincter) (acquired), congenital[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Prune belly (syndrome)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Syndrome, abdominal, muscle deficiency[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Syndrome, Eagle-Barrett[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Syndrome, prune belly[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026

Nearest codes (16)

• Q79 — Congenital malformations of musculoskeletal system, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q79.0 — Congenital diaphragmatic hernia[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q79.1 — Other congenital malformations of diaphragm[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q79.2 — Exomphalos[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q79.3 — Gastroschisis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q79.5 — Other congenital malformations of abdominal wall[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q79.51 — Congenital hernia of bladder[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q79.59 — Other congenital malformations of abdominal wall[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• and 8 more

Change history

• FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data

CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page

Claim edits Official source data

CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page

Inpatient payment groups Official source data

CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page

Change history and date-of-service validity Official source data

CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page

Comparisons, relationships and the contextual map MedCoder structured relationship

Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears

Summary and FAQ answers MedCoder explanation

Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q79.4 in its code family, with their registry titles.

• Q79 — Congenital malformations of musculoskeletal system, not elsewhere classified
• Q79.0 — Congenital diaphragmatic hernia
• Q79.1 — Other congenital malformations of diaphragm
• Q79.2 — Exomphalos
• Q79.3 — Gastroschisis
• Q79.5 — Other congenital malformations of abdominal wall
• Q79.51 — Congenital hernia of bladder
• Q79.59 — Other congenital malformations of abdominal wall
• Q79.6 — Ehlers-Danlos syndromes
• Q79.60 — Ehlers-Danlos syndrome, unspecified

View all codes in the Q79 family