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Q64.4 ICD-10-CM Code: Malformation of urachus

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
3 inclusion terms

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.

  • MS-DRG 698 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH MCC (MDC 11)
  • MS-DRG 699 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH CC (MDC 11)
  • MS-DRG 700 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITHOUT CC/MCC (MDC 11)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q64.4 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Cyst of urachus
  • Patent urachus
  • Prolapse of urachus

Code Overview

Malformation of urachus is a billable ICD-10-CM diagnosis code (Q64.4).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (13)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Verify Before Coding

  • No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.

Named in the grouper logic of 3 MS-DRGs: DRG 698 (MDC 11), DRG 699 (MDC 11), DRG 700 (MDC 11).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MAL003 — Genitourinary congenital anomalies (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Genitourinary congenital anomalies).

Q64.0 — Epispadias, Q64.10 — Exstrophy of urinary bladder, unspecified, Q64.11 — Supravesical fissure of urinary bladder, Q64.12 — Cloacal exstrophy of urinary bladder, Q64.19 — Other exstrophy of urinary bladder, Q64.2 — Congenital posterior urethral valves, Q64.31 — Congenital bladder neck obstruction, Q64.32 — Congenital stricture of urethra, Q64.33 — Congenital stricture of urinary meatus, Q64.39 — Other atresia and stenosis of urethra and bladder neck, Q64.5 — Congenital absence of bladder and urethra, Q64.6 — Congenital diverticulum of bladder, Q64.70 — Unspecified congenital malformation of bladder and urethra, Q64.71 — Congenital prolapse of urethra, Q64.72 — Congenital prolapse of urinary meatus, Q64.73 — Congenital urethrorectal fistula, Q64.74 — Double urethra, Q64.75 — Double urinary meatus, Q64.79 — Other congenital malformations of bladder and urethra, Q64.8 — Other specified congenital malformations of urinary system, +137 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Deformity”, “Anomaly, anomalous”, “Prolapse, prolapsed”, …; these codes share that main term but sit in a different category of the Tabular List.

Q61.19 — Other polycystic kidney, infantile type (kidney, more than one, specified as polycystic, infantile type NEC), Q61.2 — Polycystic kidney, adult type (kidney, more than one, specified as polycystic, adult type), Q61.3 — Polycystic kidney, unspecified (kidney, more than one, specified as polycystic), Q62.31 — Congenital ureterocele, orthotopic (ureter, obstructive NEC, orthotopic ureterocele), Q62.32 — Cecoureterocele (ureter, obstructive NEC, cecoureterocele), Q62.39 — Other obstructive defects of renal pelvis and ureter (ureter, obstructive NEC), Q62.8 — Other congenital malformations of ureter (ureter), Q63.2 — Ectopic kidney (kidney, congenital), Q63.8 — Other specified congenital malformations of kidney (kidney, specified NEC), Q63.9 — Congenital malformation of kidney, unspecified (kidney), Q65.89 — Other specified congenital deformities of hip (rotation, hip, congenital), Q65.9 — Congenital deformity of hip, unspecified (hip, congenital), Q66.1 — Congenital talipes calcaneovarus (foot, cavovarus), Q66.3 — Other congenital varus deformities of feet (foot, varus NEC), Q66.6 — Other congenital valgus deformities of feet (foot, valgus), Q66.80 — Congenital vertical talus deformity, unspecified foot (vertical talus), Q66.81 — Congenital vertical talus deformity, right foot (vertical talus, right foot), Q66.82 — Congenital vertical talus deformity, left foot (vertical talus, left foot), Q66.89 — Other specified congenital deformities of feet (foot, congenital NOS, specified type NEC), Q66.9 — Congenital deformity of feet, unspecified (toe, congenital), +691 more

Contextual Map

Every relationship of Q64.4 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Hierarchy

Clinical classification (CCSR)

MS-DRG Grouper

MDC crossing

  • MDC 11 — Diseases and Disorders of the Kidney and Urinary Tract[MDC crossing]: “Diseases and Disorders of the Kidney and Urinary Tract — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 3,574 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries (13)

  • Anomaly, anomalous (congenital) (unspecified type), urachus[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Cyst (colloid) (mucous) (simple) (retention), allantoic[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Cyst (colloid) (mucous) (simple) (retention), urachus, congenital[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Deformity, urachus, congenital[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Deformity, urinary tract (congenital), urachus[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Fistula (cutaneous), urachus, congenital[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Patent, urachus[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Persistence, persistent (congenital), umbilical sinus[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • and 5 more

Nearest codes (25)

Change history

  • FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "Q64.4 — Malformation of urachus." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/q64.4-malformation-of-urachus

Change history

  • FY2016 — October 1, 2015
    In the code set at ICD-10-CM adoption
    Malformation of urachus

No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027 (effective October 1, 2026), and none are recorded for this code. Note changes are tracked from FY2027 only.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q64.4 in its code family, with their registry titles.

View all codes in the Q64 family