Q64.2 ICD-10-CM Code: Congenital posterior urethral valves
Compare with another codeCheck this code on a claim
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Billable · FY2027A valid, specific ICD-10-CM code, reportable for dates of service in FY2027.
What you need to know
Source: CMS/NCHS Official ICD-10-CM tabular notes, quoted. From the CMS/NCHS tabular list for the release in force. A note the category or block publishes applies to this code too; the Instructions section marks which is which.
The tabular list publishes no instructional note for this code itself.
Inpatient Payment Groups (MS-DRG)
Potential MS-DRG participation — not a DRG assignment.
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v44, Appendix B.
- MS-DRG 698 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH MCC (MDC 11)
- MS-DRG 699 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH CC (MDC 11)
- MS-DRG 700 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITHOUT CC/MCC (MDC 11)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Coding context
Guidelines, coding notes, decision aids, relationships (with MS-DRG and CCSR classification), hierarchy, HCC, coverage and the context map: what a coder reaches for after the core. Each section names whether it is official source data, a MedCoder-derived relationship or MedCoder editorial.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Verify Before Coding
- CC as a secondary diagnosis (FY2027). Can raise the stay's MS-DRG severity tier.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder-derived relationships — computed from published CMS and AHRQ datasets
MS-DRG Grouper Relationships (FY2027)
Potential MS-DRG participation — not a DRG assignment.
FY2027 MS-DRG: CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 8 clinically related codes on its CMS exclusion list.
Named in the grouper logic of 3 MS-DRGs: DRG 698 (MDC 11), DRG 699 (MDC 11), DRG 700 (MDC 11).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Clinical classification (AHRQ CCSR):MAL003 — Genitourinary congenital anomalies (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same clinical process (MS-DRG)
Acts as CC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.
N13.9 — Obstructive and reflux uropathy, unspecified, Q64.31 — Congenital bladder neck obstruction, Q64.32 — Congenital stricture of urethra, Q64.33 — Congenital stricture of urinary meatus, Q64.39 — Other atresia and stenosis of urethra and bladder neck, Q64.8 — Other specified congenital malformations of urinary system, Q64.9 — Congenital malformation of urinary system, unspecified
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Genitourinary congenital anomalies).
Q63.1 — Lobulated, fused and horseshoe kidney, Q63.2 — Ectopic kidney, Q63.3 — Hyperplastic and giant kidney, Q63.8 — Other specified congenital malformations of kidney, Q63.9 — Congenital malformation of kidney, unspecified, Q64.0 — Epispadias, Q64.10 — Exstrophy of urinary bladder, unspecified, Q64.11 — Supravesical fissure of urinary bladder, Q64.12 — Cloacal exstrophy of urinary bladder, Q64.19 — Other exstrophy of urinary bladder, Q64.31 — Congenital bladder neck obstruction, Q64.32 — Congenital stricture of urethra, Q64.33 — Congenital stricture of urinary meatus, Q64.39 — Other atresia and stenosis of urethra and bladder neck, Q64.4 — Malformation of urachus, Q64.5 — Congenital absence of bladder and urethra, Q64.6 — Congenital diverticulum of bladder, Q64.70 — Unspecified congenital malformation of bladder and urethra, Q64.71 — Congenital prolapse of urethra, Q64.72 — Congenital prolapse of urinary meatus, +137 more
Same Index main term, other category
The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Malformation”, “Valve, valvular”, “Stricture”; these codes share that main term but sit in a different category of the Tabular List.
Q62.4 — Agenesis of ureter (ureter, agenesis), Q62.5 — Duplication of ureter (ureter, duplication), Q62.7 — Congenital vesico-uretero-renal reflux (ureter, vesico-uretero-renal reflux), Q62.8 — Other congenital malformations of ureter (ureter), Q63.0 — Accessory kidney (kidney, accessory), Q63.1 — Lobulated, fused and horseshoe kidney (kidney, horseshoe), Q63.2 — Ectopic kidney (kidney, malposition), Q63.3 — Hyperplastic and giant kidney (kidney, giant), Q63.8 — Other specified congenital malformations of kidney (kidney, specified type NEC), Q63.9 — Congenital malformation of kidney, unspecified (kidney), Q74.2 — Other congenital malformations of lower limb(s), including pelvic girdle (joint, ankle), Q74.8 — Other specified congenital malformations of limb(s) (joint, specified type NEC), Q74.9 — Unspecified congenital malformation of limb(s) (joint), Q75.8 — Other specified congenital malformations of skull and face bones (bone, face, specified type NEC), Q75.9 — Congenital malformation of skull and face bones, unspecified (bone, face), Q76.49 — Other congenital malformations of spine, not associated with scoliosis (spine), Q76.9 — Congenital malformation of bony thorax, unspecified (thorax, bony), Q79.1 — Other congenital malformations of diaphragm (diaphragm), Q79.9 — Congenital malformation of musculoskeletal system, unspecified (bone), Q82.9 — Congenital malformation of skin, unspecified (skin), +288 more
Contextual Map
Every relationship of Q64.2 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Hierarchy
- Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q60-Q64 — Congenital malformations of the urinary system[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
Clinical classification (CCSR)
- MAL003 — Genitourinary congenital anomalies[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
MS-DRG Grouper
- CC — Complication or Comorbidity [MS-DRG severity]: “As a secondary diagnosis this code can raise the stay's MS-DRG severity tier (CC).”— CMS MS-DRG Definitions Manual (Appendix C) · FY2027
- DRG 698 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH MCC[MS-DRG]: “OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH MCC (MDC 11)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2027
- DRG 699 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH CC[MS-DRG]: “OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH CC (MDC 11)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2027
- DRG 700 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITHOUT CC/MCC[MS-DRG]: “OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITHOUT CC/MCC (MDC 11)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2027
MDC crossing
- MDC 11 — Diseases and Disorders of the Kidney and Urinary Tract[MDC crossing]: “Diseases and Disorders of the Kidney and Urinary Tract — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 3,578 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2027
Index entries
- Malformation (congenital), urethra, posterior valves[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
- Stricture, urethra (organic) (spasmodic), congenital, valvular (posterior)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
- Stricture, urethra (organic) (spasmodic), valvular, congenital (posterior)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
- Valve, valvular (formation), urethra (congenital) (posterior)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
Nearest codes (25)
- Q64 — Other congenital malformations of urinary system[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q64.0 — Epispadias[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q64.1 — Exstrophy of urinary bladder[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q64.10 — Exstrophy of urinary bladder, unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q64.11 — Supravesical fissure of urinary bladder[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q64.12 — Cloacal exstrophy of urinary bladder[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q64.19 — Other exstrophy of urinary bladder[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q64.3 — Other atresia and stenosis of urethra and bladder neck[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- and 17 more
Change history
- FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016
Reference
Index terms and tables, published questions and FAQ, every source behind this page with its release and checksum, the date-of-service check and the complete change history.
Indexed Clinical Terms (4)
Official source data — entries quoted as published, in the Index’s own lookup phrasing
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
- Inpatient payment groups Official source data
- CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v44 Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder-derived relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder editorial explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Current data releases:ICD-10-CM FY2027 · ICD-10-PCS FY2027 · HCPCS October 2026 · MS-DRG v44 · Medicare Code Editor v44.0 · NCCI PTP Q4 2026 · MUE Q4 2026 · NCD code lists 2026-01 · LCD export September 20, 2026 · All releases and sources
Labels on this page: Official source data · MedCoder-derived relationship · MedCoder editorial explanation. How to read the labels · All data sources and release dates · CMS coding rules
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "Q64.2 — Congenital posterior urethral valves." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/q64.2-congenital-posterior-urethral-valves
Change history
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionCongenital posterior urethral valves
No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027, and none are recorded for this code. Note changes are tracked from FY2027 only.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q64.2 in its code family, with their registry titles.
- Q64.1 — Exstrophy of urinary bladder
- Q64.10 — Exstrophy of urinary bladder, unspecified
- Q64.11 — Supravesical fissure of urinary bladder
- Q64.12 — Cloacal exstrophy of urinary bladder
- Q64.19 — Other exstrophy of urinary bladder
- Q64.3 — Other atresia and stenosis of urethra and bladder neck
- Q64.31 — Congenital bladder neck obstruction
- Q64.32 — Congenital stricture of urethra
- Q64.33 — Congenital stricture of urinary meatus
- Q64.39 — Other atresia and stenosis of urethra and bladder neck