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Compare/D84.1 vs L50

D84.1 vs L50

D84.1 (Defects in the complement system) compared with L50 (Urticaria), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.

Can these codes be reported together?

No — do not report together. L50 carries an Excludes1 note covering D84.1: “hereditary angio-edema (D84.1)”

Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Side by side

D84.1Defects in the complement systemL50Urticaria
Billing statusBillableNon-billable header

Report instead: L50.0, L50.1, L50.2, L50.3, L50.4

ClassificationD50-D89 — Diseases of the Blood and Blood-forming Organs and Certain Disorders Involving the Immune Mechanism (D50-D89)L00-L99 — Diseases of the Skin and Subcutaneous Tissue (L00-L99)
DefinitionDefects in the complement system is a billable ICD-10-CM diagnosis code (D84.1).Urticaria is a non-billable ICD-10-CM category code (L50).
Includes
defects in the complement system
immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
sarcoidosis
C1 esterase inhibitor [C1-INH] deficiency

Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources