E71.314 vs E71.42

Summary

What is different?

The conditions named.E71.314 is “Muscle carnitine palmitoyltransferase deficiency”; E71.42 is “Carnitine deficiency due to inborn errors of metabolism”.

Registry fact

Can these codes be reported together?

No.E71.42’s entry carries an Excludes1 note covering E71.314: “Muscle carnitine palmitoyltransferase deficiency (E71.314)”. Both may be reported only when the documentation shows the two conditions are unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Official ruleGuide: Excludes1 vs Excludes2

Is there an Excludes1 relationship?

Yes.E71.42’s tabular entry: “Muscle carnitine palmitoyltransferase deficiency (E71.314)”. The note covers E71.314.

Official ruleGuide: Excludes1 vs Excludes2

Is there an Excludes2 relationship?

Yes.E71.314’s tabular entry: “carnitine deficiency due to inborn error of metabolism (E71.42)”. The note covers E71.42.

Official ruleGuide: Excludes1 vs Excludes2

Official rule: a tabular instructional note or a section of the ICD-10-CM Official Guidelines, quoted as published. Registry fact: the codes’ own published attributes (titles, billable status, position in the hierarchy, code set). MedCoder-derived: a reading MedCoder computes from those facts; it is not itself a rule. How to read the labels

Can these codes be reported together?

Official guidance behind these answers

• Section I.A.12.a — Excludes1 · applies to: Excludes1

  A type 1 Excludes note is a pure excludes note. It means “NOT CODED HERE!” An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition. An exception to the Excludes1 definition is the circumstance when the two conditions are unrelated to each other. If it is not clear whether the two conditions involving an Excludes1 note are related or not, query the provider. For example, code F45.8, Other somatoform disorders, has an Excludes1 note for "sleep related teeth grinding (G47.63)," because "teeth grinding" is an inclusion term under F45.8. Only one of these two codes should be assigned for teeth grinding. However psychogenic dysmenorrhea is also an inclusion term under F45.8, and a patient could have both this condition and sleep related teeth grinding. In this case, the two conditions are clearly unrelated to each other, and so it would be appropriate to report F45.8 and G47.63 together.

  ICD-10-CM Official Guidelines FY2027

• Section I.A.12.b — Excludes2 · applies to: Excludes2

  A type 2 Excludes note represents “Not included here.” An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

  ICD-10-CM Official Guidelines FY2027

Quoted from the ICD-10-CM Official Guidelines for Coding and Reporting in effect for the release shown. The tabular notes above are the code-level instruction; these sections are the convention that says how such a note is applied. Source document (CMS PDF) · Release and checksum

Side by side

Similar descriptions do not make codes interchangeable. The documentation and the official instructions decide which code applies.

No Code first, Use additional code, Includes and 7th character note at either code.

Notes are the code’s own tabular entry, quoted as published. A note that names the other code is the one the verdict above rests on. In a row that differs, each code’s own notes are listed under it, and the notes every code shares are listed once beneath them.