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Clinical Concepts/MAL003

Genitourinary congenital anomalies

CCSR category MAL003 · 158 ICD-10-CM codes

Code Families in This Category

  • Q64 Other congenital malformations of urinary system · 22
  • Q52 Other congenital malformations of female genitalia · 20
  • Q51 Congenital malformations of uterus and cervix · 19
  • Q55 Other congenital malformations of male genital organs · 18
  • Q62 Congenital obstructive defects of renal pelvis and congenital malformations of ureter · 17
  • Q53 Undescended and ectopic testicle · 16
  • Q61 Cystic kidney disease · 11
  • Q50 Congenital malformations of ovaries, fallopian tubes and broad ligaments · 10
  • Q54 Hypospadias · 7
  • Q60 Renal agenesis and other reduction defects of kidney · 7
  • Q63 Other congenital malformations of kidney · 6
  • Q56 Indeterminate sex and pseudohermaphroditism · 5

ICD-10-CM Codes in This Category (first 100 of 158)

  • Q50.01 — Congenital absence of ovary, unilateral
  • Q50.02 — Congenital absence of ovary, bilateral
  • Q50.1 — Developmental ovarian cyst
  • Q50.2 — Congenital torsion of ovary
  • Q50.31 — Accessory ovary
  • Q50.32 — Ovarian streak
  • Q50.39 — Other congenital malformation of ovary
  • Q50.4 — Embryonic cyst of fallopian tube
  • Q50.5 — Embryonic cyst of broad ligament
  • Q50.6 — Other congenital malformations of fallopian tube and broad ligament
  • Q51.0 — Agenesis and aplasia of uterus
  • Q51.10 — Doubling of uterus with doubling of cervix and vagina without obstruction
  • Q51.11 — Doubling of uterus with doubling of cervix and vagina with obstruction
  • Q51.2 — Other doubling of uterus
  • Q51.21 — Complete doubling of uterus
  • Q51.22 — Partial doubling of uterus
  • Q51.28 — Other and unspecified doubling of uterus
  • Q51.3 — Bicornate uterus
  • Q51.4 — Unicornate uterus
  • Q51.5 — Agenesis and aplasia of cervix
  • Q51.6 — Embryonic cyst of cervix
  • Q51.7 — Congenital fistulae between uterus and digestive and urinary tracts
  • Q51.810 — Arcuate uterus
  • Q51.811 — Hypoplasia of uterus
  • Q51.818 — Other congenital malformations of uterus
  • Q51.820 — Cervical duplication
  • Q51.821 — Hypoplasia of cervix
  • Q51.828 — Other congenital malformations of cervix
  • Q51.9 — Congenital malformation of uterus and cervix, unspecified
  • Q52.0 — Congenital absence of vagina
  • Q52.10 — Doubling of vagina, unspecified
  • Q52.11 — Transverse vaginal septum
  • Q52.12 — Longitudinal vaginal septum
  • Q52.120 — Longitudinal vaginal septum, nonobstructing
  • Q52.121 — Longitudinal vaginal septum, obstructing, right side
  • Q52.122 — Longitudinal vaginal septum, obstructing, left side
  • Q52.123 — Longitudinal vaginal septum, microperforate, right side
  • Q52.124 — Longitudinal vaginal septum, microperforate, left side
  • Q52.129 — Other and unspecified longitudinal vaginal septum
  • Q52.2 — Congenital rectovaginal fistula
  • Q52.3 — Imperforate hymen
  • Q52.4 — Other congenital malformations of vagina
  • Q52.5 — Fusion of labia
  • Q52.6 — Congenital malformation of clitoris
  • Q52.70 — Unspecified congenital malformations of vulva
  • Q52.71 — Congenital absence of vulva
  • Q52.79 — Other congenital malformations of vulva
  • Q52.8 — Other specified congenital malformations of female genitalia
  • Q52.9 — Congenital malformation of female genitalia, unspecified
  • Q53.00 — Ectopic testis, unspecified
  • Q53.01 — Ectopic testis, unilateral
  • Q53.02 — Ectopic testes, bilateral
  • Q53.10 — Unspecified undescended testicle, unilateral
  • Q53.11 — Abdominal testis, unilateral
  • Q53.111 — Unilateral intraabdominal testis
  • Q53.112 — Unilateral inguinal testis
  • Q53.12 — Ectopic perineal testis, unilateral
  • Q53.13 — Unilateral high scrotal testis
  • Q53.20 — Undescended testicle, unspecified, bilateral
  • Q53.21 — Abdominal testis, bilateral
  • Q53.211 — Bilateral intraabdominal testes
  • Q53.212 — Bilateral inguinal testes
  • Q53.22 — Ectopic perineal testis, bilateral
  • Q53.23 — Bilateral high scrotal testes
  • Q53.9 — Undescended testicle, unspecified
  • Q54.0 — Hypospadias, balanic
  • Q54.1 — Hypospadias, penile
  • Q54.2 — Hypospadias, penoscrotal
  • Q54.3 — Hypospadias, perineal
  • Q54.4 — Congenital chordee
  • Q54.8 — Other hypospadias
  • Q54.9 — Hypospadias, unspecified
  • Q55.0 — Absence and aplasia of testis
  • Q55.1 — Hypoplasia of testis and scrotum
  • Q55.20 — Unspecified congenital malformations of testis and scrotum
  • Q55.21 — Polyorchism
  • Q55.22 — Retractile testis
  • Q55.23 — Scrotal transposition
  • Q55.29 — Other congenital malformations of testis and scrotum
  • Q55.3 — Atresia of vas deferens
  • Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • Q55.5 — Congenital absence and aplasia of penis
  • Q55.61 — Curvature of penis (lateral)
  • Q55.62 — Hypoplasia of penis
  • Q55.63 — Congenital torsion of penis
  • Q55.64 — Hidden penis
  • Q55.69 — Other congenital malformation of penis
  • Q55.7 — Congenital vasocutaneous fistula
  • Q55.8 — Other specified congenital malformations of male genital organs
  • Q55.9 — Congenital malformation of male genital organ, unspecified
  • Q56.0 — Hermaphroditism, not elsewhere classified
  • Q56.1 — Male pseudohermaphroditism, not elsewhere classified
  • Q56.2 — Female pseudohermaphroditism, not elsewhere classified
  • Q56.3 — Pseudohermaphroditism, unspecified
  • Q56.4 — Indeterminate sex, unspecified
  • Q60.0 — Renal agenesis, unilateral
  • Q60.1 — Renal agenesis, bilateral
  • Q60.2 — Renal agenesis, unspecified
  • Q60.3 — Renal hypoplasia, unilateral
  • Q60.4 — Renal hypoplasia, bilateral

The remaining 58 codes are reachable through the code families above.

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, Rockville, MD. All data sources.