Q56.3 ICD-10-CM Code: Pseudohermaphroditism, unspecified
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Coding at a Glance
- Tabular directives
- 7 Excludes1
Inpatient Payment Groups (MS-DRG)
Potential MS-DRG participation — not a DRG assignment.
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.
- MS-DRG 729 — OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITH CC/MCC (MDC 12)
- MS-DRG 730 — OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITHOUT CC/MCC (MDC 12)
- MS-DRG 742 — UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITH CC/MCC (MDC 13)
- MS-DRG 743 — UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITHOUT CC/MCC (MDC 13)
- MS-DRG 760 — MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITH CC/MCC (MDC 13)
- MS-DRG 761 — MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITHOUT CC/MCC (MDC 13)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q56.3 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025
Notes without a marker are published on Q56.3 itself; “inherited from” names the category or block whose note applies here.
Excludes1 — Not Coded Here
Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
- 46,XX true hermaphrodite (Q99.1) inherited from Q56Compare Q56.3 vs Q99.1 →
- androgen insensitivity syndrome (E34.5-) inherited from Q50-Q56Compare Q56.3 vs E34.5 →
- chimera 46,XX/46,XY true hermaphrodite (Q99.0) inherited from Q56Compare Q56.3 vs Q99.0 →
- female pseudohermaphroditism with adrenocortical disorder (E25.-) inherited from Q56Compare Q56.3 vs E25 →
- pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99) inherited from Q56Compare Q56.3 vs Q96 →
- pure gonadal dysgenesis (Q99.1) inherited from Q56Compare Q56.3 vs Q99.1 →
- syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99) inherited from Q50-Q56Compare Q56.3 vs Q90 →
Coder workflow for Q56.3
MedCoder structured workflow — derived from this code’s own official record
Before you code Q56.3
- Unspecified does not mean incorrect. When the record gives no greater specificity, Q56.3 may be the appropriate code. Check the record for detail that supports a more specific sibling. An unspecified code is for records that do not provide the detail a more specific code needs; a query, not an assumption, is the route to specificity (Guidelines I.A.9.b, I.B.18).
See the relationships section · Guide: Other vs unspecified (NEC vs NOS) →
- Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with Q56.3. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).
Choose the right path
- Does the record document the detail a more specific sibling code needs?
Yes → Review the specific siblings in this subcategory.
No → Continue — Q56.3 is appropriate when the documentation goes no further. - Does the documentation support a condition named in Q56.3’s Excludes1 note?
Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
No → Continue.
Consider Q56.3. Then confirm the code is valid for the date of service in the Verify section.
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
- Any detail beyond this code’s title
- What the record states that a more specific sibling code would capture — or its absence, which itself supports the unspecified code.
Official instructions as workflow
Excludes1 — check before selecting Q56.3(7 notes)
Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with Q56.3: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.
CompareQ99.1, E34.5, Q99.0, E25
See the official tabular notes · Guidelines I.A.12.a
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: The provider documents the condition in the terms of this code’s title and records no further detail.
Coding question: Is a more specific sibling code supportable?
Path: Review the specific siblings in this subcategory and what each requires the record to state.
Reason: A more specific code needs documentation of the distinguishing element; without it the unspecified code is appropriate, and a provider query is the route to specificity (Guidelines I.A.9.b, I.B.18).
Documentation: Both the condition Q56.3 describes and a condition named in its Excludes1 note are documented for the same encounter.
Coding question: Can both codes be reported?
Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.
Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Indexed Clinical Terms (1)
Official source data — entries quoted as published, in the Index’s own lookup phrasing
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.
Verify Before Coding
- No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder structured relationships — computed from published CMS and AHRQ datasets
MS-DRG Grouper Relationships (FY2026)
Potential MS-DRG participation — not a DRG assignment.
FY2026 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.
Named in the grouper logic of 6 MS-DRGs: DRG 729 (MDC 12), DRG 730 (MDC 12), DRG 742 (MDC 13), DRG 743 (MDC 13), DRG 760 (MDC 13), DRG 761 (MDC 13).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Clinical classification (AHRQ CCSR):MAL003 — Genitourinary congenital anomalies (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Genitourinary congenital anomalies).
Q55.62 — Hypoplasia of penis, Q55.63 — Congenital torsion of penis, Q55.64 — Hidden penis, Q55.69 — Other congenital malformation of penis, Q55.7 — Congenital vasocutaneous fistula, Q55.8 — Other specified congenital malformations of male genital organs, Q55.9 — Congenital malformation of male genital organ, unspecified, Q56.0 — Hermaphroditism, not elsewhere classified, Q56.1 — Male pseudohermaphroditism, not elsewhere classified, Q56.2 — Female pseudohermaphroditism, not elsewhere classified, Q56.4 — Indeterminate sex, unspecified, Q60.0 — Renal agenesis, unilateral, Q60.1 — Renal agenesis, bilateral, Q60.2 — Renal agenesis, unspecified, Q60.3 — Renal hypoplasia, unilateral, Q60.4 — Renal hypoplasia, bilateral, Q60.5 — Renal hypoplasia, unspecified, Q60.6 — Potter's syndrome, Q61.00 — Congenital renal cyst, unspecified, Q61.01 — Congenital single renal cyst, +137 more
Same Index main term, other category
The ICD-10-CM Index to Diseases and Injuries files this code under the main term “Pseudohermaphroditism”; these codes share that main term but sit in a different category of the Tabular List.
E25.0 — Congenital adrenogenital disorders associated with enzyme deficiency (female, adrenal), E25.8 — Other adrenogenital disorders (adrenal), E29.1 — Testicular hypofunction (male, with, 5-alpha-reductase deficiency), E34.51 — Complete androgen insensitivity syndrome (male, with, feminizing testis)
Contextual Map
Every relationship of Q56.3 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Hierarchy
- Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q50-Q56 — Congenital malformations of genital organs[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Clinical classification (CCSR)
- MAL003 — Genitourinary congenital anomalies[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
MS-DRG Grouper
- DRG 729 — OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITH CC/MCC[MS-DRG]: “OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITH CC/MCC (MDC 12)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 730 — OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITHOUT CC/MCC[MS-DRG]: “OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITHOUT CC/MCC (MDC 12)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 742 — UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITH CC/MCC[MS-DRG]: “UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITH CC/MCC (MDC 13)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 743 — UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITHOUT CC/MCC[MS-DRG]: “UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITHOUT CC/MCC (MDC 13)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 760 — MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITH CC/MCC[MS-DRG]: “MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITH CC/MCC (MDC 13)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 761 — MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITHOUT CC/MCC[MS-DRG]: “MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITHOUT CC/MCC (MDC 13)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
MDC crossing
- MDC 12 — Diseases and Disorders of the Male Reproductive System[MDC crossing]: “Diseases and Disorders of the Male Reproductive System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 1,964 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026
- MDC 13 — Diseases and Disorders of the Female Reproductive System[MDC crossing]: “Diseases and Disorders of the Female Reproductive System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 2,232 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026
Index entries
- Pseudohermaphroditism[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
Nearest codes
- Q56 — Indeterminate sex and pseudohermaphroditism[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q56.0 — Hermaphroditism, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q56.1 — Male pseudohermaphroditism, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q56.2 — Female pseudohermaphroditism, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q56.4 — Indeterminate sex, unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Change history
- FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
- Inpatient payment groups Official source data
- CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder structured relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "Q56.3 — Pseudohermaphroditism, unspecified." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/q56.3-pseudohermaphroditism-unspecified
Change history
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionPseudohermaphroditism, unspecified
No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027 (effective October 1, 2026), and none are recorded for this code. Note changes are tracked from FY2027 only.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q56.3 in its code family, with their registry titles.