Skip to main content

D47.02 ICD-10-CM Code: Systemic mastocytosis

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
4 inclusion terms · 6 Excludes1 · 10 code-also instructions
Risk adjustment
RxHCC V08 category 21

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.

  • MS-DRG 820 — LYMPHOMA AND LEUKEMIA WITH MAJOR O.R. PROCEDURES WITH MCC (MDC 17)
  • MS-DRG 821 — LYMPHOMA AND LEUKEMIA WITH MAJOR O.R. PROCEDURES WITH CC (MDC 17)
  • MS-DRG 822 — LYMPHOMA AND LEUKEMIA WITH MAJOR O.R. PROCEDURES WITHOUT CC/MCC (MDC 17)
  • MS-DRG 823 — LYMPHOMA AND NON-ACUTE LEUKEMIA WITH OTHER PROCEDURES WITH MCC (MDC 17)
  • MS-DRG 824 — LYMPHOMA AND NON-ACUTE LEUKEMIA WITH OTHER PROCEDURES WITH CC (MDC 17)
  • MS-DRG 825 — LYMPHOMA AND NON-ACUTE LEUKEMIA WITH OTHER PROCEDURES WITHOUT CC/MCC (MDC 17)
  • MS-DRG 840 — LYMPHOMA AND NON-ACUTE LEUKEMIA WITH MCC (MDC 17)
  • MS-DRG 841 — LYMPHOMA AND NON-ACUTE LEUKEMIA WITH CC (MDC 17)
  • MS-DRG 842 — LYMPHOMA AND NON-ACUTE LEUKEMIA WITHOUT CC/MCC (MDC 17)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for D47.02 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on D47.02 itself; “inherited from” names the category or block whose note applies here.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Indolent systemic mastocytosis
  • Isolated bone marrow mastocytosis
  • Smoldering systemic mastocytosis
  • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)

Excludes1 — Not Coded Here

Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Code Also

Additional codes that may be required to fully describe the encounter.

  • Code also, if applicable, any associated hematological non-mast cell lineage disease, such as:
  • acute myeloid leukemia (C92.6-, C92.A-)
  • chronic myelomonocytic leukemia (C93.1-)
  • essential thrombocytosis (D47.3)
  • hypereosinophilic syndrome (D72.1)
  • myelodysplastic syndrome (D46.9)
  • myeloproliferative syndrome (D47.1)
  • non-Hodgkin lymphoma (C82-C85)
  • plasma cell myeloma (C90.0-)
  • polycythemia vera (D45)

Coder workflow for D47.02

MedCoder structured workflow — derived from this code’s own official record

Before you code D47.02

  1. Confirm the documented site and behavior (this code’s block classifies uncertain behavior neoplasms), whether the site is primary or secondary, and whether the malignancy is current or a personal history: a previously excised malignancy with no further treatment and no evidence of disease is history, not current disease. Verify the site against the Table of Neoplasms. Neoplasm chapter guidelines (Guidelines I.C.2.a, I.C.2.d, I.C.2.m).

    See the Table of Neoplasms entries · Guide: Active cancer vs history of cancer →

  2. Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with D47.02. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).

    See the official tabular notes

Choose the right path

  1. Does the documentation support a condition named in D47.02’s Excludes1 note?
    Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
    No → Continue.

    ReviewC96.21, C94.3, Q82.2, D47.Z9, C96.2, D49

Consider D47.02. Then review the Code Also note, and confirm the code is valid for the date of service in the Verify section.

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
Anatomical site
At the most specific level the record states; a site the classification separates cannot be assumed from a procedure or a measurement.
Behavior and current-versus-history status
Malignant, in situ, benign or uncertain; primary or secondary; current disease or personal history (Guidelines I.C.2.m).

Official instructions as workflow

  • Excludes1 — check before selecting D47.02(6 notes)

    Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with D47.02: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.

    CompareC96.21, C94.3, Q82.2, D47.Z9, C96.2, D49

    See the official tabular notes · Guidelines I.A.12.a

  • Code Also — related condition(10 notes)

    Coding workflow: Review the related condition when both are documented and the instruction applies. A Code Also note does not fix sequencing; the order follows the circumstances of the encounter.

    ReviewC92.6, C92.A, C93.1, D47.3, D72.1, D46.9

    See the official tabular notes · Guidelines I.A.17

Coding decision scenarios

Pattern scenarios for this code’s structure — decision rules, not clinical cases

Documentation: Both the condition D47.02 describes and a condition named in its Excludes1 note are documented for the same encounter.

Coding question: Can both codes be reported?

Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.

Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).

ReviewC96.21, C94.3, Q82.2, D47.Z9, C96.2, D49

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Code Overview

Systemic mastocytosis is a billable ICD-10-CM diagnosis code (D47.02).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (5)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Verify Before Coding

  • CC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name D47.02 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 3 Excludes1 notes across 3 chapters: C96.2 — Malignant mast cell neoplasm, D89.4 — Mast cell activation syndrome and related disorders, Q82.2 — Congenital cutaneous mastocytosis.

These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 27 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 9 MS-DRGs: DRG 820 (MDC 17), DRG 821 (MDC 17), DRG 822 (MDC 17), DRG 823 (MDC 17), DRG 824 (MDC 17), DRG 825 (MDC 17), DRG 840 (MDC 17), DRG 841 (MDC 17), DRG 842 (MDC 17).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):NEO072 — Neoplasms of unspecified nature or uncertain behavior (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical process (MS-DRG)

Acts as CC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

D45 — Polycythemia vera, D46.0 — Refractory anemia without ring sideroblasts, so stated, D46.1 — Refractory anemia with ring sideroblasts, D46.20 — Refractory anemia with excess of blasts, unspecified, D46.21 — Refractory anemia with excess of blasts 1, D46.22 — Refractory anemia with excess of blasts 2, D46.4 — Refractory anemia, unspecified, D46.9 — Myelodysplastic syndrome, unspecified, D46.A — Refractory cytopenia with multilineage dysplasia, D46.B — Refractory cytopenia with multilineage dysplasia and ring sideroblasts, D46.C — Myelodysplastic syndrome with isolated del(5q) chromosomal abnormality, D46.Z — Other myelodysplastic syndromes, D47.01 — Cutaneous mastocytosis, D47.09 — Other mast cell neoplasms of uncertain behavior, D47.1 — Chronic myeloproliferative disease, D47.3 — Essential (hemorrhagic) thrombocythemia, D47.9 — Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified, D47.Z2 — Castleman disease, D47.Z9 — Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue, Z51.0 — Encounter for antineoplastic radiation therapy, +6 more

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Neoplasms of unspecified nature or uncertain behavior).

D44.2 — Neoplasm of uncertain behavior of parathyroid gland, D44.3 — Neoplasm of uncertain behavior of pituitary gland, D44.4 — Neoplasm of uncertain behavior of craniopharyngeal duct, D44.5 — Neoplasm of uncertain behavior of pineal gland, D44.6 — Neoplasm of uncertain behavior of carotid body, D44.7 — Neoplasm of uncertain behavior of aortic body and other paraganglia, D44.9 — Neoplasm of uncertain behavior of unspecified endocrine gland, D45 — Polycythemia vera, D47.0 — Mast cell neoplasms of uncertain behavior, D47.01 — Cutaneous mastocytosis, D47.09 — Other mast cell neoplasms of uncertain behavior, D47.1 — Chronic myeloproliferative disease, D47.2 — Monoclonal gammopathy, D47.3 — Essential (hemorrhagic) thrombocythemia, D47.4 — Osteomyelofibrosis, D47.9 — Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified, D47.Z1 — Post-transplant lymphoproliferative disorder (PTLD), D47.Z2 — Castleman disease, D47.Z9 — Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue, D48.0 — Neoplasm of uncertain behavior of bone and articular cartilage, +100 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Mastocytosis”, “Mast cell”; these codes share that main term but sit in a different category of the Tabular List.

C94.3 — Mast cell leukemia (leukemia), C96.20 — Malignant mast cell neoplasm, unspecified (neoplasm, malignant), C96.21 — Aggressive systemic mastocytosis (aggressive systemic), C96.22 — Mast cell sarcoma (sarcoma), C96.29 — Other malignant mast cell neoplasm (malignant), Q82.2 — Congenital cutaneous mastocytosis (cutaneous, congenital)

Lab tests where this diagnosis supports Medicare coverage (NCD)

Medicare's National Coverage Determination (NCD) program lists this diagnosis as medical justification for these lab tests.

Prothrombin Time Test and INR (PT/INR)

Contextual Map

Every relationship of D47.02 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run D47.02 with these 13 related codes in Claim Check

Hierarchy

Excludes1

Code Also (13)

Referenced by Excludes1 notes

Clinical classification (CCSR)

MS-DRG Grouper (9)

MDC crossing

  • MDC 17 — Myeloproliferative Diseases and Disorders, Poorly Differentiated Neoplasms[MDC crossing]: “Myeloproliferative Diseases and Disorders, Poorly Differentiated Neoplasms — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 4,730 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries

  • Disease, diseased, systemic tissue mast cell[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Mast cell, disease, systemic tissue[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Mastocytosis, indolent systemic[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Mastocytosis, isolated bone marrow[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Mastocytosis, systemic (indolent) (smoldering), with an associated hematological non-mast cell lineage disease (SM-AHNMD)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026

Nearest codes (13)

Change history

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "D47.02 — Systemic mastocytosis." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/d47.02-systemic-mastocytosis

Change history

  • FY2018 — October 1, 2017
    Added to the code set
    Systemic mastocytosis
    FY2018 changes

Nearest Codes in This Family

Official ICD-10-CM classifications closest to D47.02 in its code family, with their registry titles.

View all codes in the D47 family