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K00.0 ICD-10-CM Code: Anodontia

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
2 inclusion terms · 1 Excludes1 · 1 Excludes2

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.

  • MS-DRG 011 — TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITH MCC (MDC PRE)
  • MS-DRG 012 — TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITH CC (MDC PRE)
  • MS-DRG 013 — TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITHOUT CC/MCC (MDC PRE)
  • MS-DRG 157 — DENTAL AND ORAL DISEASES WITH MCC (MDC 03)
  • MS-DRG 158 — DENTAL AND ORAL DISEASES WITH CC (MDC 03)
  • MS-DRG 159 — DENTAL AND ORAL DISEASES WITHOUT CC/MCC (MDC 03)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for K00.0 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on K00.0 itself; “inherited from” names the category or block whose note applies here.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Hypodontia
  • Oligodontia

Excludes1 — Not Coded Here

Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

Source: inherited from K00

Coder workflow for K00.0

MedCoder structured workflow — derived from this code’s own official record

Before you code K00.0

  1. Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with K00.0. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).

    See the official tabular notes

Choose the right path

  1. Does the documentation support a condition named in K00.0’s Excludes1 note?
    Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
    No → Continue.

    ReviewK08.1

Consider K00.0. Then confirm the code is valid for the date of service in the Verify section.

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).

Official instructions as workflow

  • Excludes1 — check before selecting K00.0(1 note)

    Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with K00.0: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.

    CompareK08.1

    See the official tabular notes · Guidelines I.A.12.a

  • Excludes2 — not part of K00.0(1 note)

    Coding workflow: The conditions named in this note are not included in K00.0. When the record documents both, both may be reported; the note is a boundary, not a prohibition.

    CompareK01

    See the official tabular notes · Guidelines I.A.12.b

Coding decision scenarios

Pattern scenarios for this code’s structure — decision rules, not clinical cases

Documentation: Both the condition K00.0 describes and a condition named in its Excludes1 note are documented for the same encounter.

Coding question: Can both codes be reported?

Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.

Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).

ReviewK08.1

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Code Overview

Anodontia is a billable ICD-10-CM diagnosis code (K00.0).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (3)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Official Coding Guidelines

No excerpt in the ICD-10-CM Official Guidelines names this code specifically. Its chapter carries only this chapter-wide note:

Chapter 11: Diseases of the Digestive System (K00-K95)

Reserved for future guideline expansion

Verify Before Coding

  • No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name K00.0 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 2 Excludes1 notes: K08.1 — Complete loss of teeth, K08.4 — Partial loss of teeth.

These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.

Named in the grouper logic of 6 MS-DRGs: DRG 011 (MDC PRE), DRG 012 (MDC PRE), DRG 013 (MDC PRE), DRG 157 (MDC 03), DRG 158 (MDC 03), DRG 159 (MDC 03).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):DIG002 — Disorders of teeth and gingiva (default); DEN001 — Any dental condition including traumatic injury; DEN002 — Nontraumatic dental conditions.

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical categories (Disorders of teeth and gingiva, Any dental condition including traumatic injury, Nontraumatic dental conditions).

G11.5 — Hypomyelination - hypogonadotropic hypogonadism - hypodontia, K00.1 — Supernumerary teeth, K00.2 — Abnormalities of size and form of teeth, K00.3 — Mottled teeth, K00.4 — Disturbances in tooth formation, K00.5 — Hereditary disturbances in tooth structure, not elsewhere classified, K00.6 — Disturbances in tooth eruption, K00.7 — Teething syndrome, K00.8 — Other disorders of tooth development, K00.9 — Disorder of tooth development, unspecified, K01.0 — Embedded teeth, K01.1 — Impacted teeth, K02.3 — Arrested dental caries, K02.51 — Dental caries on pit and fissure surface limited to enamel, K02.52 — Dental caries on pit and fissure surface penetrating into dentin, K02.53 — Dental caries on pit and fissure surface penetrating into pulp, K02.61 — Dental caries on smooth surface limited to enamel, K02.62 — Dental caries on smooth surface penetrating into dentin, K02.63 — Dental caries on smooth surface penetrating into pulp, K02.7 — Dental root caries, +613 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Deficiency, deficient”, “Anodontia”, “Absence”; these codes share that main term but sit in a different category of the Tabular List.

H53.51 — Achromatopsia (color vision, achromatopsia), H53.52 — Acquired color vision deficiency (color vision, acquired), H53.53 — Deuteranomaly (color vision, deuteranomaly), H53.54 — Protanomaly (color vision, protanomaly), H53.55 — Tritanomaly (color vision, tritanomaly), H53.59 — Other color vision deficiencies (color vision, specified type NEC), H55.81 — Deficient saccadic eye movements (eye movements, saccadic), H55.82 — Deficient smooth pursuit eye movements (eye movements, smooth pursuit), H93.8 — Other specified disorders of ear (ear, congenital, acquired), I99.9 — Unspecified disorder of circulatory system (vascular), K06.8 — Other specified disorders of gingiva and edentulous alveolar ridge (vertical ridge), K08.10 — Complete loss of teeth, unspecified cause (acquired), K08.101 — Complete loss of teeth, unspecified cause, class I (teeth, tooth, acquired, class I), K08.102 — Complete loss of teeth, unspecified cause, class II (teeth, tooth, acquired, class II), K08.103 — Complete loss of teeth, unspecified cause, class III (teeth, tooth, acquired, class III), K08.104 — Complete loss of teeth, unspecified cause, class IV (teeth, tooth, acquired, class IV), K08.109 — Complete loss of teeth, unspecified cause, unspecified class (teeth, tooth, acquired), K08.111 — Complete loss of teeth due to trauma, class I (teeth, tooth, acquired, due to, trauma, class I), K08.112 — Complete loss of teeth due to trauma, class II (teeth, tooth, acquired, due to, trauma, class II), K08.113 — Complete loss of teeth due to trauma, class III (teeth, tooth, acquired, due to, trauma, class III), +375 more

Contextual Map

Every relationship of K00.0 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run K00.0 with these 2 related codes in Claim Check

Hierarchy

Excludes1

Referenced by Excludes1 notes

Clinical classification (CCSR)

MS-DRG Grouper

MDC crossing

  • Pre-MDC[MDC crossing]: “Pre-MDC — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 153 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026
  • MDC 03 — Diseases and Disorders of the Ear, Nose, Mouth and Throat[MDC crossing]: “Diseases and Disorders of the Ear, Nose, Mouth and Throat — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 5,147 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries

  • Absence (of) (organ or part) (complete or partial), teeth, tooth (congenital)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Anodontia (complete) (partial) (vera)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Deficiency, deficient, tooth bud[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026

Nearest codes (10)

Change history

  • FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
Coding guidelines Official source data
ICD-10-CM Official Guidelines for Coding and Reporting (FY2026), quoted by section Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "K00.0 — Anodontia." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/k00.0-anodontia

Change history

  • FY2016 — October 1, 2015
    In the code set at ICD-10-CM adoption
    Anodontia

No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027 (effective October 1, 2026), and none are recorded for this code. Note changes are tracked from FY2027 only.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to K00.0 in its code family, with their registry titles.

View all codes in the K00 family