K90.0 ICD-10-CM Code: Celiac disease
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Coding at a Glance
- Tabular directives
- 3 inclusion terms · 1 Excludes1 · 3 use-additional codes · 1 code-also instruction
- Risk adjustment
- RxHCC V08 category 66
Inpatient Payment Groups (MS-DRG)
Potential MS-DRG participation — not a DRG assignment.
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.
- MS-DRG 391 — ESOPHAGITIS, GASTROENTERITIS AND MISCELLANEOUS DIGESTIVE DISORDERS WITH MCC (MDC 06)
- MS-DRG 392 — ESOPHAGITIS, GASTROENTERITIS AND MISCELLANEOUS DIGESTIVE DISORDERS WITHOUT MCC (MDC 06)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for K90.0 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025
Notes without a marker are published on K90.0 itself; “inherited from” names the category or block whose note applies here.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Celiac disease with steatorrhea
- Celiac gluten-sensitive enteropathy
- Nontropical sprue
Excludes1 — Not Coded Here
Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
- intestinal malabsorption following gastrointestinal surgery (K91.2) Compare K90.0 vs K91.2 →
Source: inherited from K90
Code Also
Additional codes that may be required to fully describe the encounter.
- exocrine pancreatic insufficiency (K86.81)
Coder workflow for K90.0
MedCoder structured workflow — derived from this code’s own official record
Before you code K90.0
- Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with K90.0. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).
Choose the right path
- Does the documentation support a condition named in K90.0’s Excludes1 note?
Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
No → Continue.ReviewK91.2
Consider K90.0. Then work the Use Additional Code note and review the Code Also note, and confirm the code is valid for the date of service in the Verify section.
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
- The conditions the Use Additional Code note names
- Reported with this code when documented; a conditional instruction (“if applicable”, “if known”) applies only when the record supports it.
Official instructions as workflow
Excludes1 — check before selecting K90.0(1 note)
Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with K90.0: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.
CompareK91.2
See the official tabular notes · Guidelines I.A.12.a
Use Additional Code — after identifying K90.0(3 notes)
Coding workflow: Check whether the documentation supports the additional code(s) the note names, and report them with K90.0 when it does. Where the instruction is conditional (“if applicable”, “if known”), it applies only when the record documents the condition.
See the official tabular notes · Guidelines I.A.13
Code Also — related condition(1 note)
Coding workflow: Review the related condition when both are documented and the instruction applies. A Code Also note does not fix sequencing; the order follows the circumstances of the encounter.
ReviewK86.81
See the official tabular notes · Guidelines I.A.17
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: Both the condition K90.0 describes and a condition named in its Excludes1 note are documented for the same encounter.
Coding question: Can both codes be reported?
Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.
Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).
ReviewK91.2
Documentation: A condition the Use Additional Code note names is documented.
Coding question: Is a second code reported with K90.0?
Path: Review the Use Additional Code note and the code it names.
Reason: The additional code is reported when the record documents the condition; a conditional instruction applies only when its condition is met (Guidelines I.A.13).
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Indexed Clinical Terms (28)
Official source data — entries quoted as published, in the Index’s own lookup phrasing
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.
- Ataxia, ataxy, ataxic, gluten, with celiac disease
- Celiac, disease (with steatorrhea)
- Celiac, infantilism
- Crisis, celiac
- Disease, diseased, celiac (adult) (infantile) (with steatorrhea)
- Disease, diseased, Gee (-Herter) (-Heubner) (-Thaysen) (nontropical sprue)
- Disease, diseased, Herter (-Gee) (-Heubner) (nontropical sprue)
- Disease, diseased, Heubner-Herter (nontropical sprue)
- Disease, diseased, Thaysen-Gee (nontropical sprue)
- Enteropathy, celiac-gluten-sensitive
- Gee (-Herter)(-Thaysen) disease (nontropical sprue)
- Herter-Gee syndrome
- Heubner-Herter disease
- Infancy, infantile, infantilism, celiac
- Infancy, infantile, infantilism, Herter's (nontropical sprue)
- Infancy, infantile, infantilism, intestinal
- Morbus, celiacus
- Psilosis (sprue) (tropical), nontropical
- Rickets (active) (acute) (adolescent) (chest wall) (congenital) (current) (infantile) (intestinal), celiac
- Sprue (tropical), celiac
- Sprue (tropical), nontropical
- Steatorrhea (chronic), primary
- Syndrome, celiac
- Syndrome, Gee-Herter-Heubner
- Syndrome, Herter (-Gee) (nontropical sprue)
- Syndrome, Heubner-Herter
- Thaysen-Gee disease (nontropical sprue)
- Thaysen's disease
Official Coding Guidelines
No excerpt in the ICD-10-CM Official Guidelines names this code specifically. Its chapter carries only this chapter-wide note:
Chapter 11: Diseases of the Digestive System (K00-K95)
Reserved for future guideline expansion
Decision Points
The directives on this code's own record, as a pre-claim checklist.
- 3 Use Additional Code instructions — report the named additional code(s) when the documentation supports them. See the Use Additional Code notes
- 1 Code Also note — a second code may apply; the guidelines leave its sequencing to the circumstances of the encounter. See the Code Also notes
- 1 Excludes1 entry — codes named there are generally not reported together with this code (Guidelines I.A.12.a). See the Excludes1 notes
Checklist rows are derived from this code's own official directives; the wording of each check is MedCoder editorial. The official notes themselves are in the sections each row links to.
Verify Before Coding
- No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder structured relationships — computed from published CMS and AHRQ datasets
Other codes that name K90.0 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.
Referenced by 10 Excludes1 notes across 2 chapters: E40 — Kwashiorkor (via K90.-), E40-E46 — Malnutrition (E40-E46) (via K90.-), E41 — Nutritional marasmus (via K90.-), E42 — Marasmic kwashiorkor (via K90.-), E43 — Unspecified severe protein-calorie malnutrition (via K90.-), E44 — Protein-calorie malnutrition of moderate and mild degree (via K90.-), E45 — Retarded development following protein-calorie malnutrition (via K90.-), E46 — Unspecified protein-calorie malnutrition (via K90.-), E55.0 — Rickets, active, K59 — Other functional intestinal disorders (via K90.-).
These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.
Referenced by 1 Excludes2 note: K90.4 — Other malabsorption due to intolerance.
These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.
Referenced by 1 Code First instruction: G32.81 — Cerebellar ataxia in diseases classified elsewhere.
Each of these codes carries a Code First note naming this condition — when that code is reported, THIS code is sequenced first, ahead of it.
MS-DRG Grouper Relationships (FY2026)
Potential MS-DRG participation — not a DRG assignment.
FY2026 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.
Named in the grouper logic of 2 MS-DRGs: DRG 391 (MDC 06), DRG 392 (MDC 06).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Clinical classification (AHRQ CCSR):DIG025 — Other specified and unspecified gastrointestinal disorders (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Other specified and unspecified gastrointestinal disorders).
K63.829 — Intestinal methanogen overgrowth, unspecified, K63.89 — Other specified diseases of intestine, K63.9 — Disease of intestine, unspecified, K66.0 — Peritoneal adhesions (postprocedural) (postinfection), K66.1 — Hemoperitoneum, K66.8 — Other specified disorders of peritoneum, K66.9 — Disorder of peritoneum, unspecified, K68.2 — Retroperitoneal fibrosis, K68.3 — Retroperitoneal hematoma, K68.9 — Other disorders of retroperitoneum, K90.1 — Tropical sprue, K90.2 — Blind loop syndrome, not elsewhere classified, K90.4 — Other malabsorption due to intolerance, K90.41 — Non-celiac gluten sensitivity, K90.49 — Malabsorption due to intolerance, not elsewhere classified, K90.81 — Whipple's disease, K90.821 — Short bowel syndrome with colon in continuity, K90.822 — Short bowel syndrome without colon in continuity, K90.829 — Short bowel syndrome, unspecified, K90.83 — Intestinal failure, +64 more
Same Index main term, other category
The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Morbus”, “Ataxia, ataxy, ataxic”, “Infancy, infantile, infantilism”, …; these codes share that main term but sit in a different category of the Tabular List.
I69.293 — Ataxia following other nontraumatic intracranial hemorrhage (following, cerebrovascular disease, nontraumatic intracranial hemorrhage NEC), I69.393 — Ataxia following cerebral infarction (following, cerebrovascular disease, cerebral infarction), I69.893 — Ataxia following other cerebrovascular disease (following, cerebrovascular disease, specified disease NEC), I69.993 — Ataxia following unspecified cerebrovascular disease (following, cerebrovascular disease), I77.4 — Celiac artery compression syndrome (artery compression syndrome), I95.2 — Hypotension due to drugs (nitritoid), K52.22 — Food protein-induced enteropathy (food protein-induced), K55.059 — Acute (reversible) ischemia of intestine, part and extent unspecified (hemorrhagic, terminal), K63.9 — Disease of intestine, unspecified, K86.89 — Other specified diseases of pancreas (pancreatic), M16.9 — Osteoarthritis of hip, unspecified (coxae senilis), M35.9 — Systemic involvement of connective tissue, unspecified (gluten), M95.5 — Acquired deformity of pelvis (pelvis), N13.8 — Other obstructive and reflux uropathy (Dietl's), N25.0 — Renal osteodystrophy (renal), N28.0 — Ischemia and infarction of kidney (renal), O33.1 — Maternal care for disproportion due to generally contracted pelvis (pelvis, with disproportion), O65.1 — Obstructed labor due to generally contracted pelvis (pelvis, with disproportion, causing obstructed labor), P53 — Hemorrhagic disease of newborn (hemorrhagicus neonatorum), P54.5 — Neonatal cutaneous hemorrhage (maculosus neonatorum), +44 more
Lab tests where this diagnosis supports Medicare coverage (NCD)
Medicare's National Coverage Determination (NCD) program lists this diagnosis as medical justification for these lab tests.
Fecal Occult Blood Test (FOBT), Iron Panel, Partial Thromboplastin Time (PTT) Test, Prothrombin Time Test and INR (PT/INR)
Contextual Map
Every relationship of K90.0 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Run K90.0 with these 12 related codes in Claim Check
Hierarchy
- K00-K95 — Chapter 11: Diseases of the Digestive System (K00-K95) (K00-K95)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- K90-K95 — Other diseases of the digestive system[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Use Additional Code
- G32.81 — Cerebellar ataxia in diseases classified elsewhere[Use Additional Code]: “gluten ataxia (G32.81)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- L13.0 — Dermatitis herpetiformis[Use Additional Code]: “dermatitis herpetiformis (L13.0)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Code Also
- K86.81 — Exocrine pancreatic insufficiency[Code Also]: “exocrine pancreatic insufficiency (K86.81)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Referenced by Excludes1 notes (10)
- E40 — Kwashiorkor[Excludes1](via K90.-): “intestinal malabsorption (K90.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- E40-E46 — Malnutrition (E40-E46)[Excludes1](via K90.-): “intestinal malabsorption (K90.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- E41 — Nutritional marasmus[Excludes1](via K90.-): “intestinal malabsorption (K90.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- E42 — Marasmic kwashiorkor[Excludes1](via K90.-): “intestinal malabsorption (K90.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- E43 — Unspecified severe protein-calorie malnutrition[Excludes1](via K90.-): “intestinal malabsorption (K90.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- E44 — Protein-calorie malnutrition of moderate and mild degree[Excludes1](via K90.-): “intestinal malabsorption (K90.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- E45 — Retarded development following protein-calorie malnutrition[Excludes1](via K90.-): “intestinal malabsorption (K90.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- E46 — Unspecified protein-calorie malnutrition[Excludes1](via K90.-): “intestinal malabsorption (K90.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- and 2 more
Referenced by Excludes2 notes
- K90.4 — Other malabsorption due to intolerance[Excludes2]: “celiac gluten-sensitive enteropathy (K90.0)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Referenced by Code First instructions
- G32.81 — Cerebellar ataxia in diseases classified elsewhere[Code First]: “celiac disease (with gluten ataxia) (K90.0)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Clinical classification (CCSR)
- DIG025 — Other specified and unspecified gastrointestinal disorders[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
MS-DRG Grouper
- DRG 391 — ESOPHAGITIS, GASTROENTERITIS AND MISCELLANEOUS DIGESTIVE DISORDERS WITH MCC[MS-DRG]: “ESOPHAGITIS, GASTROENTERITIS AND MISCELLANEOUS DIGESTIVE DISORDERS WITH MCC (MDC 06)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 392 — ESOPHAGITIS, GASTROENTERITIS AND MISCELLANEOUS DIGESTIVE DISORDERS WITHOUT MCC[MS-DRG]: “ESOPHAGITIS, GASTROENTERITIS AND MISCELLANEOUS DIGESTIVE DISORDERS WITHOUT MCC (MDC 06)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
MDC crossing
- MDC 06 — Diseases and Disorders of the Digestive System[MDC crossing]: “Diseases and Disorders of the Digestive System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 5,744 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026
Index entries (28)
- Ataxia, ataxy, ataxic, gluten, with celiac disease[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Celiac, disease (with steatorrhea)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Celiac, infantilism[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Crisis, celiac[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Disease, diseased, celiac (adult) (infantile) (with steatorrhea)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Disease, diseased, Gee (-Herter) (-Heubner) (-Thaysen) (nontropical sprue)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Disease, diseased, Herter (-Gee) (-Heubner) (nontropical sprue)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Disease, diseased, Heubner-Herter (nontropical sprue)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- and 20 more
Nearest codes (16)
- K90 — Intestinal malabsorption[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- K90.1 — Tropical sprue[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- K90.2 — Blind loop syndrome, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- K90.3 — Pancreatic steatorrhea[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- K90.4 — Other malabsorption due to intolerance[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- K90.41 — Non-celiac gluten sensitivity[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- K90.49 — Malabsorption due to intolerance, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- K90.8 — Other intestinal malabsorption[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- and 8 more
Change history
- FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
- Coding guidelines Official source data
- ICD-10-CM Official Guidelines for Coding and Reporting (FY2026), quoted by section Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
- Inpatient payment groups Official source data
- CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder structured relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "K90.0 — Celiac disease." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/k90.0-celiac-disease
Change history
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionCeliac disease
No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027 (effective October 1, 2026), and none are recorded for this code. Note changes are tracked from FY2027 only.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to K90.0 in its code family, with their registry titles.
- K90 — Intestinal malabsorption
- K90.1 — Tropical sprue
- K90.2 — Blind loop syndrome, not elsewhere classified
- K90.3 — Pancreatic steatorrhea
- K90.4 — Other malabsorption due to intolerance
- K90.41 — Non-celiac gluten sensitivity
- K90.49 — Malabsorption due to intolerance, not elsewhere classified
- K90.8 — Other intestinal malabsorption
- K90.81 — Whipple's disease
- K90.82 — Short bowel syndrome