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Q13.81 ICD-10-CM Code: Rieger anomaly

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
1 inclusion term · 7 Excludes2 · 1 use-additional code · 1 code-also instruction

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.

  • MS-DRG 124 — OTHER DISORDERS OF THE EYE WITH MCC OR THROMBOLYTIC AGENT (MDC 02)
  • MS-DRG 125 — OTHER DISORDERS OF THE EYE WITHOUT MCC (MDC 02)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q13.81 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on Q13.81 itself; “inherited from” names the category or block whose note applies here.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Axenfeld-Rieger syndrome

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

Source: inherited from Q10-Q18

Code Also

Additional codes that may be required to fully describe the encounter.

  • any other associated congenital malformations such as cardiac defects

Use Additional Code

Supplementary codes the tabular list directs you to add.

  • Use additional code for associated glaucoma (H42)

Coder workflow for Q13.81

MedCoder structured workflow — derived from this code’s own official record

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
The conditions the Use Additional Code note names
Reported with this code when documented; a conditional instruction (“if applicable”, “if known”) applies only when the record supports it.

Official instructions as workflow

  • Excludes2 — not part of Q13.81(7 notes)

    Coding workflow: The conditions named in this note are not included in Q13.81. When the record documents both, both may be reported; the note is a boundary, not a prohibition.

    CompareQ05.0, Q05.5, Q67.5, Q31, Q38.0, Q30

    See the official tabular notes · Guidelines I.A.12.b

  • Use Additional Code — after identifying Q13.81(1 note)

    Coding workflow: Check whether the documentation supports the additional code(s) the note names, and report them with Q13.81 when it does. Where the instruction is conditional (“if applicable”, “if known”), it applies only when the record documents the condition.

    ReviewH42

    See the official tabular notes · Guidelines I.A.13

  • Code Also — related condition(1 note)

    Coding workflow: Review the related condition when both are documented and the instruction applies. A Code Also note does not fix sequencing; the order follows the circumstances of the encounter.

    See the official tabular notes · Guidelines I.A.17

Coding decision scenarios

Pattern scenarios for this code’s structure — decision rules, not clinical cases

Documentation: A condition the Use Additional Code note names is documented.

Coding question: Is a second code reported with Q13.81?

Path: Review the Use Additional Code note and the code it names.

Reason: The additional code is reported when the record documents the condition; a conditional instruction applies only when its condition is met (Guidelines I.A.13).

ReviewH42

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Code Overview

Rieger anomaly is a billable ICD-10-CM diagnosis code (Q13.81).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (4)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Decision Points

The directives on this code's own record, as a pre-claim checklist.

  1. 1 Use Additional Code instruction — report the named additional code(s) when the documentation supports them. See the Use Additional Code notes
  2. 1 Code Also note — a second code may apply; the guidelines leave its sequencing to the circumstances of the encounter. See the Code Also notes
  3. 7 Excludes2 entries — those conditions are not part of this code and may be reported additionally when documented. See the Excludes2 notes

Checklist rows are derived from this code's own official directives; the wording of each check is MedCoder editorial. The official notes themselves are in the sections each row links to.

Verify Before Coding

  • No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name Q13.81 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 1 Code First instruction: H42 — Glaucoma in diseases classified elsewhere.

Each of these codes carries a Code First note naming this condition — when that code is reported, THIS code is sequenced first, ahead of it.

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.

Named in the grouper logic of 2 MS-DRGs: DRG 124 (MDC 02), DRG 125 (MDC 02).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MAL005 — Congenital malformations of eye, ear, face, neck (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Congenital malformations of eye, ear, face, neck).

Q12.3 — Congenital aphakia, Q12.4 — Spherophakia, Q12.8 — Other congenital lens malformations, Q12.9 — Congenital lens malformation, unspecified, Q13.0 — Coloboma of iris, Q13.1 — Absence of iris, Q13.2 — Other congenital malformations of iris, Q13.3 — Congenital corneal opacity, Q13.4 — Other congenital corneal malformations, Q13.5 — Blue sclera, Q13.89 — Other congenital malformations of anterior segment of eye, Q13.9 — Congenital malformation of anterior segment of eye, unspecified, Q14.0 — Congenital malformation of vitreous humor, Q14.1 — Congenital malformation of retina, Q14.2 — Congenital malformation of optic disc, Q14.3 — Congenital malformation of choroid, Q14.8 — Other congenital malformations of posterior segment of eye, Q14.9 — Congenital malformation of posterior segment of eye, unspecified, Q15.0 — Congenital glaucoma, Q15.8 — Other specified congenital malformations of eye, +41 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Anomaly, anomalous”, “Glaucoma”; these codes share that main term but sit in a different category of the Tabular List.

Q05.9 — Spina bifida, unspecified (meningocele), Q06.3 — Other congenital cauda equina malformations (cauda equina), Q06.9 — Congenital malformation of spinal cord, unspecified (meninges, spinal), Q07.8 — Other specified congenital malformations of nervous system (optic, nerve), Q07.9 — Congenital malformation of nervous system, unspecified (gyri), Q10.0 — Congenital ptosis (eye, ptosis), Q10.3 — Other congenital malformations of eyelid (lid), Q10.6 — Other congenital malformations of lacrimal apparatus (caruncle, lacrimal), Q10.7 — Congenital malformation of orbit (orbit), Q12.9 — Congenital lens malformation, unspecified (lens), Q14.0 — Congenital malformation of vitreous humor (vitreous body or humor), Q14.1 — Congenital malformation of retina (retina), Q14.2 — Congenital malformation of optic disc (optic, disc), Q14.3 — Congenital malformation of choroid (choroid), Q14.8 — Other congenital malformations of posterior segment of eye (eye, posterior segment, specified NEC), Q14.9 — Congenital malformation of posterior segment of eye, unspecified (eye, posterior segment), Q15.0 — Congenital glaucoma (newborn), Q15.8 — Other specified congenital malformations of eye (artery, eye), Q15.9 — Congenital malformation of eye, unspecified (eye), Q16.1 — Congenital absence, atresia and stricture of auditory canal (external) (osseous meatus), +263 more

Contextual Map

Every relationship of Q13.81 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run Q13.81 with this related code in Claim Check

Hierarchy

Use Additional Code

Referenced by Code First instructions

Clinical classification (CCSR)

MS-DRG Grouper

MDC crossing

  • MDC 02 — Diseases and Disorders of the Eye[MDC crossing]: “Diseases and Disorders of the Eye — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 1,200 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries

  • Anomaly, anomalous (congenital) (unspecified type), Rieger[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Glaucoma, in (due to), Rieger anomaly[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Rieger anomaly or syndrome[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Syndrome, Axenfeld-Rieger[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026

Nearest codes (10)

Change history (3)

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "Q13.81 — Rieger anomaly." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/q13.81-rieger-anomaly

Change history

  • FY2025 — October 1, 2024
    Description revised
    Rieger's anomaly → Rieger anomaly
    FY2025 changes
  • FY2025 — October 1, 2024
    Short description revised
    Rieger's anomaly → Rieger anomaly
    FY2025 changes
  • FY2016 — October 1, 2015
    In the code set at ICD-10-CM adoption
    Rieger's anomaly

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q13.81 in its code family, with their registry titles.

View all codes in the Q13 family