Q33.6 ICD-10-CM Code: Congenital hypoplasia and dysplasia of lung
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Inpatient Payment Groups (MS-DRG)
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0 (FY2026), Appendix B.
- MS-DRG 205 — OTHER RESPIRATORY SYSTEM DIAGNOSES WITH MCC (MDC 04)
- MS-DRG 206 — OTHER RESPIRATORY SYSTEM DIAGNOSES WITHOUT MCC (MDC 04)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Code Set: Valid FY2026 and FY2027. FY2026 took effect October 1, 2025.
Official Registry Overview & Definition
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for Q33.6 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- pulmonary hypoplasia associated with short gestation (P28.0)
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q33.6 in its code family, with their registry titles.
- Q33 — Congenital malformations of lung
- Q33.0 — Congenital cystic lung
- Q33.1 — Accessory lobe of lung
- Q33.2 — Sequestration of lung
- Q33.3 — Agenesis of lung
- Q33.4 — Congenital bronchiectasis
- Q33.5 — Ectopic tissue in lung
- Q33.8 — Other congenital malformations of lung
- Q33.9 — Congenital malformation of lung, unspecified
Indexed Clinical Terms (6)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Development, imperfect, congenital, lungs
- Dysplasia, lung, congenital (not associated with short gestation)
- Hypoplasia, hypoplastic, lung (lobe) (not associated with short gestation)
- Hypoplasia, hypoplastic, pulmonary (not associated with short gestation)
- Inadequate, inadequacy, development, lungs
- Undeveloped, undevelopment, lung