Q33.2 ICD-10-CM Code: Sequestration of lung

Indexed Clinical Terms (1)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

• Sequestration, lung, congenital

Don’t confuse Q33.2 with…

MedCoder analysis — pairs from this code’s official notes, distinctions written by MedCoder

The codes most likely to be picked instead of Q33.2 — named in its own official notes, or sharing its laterality or encounter family — with what separates them and which documentation moves the case. Each links to the full comparison.

• Q33.9— Specificity relationship (Review)

  Overlapping diagnoses in the same category.

  Overlapping codes in the same category — the documentation decides which is the more specific fit.

  What moves you there: A record that documents no more than “Congenital malformation of lung, unspecified” takes Q33.9; specificity in the record moves it back here.

  Full comparison: Q33.2 vs Q33.9 →

Relationships are read from this code's own official notes, its laterality siblings and its encounter family; the wording of each distinction is MedCoder editorial, and the documentation named in each “what moves you there” line is the official note phrase or sibling title itself. Source: CMS ICD-10-CM tabular instructional notes; ICD-10-CM Official Guidelines, Section I.A.12.a.

Verify Before Coding

• MCC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name Q33.2 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 1 Code Also instruction: P28 — Other respiratory conditions originating in the perinatal period (via Q33.-).

These codes suggest coding this condition alongside when both are present.

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: MCC — Major Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 13 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 2 MS-DRGs: DRG 205 (MDC 04), DRG 206 (MDC 04).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MAL007 — Respiratory congenital malformations (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical process (MS-DRG)

Acts as MCC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

Q33.0 — Congenital cystic lung, Q33.1 — Accessory lobe of lung, Q33.3 — Agenesis of lung, Q33.4 — Congenital bronchiectasis, Q33.5 — Ectopic tissue in lung, Q33.6 — Congenital hypoplasia and dysplasia of lung, Q33.8 — Other congenital malformations of lung, Q33.9 — Congenital malformation of lung, unspecified, Q34.0 — Anomaly of pleura, Q34.1 — Congenital cyst of mediastinum, Q34.8 — Other specified congenital malformations of respiratory system, Q34.9 — Congenital malformation of respiratory system, unspecified

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Respiratory congenital malformations).

Q31.5 — Congenital laryngomalacia, Q31.8 — Other congenital malformations of larynx, Q31.9 — Congenital malformation of larynx, unspecified, Q32.0 — Congenital tracheomalacia, Q32.1 — Other congenital malformations of trachea, Q32.2 — Congenital bronchomalacia, Q32.3 — Congenital stenosis of bronchus, Q32.4 — Other congenital malformations of bronchus, Q33.0 — Congenital cystic lung, Q33.1 — Accessory lobe of lung, Q33.3 — Agenesis of lung, Q33.4 — Congenital bronchiectasis, Q33.5 — Ectopic tissue in lung, Q33.6 — Congenital hypoplasia and dysplasia of lung, Q33.8 — Other congenital malformations of lung, Q33.9 — Congenital malformation of lung, unspecified, Q34.0 — Anomaly of pleura, Q34.1 — Congenital cyst of mediastinum, Q34.8 — Other specified congenital malformations of respiratory system, Q34.9 — Congenital malformation of respiratory system, unspecified, +10 more

Contextual Map

Every relationship of Q33.2 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run Q33.2 with this related code in Claim Check

Hierarchy

• Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q30-Q34 — Congenital malformations of the respiratory system[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026

Referenced by Code Also instructions

• P28 — Other respiratory conditions originating in the perinatal period[Code Also](via Q33.-): “, if applicable, congenital malformations of the respiratory system (Q30-Q34)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026

Clinical classification (CCSR)

• MAL007 — Respiratory congenital malformations[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)

MS-DRG Grouper

• MCC — Major Complication or Comorbidity [MS-DRG severity]: “As a secondary diagnosis this code can raise the stay's MS-DRG severity tier (MCC).”— CMS MS-DRG Definitions Manual (Appendix C) · FY2026
• DRG 205 — OTHER RESPIRATORY SYSTEM DIAGNOSES WITH MCC[MS-DRG]: “OTHER RESPIRATORY SYSTEM DIAGNOSES WITH MCC (MDC 04)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
• DRG 206 — OTHER RESPIRATORY SYSTEM DIAGNOSES WITHOUT MCC[MS-DRG]: “OTHER RESPIRATORY SYSTEM DIAGNOSES WITHOUT MCC (MDC 04)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026

MDC crossing

• MDC 04 — Diseases and Disorders of the Respiratory System[MDC crossing]: “Diseases and Disorders of the Respiratory System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 3,998 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries

• Sequestration, lung, congenital[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026

Nearest codes (9)

• Q33 — Congenital malformations of lung[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q33.0 — Congenital cystic lung[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q33.1 — Accessory lobe of lung[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q33.3 — Agenesis of lung[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q33.4 — Congenital bronchiectasis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q33.5 — Ectopic tissue in lung[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q33.6 — Congenital hypoplasia and dysplasia of lung[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• Q33.8 — Other congenital malformations of lung[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• and 1 more

Change history

• FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data

CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page

Claim edits Official source data

CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page

Inpatient payment groups Official source data

CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page

Change history and date-of-service validity Official source data

CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page

Comparisons, relationships and the contextual map MedCoder structured relationship

Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears

Summary and FAQ answers MedCoder explanation

Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q33.2 in its code family, with their registry titles.

• Q33 — Congenital malformations of lung
• Q33.0 — Congenital cystic lung
• Q33.1 — Accessory lobe of lung
• Q33.3 — Agenesis of lung
• Q33.4 — Congenital bronchiectasis
• Q33.5 — Ectopic tissue in lung
• Q33.6 — Congenital hypoplasia and dysplasia of lung
• Q33.8 — Other congenital malformations of lung
• Q33.9 — Congenital malformation of lung, unspecified

View all codes in the Q33 family