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Q83.0 ICD-10-CM Code: Congenital absence of breast with absent nipple

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
3 Excludes2

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v44, Appendix B.

  • MS-DRG 600 — NON-MALIGNANT BREAST DISORDERS WITH CC/MCC (MDC 09)
  • MS-DRG 601 — NON-MALIGNANT BREAST DISORDERS WITHOUT CC/MCC (MDC 09)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q83.0 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2027Effective: October 1, 2026

Trace:FY2027 changesChange historyRelease, file and checksum

Notes without a marker are published on Q83.0 itself; “inherited from” names the category or block whose note applies here.

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

Source: inherited from Q83

Coder workflow for Q83.0

MedCoder structured workflow — derived from this code’s own official record

Before you code Q83.0

  1. Q83.0’s title joins a condition with an associated condition or complication. Confirm each component is documented. Where the classification presumes the link through the “with” convention, only a provider statement that the conditions are unrelated defeats it. A combination code is assigned only when it fully identifies the documented conditions; a required second code for the stage, type or manifestation is still reported when the notes ask for it (Guidelines I.B.9, I.A.15).

    Guide: Combination codes →

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
The associated condition or complication
Whether the associated condition the title names is documented; the “with” convention presumes some links, and a provider statement that the conditions are unrelated defeats it (Guidelines I.A.15).

Official instructions as workflow

  • Excludes2 — not part of Q83.0(3 notes)

    Coding workflow: The conditions named in this note are not included in Q83.0. When the record documents both, both may be reported; the note is a boundary, not a prohibition.

    CompareQ79.8, N64.82

    See the official tabular notes · Guidelines I.A.12.b

Coding decision scenarios

Pattern scenarios for this code’s structure — decision rules, not clinical cases

Documentation: Only one of the components this code’s title joins is documented.

Coding question: Is Q83.0 supported?

Path: Review the code for the documented component on its own.

Reason: A combination code is assigned only when it fully identifies the documented conditions; otherwise the documented component takes its own code (Guidelines I.B.9).

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Don’t confuse Q83.0 with…

MedCoder analysis — pairs from this code’s official notes, distinctions written by MedCoder

The codes most likely to be picked instead of Q83.0 — named in its own official notes, or sharing its laterality or encounter family — with what separates them and which documentation moves the case. Each links to the full comparison.

  • Q83.9— Specificity relationship (Review)

    Overlapping diagnoses in the same category.

    Overlapping codes in the same category — the documentation decides which is the more specific fit.

    What moves you there: A record that documents no more than “Congenital malformation of breast, unspecified” takes Q83.9; specificity in the record moves it back here.

    Full comparison: Q83.0 vs Q83.9 →

  • Q79.8— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of absence of pectoral muscle adds Q79.8; it is not part of this code and both may be reported when both are documented.

    Full comparison: Q83.0 vs Q79.8 →

  • N64.82— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of hypoplasia of breast adds N64.82; it is not part of this code and both may be reported when both are documented.

    Full comparison: Q83.0 vs N64.82 →

Relationships are read from this code's own official notes, its laterality siblings and its encounter family; the wording of each distinction is MedCoder editorial, and the documentation named in each “what moves you there” line is the official note phrase or sibling title itself. Source: CMS ICD-10-CM tabular instructional notes; ICD-10-CM Official Guidelines, Section I.A.12.a.

Code Overview

Congenital absence of breast with absent nipple is a billable ICD-10-CM diagnosis code (Q83.0).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (2)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Verify Before Coding

  • No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name Q83.0 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 2 Excludes1 notes across 2 chapters: N64.82 — Hypoplasia of breast, P83 — Other conditions of integument specific to newborn (via Q83.-).

These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.

MS-DRG Grouper Relationships (FY2027)

Potential MS-DRG participation — not a DRG assignment.

FY2027 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.

Named in the grouper logic of 2 MS-DRGs: DRG 600 (MDC 09), DRG 601 (MDC 09).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MAL010 — Other specified and unspecified congenital anomalies (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Other specified and unspecified congenital anomalies).

Q81.9 — Epidermolysis bullosa, unspecified, Q82.0 — Hereditary lymphedema, Q82.1 — Xeroderma pigmentosum, Q82.2 — Congenital cutaneous mastocytosis, Q82.3 — Incontinentia pigmenti, Q82.4 — Ectodermal dysplasia (anhidrotic), Q82.5 — Congenital non-neoplastic nevus, Q82.6 — Congenital sacral dimple, Q82.8 — Other specified congenital malformations of skin, Q82.9 — Congenital malformation of skin, unspecified, Q83.1 — Accessory breast, Q83.2 — Absent nipple, Q83.3 — Accessory nipple, Q83.8 — Other congenital malformations of breast, Q83.9 — Congenital malformation of breast, unspecified, Q84.0 — Congenital alopecia, Q84.1 — Congenital morphological disturbances of hair, not elsewhere classified, Q84.2 — Other congenital malformations of hair, Q84.3 — Anonychia, Q84.4 — Congenital leukonychia, +59 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main term “Agenesis”; these codes share that main term but sit in a different category of the Tabular List.

Q72.0 — Congenital complete absence of lower limb (leg), Q72.1 — Congenital absence of thigh and lower leg with foot present (leg, with foot present), Q72.2 — Congenital absence of both lower leg and foot (leg, lower leg, and foot), Q72.3 — Congenital absence of foot and toe(s) (foot), Q73.0 — Congenital absence of unspecified limb(s) (limb), Q74.0 — Other congenital malformations of upper limb(s), including shoulder girdle (scapula), Q74.1 — Congenital malformation of knee (patella), Q74.2 — Other congenital malformations of lower limb(s), including pelvic girdle (pelvic girdle), Q75.8 — Other specified congenital malformations of skull and face bones (skull), Q76.49 — Other congenital malformations of spine, not associated with scoliosis (spine), Q76.6 — Other congenital malformations of ribs (rib), Q76.7 — Congenital malformation of sternum (sternum), Q79.1 — Other congenital malformations of diaphragm (diaphragm), Q79.8 — Other congenital malformations of musculoskeletal system (tendon), Q79.9 — Congenital malformation of musculoskeletal system, unspecified (bone), Q84.0 — Congenital alopecia (hair), Q84.3 — Anonychia (nail), Q89.01 — Asplenia (congenital) (spleen), Q89.1 — Congenital malformations of adrenal gland (adrenal), Q89.2 — Congenital malformations of other endocrine glands (thymus), +92 more

Contextual Map

Every relationship of Q83.0 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run Q83.0 with these 2 related codes in Claim Check

Hierarchy

Referenced by Excludes1 notes

Clinical classification (CCSR)

MS-DRG Grouper

MDC crossing

  • MDC 09 — Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast[MDC crossing]: “Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 7,378 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2027

Index entries

  • Agenesis, breast (with nipple present), with absent nipple[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Amastia (with nipple present), with absent nipple[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026

Nearest codes

Change history

  • FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v44 Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "Q83.0 — Congenital absence of breast with absent nipple." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/q83.0-congenital-absence-of-breast-with-absent-nipple

Change history

  • FY2016 — October 1, 2015
    In the code set at ICD-10-CM adoption
    Congenital absence of breast with absent nipple

No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027, and none are recorded for this code. Note changes are tracked from FY2027 only.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q83.0 in its code family, with their registry titles.

View all codes in the Q83 family