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Other specified and unspecified congenital anomalies

CCSR category MAL010 · 80 ICD-10-CM codes

Code Families in This Category

  • Q87 Other specified congenital malformation syndromes affecting multiple systems · 20
  • Q89 Other congenital malformations, not elsewhere classified · 11
  • Q82 Other congenital malformations of skin · 9
  • Q84 Other congenital malformations of integument · 9
  • Q80 Congenital ichthyosis · 7
  • Q85 Phakomatoses, not elsewhere classified · 7
  • Q83 Congenital malformations of breast · 6
  • Q81 Epidermolysis bullosa · 5
  • Q86 Congenital malformation syndromes due to known exogenous causes, not elsewhere classified · 4
  • P09 Abnormal findings on neonatal screening · 2

ICD-10-CM Codes in This Category (80)

  • P09.2 — Abnormal findings on neonatal screening for congenital endocrine disease
  • P09.3 — Abnormal findings on neonatal screening for congenital hematologic disorders
  • Q80.0 — Ichthyosis vulgaris
  • Q80.1 — X-linked ichthyosis
  • Q80.2 — Lamellar ichthyosis
  • Q80.3 — Congenital bullous ichthyosiform erythroderma
  • Q80.4 — Harlequin fetus
  • Q80.8 — Other congenital ichthyosis
  • Q80.9 — Congenital ichthyosis, unspecified
  • Q81.0 — Epidermolysis bullosa simplex
  • Q81.1 — Epidermolysis bullosa letalis
  • Q81.2 — Epidermolysis bullosa dystrophica
  • Q81.8 — Other epidermolysis bullosa
  • Q81.9 — Epidermolysis bullosa, unspecified
  • Q82.0 — Hereditary lymphedema
  • Q82.1 — Xeroderma pigmentosum
  • Q82.2 — Congenital cutaneous mastocytosis
  • Q82.3 — Incontinentia pigmenti
  • Q82.4 — Ectodermal dysplasia (anhidrotic)
  • Q82.5 — Congenital non-neoplastic nevus
  • Q82.6 — Congenital sacral dimple
  • Q82.8 — Other specified congenital malformations of skin
  • Q82.9 — Congenital malformation of skin, unspecified
  • Q83.0 — Congenital absence of breast with absent nipple
  • Q83.1 — Accessory breast
  • Q83.2 — Absent nipple
  • Q83.3 — Accessory nipple
  • Q83.8 — Other congenital malformations of breast
  • Q83.9 — Congenital malformation of breast, unspecified
  • Q84.0 — Congenital alopecia
  • Q84.1 — Congenital morphological disturbances of hair, not elsewhere classified
  • Q84.2 — Other congenital malformations of hair
  • Q84.3 — Anonychia
  • Q84.4 — Congenital leukonychia
  • Q84.5 — Enlarged and hypertrophic nails
  • Q84.6 — Other congenital malformations of nails
  • Q84.8 — Other specified congenital malformations of integument
  • Q84.9 — Congenital malformation of integument, unspecified
  • Q85.1 — Tuberous sclerosis
  • Q85.8 — Other phakomatoses, not elsewhere classified
  • Q85.81 — PTEN hamartoma tumor syndrome
  • Q85.82 — Other Cowden syndrome
  • Q85.83 — Von Hippel-Lindau syndrome
  • Q85.89 — Other phakomatoses, not elsewhere classified
  • Q85.9 — Phakomatosis, unspecified
  • Q86.0 — Fetal alcohol syndrome (dysmorphic)
  • Q86.1 — Fetal hydantoin syndrome
  • Q86.2 — Dysmorphism due to warfarin
  • Q86.8 — Other congenital malformation syndromes due to known exogenous causes
  • Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
  • Q87.1 — Congenital malformation syndromes predominantly associated with short stature
  • Q87.11 — Prader-Willi syndrome
  • Q87.19 — Other congenital malformation syndromes predominantly associated with short stature
  • Q87.2 — Congenital malformation syndromes predominantly involving limbs
  • Q87.3 — Congenital malformation syndromes involving early overgrowth
  • Q87.40 — Marfan syndrome, unspecified
  • Q87.410 — Marfan syndrome with aortic dilation
  • Q87.418 — Marfan syndrome with other cardiovascular manifestations
  • Q87.42 — Marfan syndrome with ocular manifestations
  • Q87.43 — Marfan syndrome with skeletal manifestation
  • Q87.5 — Other congenital malformation syndromes with other skeletal changes
  • Q87.81 — Alport syndrome
  • Q87.82 — Arterial tortuosity syndrome
  • Q87.83 — Bardet-Biedl syndrome
  • Q87.84 — Laurence-Moon syndrome
  • Q87.85 — MED13L syndrome
  • Q87.87 — Hao-Fountain Syndrome
  • Q87.88 — CTNNB1 syndrome
  • Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified
  • Q89.01 — Asplenia (congenital)
  • Q89.09 — Congenital malformations of spleen
  • Q89.1 — Congenital malformations of adrenal gland
  • Q89.2 — Congenital malformations of other endocrine glands
  • Q89.3 — Situs inversus
  • Q89.4 — Conjoined twins
  • Q89.7 — Multiple congenital malformations, not elsewhere classified
  • Q89.8 — Other specified congenital malformations
  • Q89.81 — Kabuki syndrome
  • Q89.89 — Other specified congenital malformations
  • Q89.9 — Congenital malformation, unspecified

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, Rockville, MD. All data sources.