ICD-10/Q89.89

Q89.89 ICD 2026 Code: Other specified congenital malformations

Q89.89 is the authoritative medical code for Other specified congenital malformations. This classification is used in medical billing and clinical recording to specify the clinical criteria for other specified congenital malformations (ICD-10-CM Q89.89), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Other specified congenital malformations is a billable ICD-10-CM diagnosis code Q89.89. Use additional code: code(s) to identify all associated manifestations.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for Q89.89 in the official ICD-10-CM tabular list.

Use Additional Code

Supplementary codes the tabular list directs you to add.

  • code(s) to identify all associated manifestations

Frequently Asked Questions (FAQ) & Clinical Guidance

Is an additional code needed with Q89.89?

Use additional code(s) to specify: code(s) to identify all associated manifestations.

Codes in This Family (12)

Official ICD-10-CM classifications in the same code family as Q89.89, with their registry titles.

  • Q89 — Other congenital malformations, not elsewhere classified
  • Q89.0 — Congenital absence and malformations of spleen
  • Q89.01 — Asplenia (congenital)
  • Q89.09 — Congenital malformations of spleen
  • Q89.1 — Congenital malformations of adrenal gland
  • Q89.2 — Congenital malformations of other endocrine glands
  • Q89.3 — Situs inversus
  • Q89.4 — Conjoined twins
  • Q89.7 — Multiple congenital malformations, not elsewhere classified
  • Q89.8 — Other specified congenital malformations
  • Q89.81 — Kabuki syndrome
  • Q89.9 — Congenital malformation, unspecified

Indexed Clinical Terms (28)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Absence (of) (organ or part) (complete or partial), organ, or site, congenital NEC
  • Acardia, acardius
  • Acardiacus amorphus
  • Accessory (congenital), genitourinary organs NEC
  • Acephalobrachia monster
  • Acephalochirus monster
  • Acephalogaster
  • Acephalostomus monster
  • Acephalothorax
  • Anomaly, anomalous (congenital) (unspecified type), specified organ or site NEC
  • Atresia, atretic, organ or site NEC
  • CHARGE association
  • Cyst (colloid) (mucous) (simple) (retention), congenital NEC
  • Disease, diseased, Kok
  • Disease, diseased, Startle
  • Goldberg syndrome
  • Hyperekplexia
  • Hyperexplexia
  • Malformation (congenital), specified NEC
  • Myofibromatosis, infantile
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital), Finnish type (congenital)
  • Syndrome, Borjeson Forssman Lehmann
  • Syndrome, CHARGE
  • Syndrome, Coffin-Lowry
  • Syndrome, Goldberg
  • Syndrome, Stickler
  • Syndrome, stiff baby
  • Teratencephalus

Related Codes & Numerical Sequence (Crawl Map)

Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:

ICD Code Q85.89 Other phakomatoses, not elsewhere classified
ICD Code Q87.89 Other specified congenital malformation syndromes, not elsewhere classified
ICD Code Q93.89 Other deletions from the autosomes
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