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Q89.89 ICD-10-CM Code: Other specified congenital malformations

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
1 use-additional code

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.

  • MS-DRG 564 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC (MDC 08)
  • MS-DRG 565 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC (MDC 08)
  • MS-DRG 566 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC (MDC 08)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q89.89 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on Q89.89 itself; “inherited from” names the category or block whose note applies here.

Use Additional Code

Supplementary codes the tabular list directs you to add.

  • Use additional code(s) to identify all associated manifestations

Source: inherited from Q89.8

Coder workflow for Q89.89

MedCoder structured workflow — derived from this code’s own official record

Before you code Q89.89

  1. “Other” (NEC) means the condition is specified in the record but no dedicated code captures it. Confirm the documented form is not one a sibling code names before settling on Q89.89; if the record states no specifics at all, the unspecified sibling applies instead. “Other” codes are for documented conditions the classification gives no specific code; “unspecified” codes are for records lacking the detail (Guidelines I.A.9.a, I.A.9.b).

    ReviewQ89.81

    See the relationships section · Guide: Other vs unspecified (NEC vs NOS) →

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
The conditions the Use Additional Code note names
Reported with this code when documented; a conditional instruction (“if applicable”, “if known”) applies only when the record supports it.
Any detail beyond this code’s title
What the record states that a more specific sibling code would capture — or its absence, which itself supports the unspecified code.

Official instructions as workflow

  • Use Additional Code — after identifying Q89.89(1 note)

    Coding workflow: Check whether the documentation supports the additional code(s) the note names, and report them with Q89.89 when it does. Where the instruction is conditional (“if applicable”, “if known”), it applies only when the record documents the condition.

    See the official tabular notes · Guidelines I.A.13

Coding decision scenarios

Pattern scenarios for this code’s structure — decision rules, not clinical cases

Documentation: A condition the Use Additional Code note names is documented.

Coding question: Is a second code reported with Q89.89?

Path: Review the Use Additional Code note and the code it names.

Reason: The additional code is reported when the record documents the condition; a conditional instruction applies only when its condition is met (Guidelines I.A.13).

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Code Overview

Other specified congenital malformations is a billable ICD-10-CM diagnosis code (Q89.89).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (28)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Verify Before Coding

  • CC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 39 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 3 MS-DRGs: DRG 564 (MDC 08), DRG 565 (MDC 08), DRG 566 (MDC 08).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MAL010 — Other specified and unspecified congenital anomalies (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical process (MS-DRG)

Acts as CC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

Q87.5 — Other congenital malformation syndromes with other skeletal changes, Q87.81 — Alport syndrome, Q87.82 — Arterial tortuosity syndrome, Q87.83 — Bardet-Biedl syndrome, Q87.84 — Laurence-Moon syndrome, Q87.85 — MED13L syndrome, Q87.86 — Kleefstra syndrome, Q87.87 — Hao-Fountain Syndrome, Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified, Q89.81 — Kabuki syndrome, Q99.2 — Fragile X chromosome, Q99.811 — Usher syndrome, type 1, Q99.812 — Usher syndrome, type 2, Q99.813 — Usher syndrome, type 3, Q99.818 — Other Usher syndrome, Q99.819 — Usher syndrome, unspecified, QA0.0101 — SCN2A-related neurodevelopmental disorder, QA0.0102 — CACNA1A-related neurodevelopmental disorder, QA0.0109 — Neurodevelopmental disorder related to pathogenic variant in other ion channel gene, QA0.011 — Neurodevelopmental disorders, related to pathogenic variants in glutamate receptor genes, +18 more

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Other specified and unspecified congenital anomalies).

Q87.43 — Marfan syndrome with skeletal manifestation, Q87.5 — Other congenital malformation syndromes with other skeletal changes, Q87.81 — Alport syndrome, Q87.82 — Arterial tortuosity syndrome, Q87.83 — Bardet-Biedl syndrome, Q87.84 — Laurence-Moon syndrome, Q87.85 — MED13L syndrome, Q87.87 — Hao-Fountain Syndrome, Q87.88 — CTNNB1 syndrome, Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified, Q89.01 — Asplenia (congenital), Q89.09 — Congenital malformations of spleen, Q89.1 — Congenital malformations of adrenal gland, Q89.2 — Congenital malformations of other endocrine glands, Q89.3 — Situs inversus, Q89.4 — Conjoined twins, Q89.7 — Multiple congenital malformations, not elsewhere classified, Q89.8 — Other specified congenital malformations, Q89.81 — Kabuki syndrome, Q89.9 — Congenital malformation, unspecified, +59 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Accessory”, “Anomaly, anomalous”, “Absence”, …; these codes share that main term but sit in a different category of the Tabular List.

Q83.1 — Accessory breast (breast tissue, axilla), Q83.2 — Absent nipple (nipple, congenital), Q83.3 — Accessory nipple (nipple), Q83.8 — Other congenital malformations of breast (breast, congenital), Q83.9 — Congenital malformation of breast, unspecified (breast), Q84.2 — Other congenital malformations of hair (hair), Q84.6 — Other congenital malformations of nails (nail), Q84.8 — Other specified congenital malformations of integument (integument, specified type NEC), Q84.9 — Congenital malformation of integument, unspecified (integument), Q87.5 — Other congenital malformation syndromes with other skeletal changes (affecting multiple systems with skeletal changes NEC), Q92.5 — Duplications with other complex rearrangements (chromosome, with complex rearrangements NEC), Q92.8 — Other specified trisomies and partial trisomies of autosomes (chromosome, with complex rearrangements NEC, seen only at prometaphase), Q92.9 — Trisomy and partial trisomy of autosomes, unspecified (chromosome), Q96.9 — Turner's syndrome, unspecified (chromosomes, chromosomal, sex, Turner's), Q97.8 — Other specified sex chromosome abnormalities, female phenotype (sex chromosome, female phenotype), Q98.4 — Klinefelter syndrome, unspecified (chromosomes, chromosomal, sex, Klinefelter's), Q98.8 — Other specified sex chromosome abnormalities, male phenotype (sex chromosome, male phenotype), Q98.9 — Sex chromosome abnormality, male phenotype, unspecified (sex chromosomes NEC, male phenotype), Q99.1 — 46, XX true hermaphrodite (chromosomes, chromosomal, sex, gonadal dysgenesis), Q99.8 — Other specified chromosome abnormalities (chromosomes, chromosomal, specified NEC), +683 more

Contextual Map

Every relationship of Q89.89 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Hierarchy

Clinical classification (CCSR)

MS-DRG Grouper

MDC crossing

  • MDC 08 — Diseases and Disorders of the Musculoskeletal System and Connective Tissue[MDC crossing]: “Diseases and Disorders of the Musculoskeletal System and Connective Tissue — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 18,508 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries (28)

  • Absence (of) (organ or part) (complete or partial), organ, or site, congenital NEC[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Acardia, acardius[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Acardiacus amorphus[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Accessory (congenital), genitourinary organs NEC[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Acephalobrachia monster[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Acephalochirus monster[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Acephalogaster[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Acephalostomus monster[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • and 20 more

Nearest codes (12)

Change history

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "Q89.89 — Other specified congenital malformations." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/q89.89-other-specified-congenital-malformations

Change history

  • FY2026 — October 1, 2025
    Added to the code set
    Other specified congenital malformations
    FY2026 changes

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q89.89 in its code family, with their registry titles.

View all codes in the Q89 family