Q87.86 is the authoritative medical code for Kleefstra syndrome. This classification is used in medical billing and clinical recording to specify the clinical criteria for kleefstra syndrome (ICD-10-CM Q87.86), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Kleefstra syndrome is a billable ICD-10-CM diagnosis code Q87.86. Excludes1 (not coded here): Zellweger syndrome E71.510. Use additional code: code(s) to identify all associated manifestations.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for Q87.86 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- Zellweger syndrome E71.510
Use Additional Code
Supplementary codes the tabular list directs you to add.
- code(s) to identify all associated manifestations
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with Q87.86?
Per Excludes1 instructions, Q87.86 must not be reported with: Zellweger syndrome (E71.510).
Is an additional code needed with Q87.86?
Use additional code(s) to specify: code(s) to identify all associated manifestations.
Codes in This Family (25)
Official ICD-10-CM classifications in the same code family as Q87.86, with their registry titles.
- Q87 — Other specified congenital malformation syndromes affecting multiple systems
- Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
- Q87.1 — Congenital malformation syndromes predominantly associated with short stature
- Q87.11 — Prader-Willi syndrome
- Q87.19 — Other congenital malformation syndromes predominantly associated with short stature
- Q87.2 — Congenital malformation syndromes predominantly involving limbs
- Q87.3 — Congenital malformation syndromes involving early overgrowth
- Q87.4 — Marfan syndrome
- Q87.40 — Marfan syndrome, unspecified
- Q87.41 — Marfan syndrome with cardiovascular manifestations
- Q87.410 — Marfan syndrome with aortic dilation
- Q87.418 — Marfan syndrome with other cardiovascular manifestations
- Q87.42 — Marfan syndrome with ocular manifestations
- Q87.43 — Marfan syndrome with skeletal manifestation
- Q87.5 — Other congenital malformation syndromes with other skeletal changes
- Q87.8 — Other specified congenital malformation syndromes, not elsewhere classified
- Q87.81 — Alport syndrome
- Q87.82 — Arterial tortuosity syndrome
- Q87.83 — Bardet-Biedl syndrome
- Q87.84 — Laurence-Moon syndrome
- Q87.85 — MED13L syndrome
- Q87.87 — Hao-Fountain Syndrome
- Q87.88 — CTNNB1 syndrome
- Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified
- Q87.A — Loeys-Dietz syndrome
Indexed Clinical Terms (1)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: