Q87 ICD-10-CM Code: Other specified congenital malformation syndromes affecting multiple systems
Compare with another codeCheck this code on a claim
Billing Status: NO. This is a non-billable ICD-10-CM code: report a more specific billable code beneath it.
Coding at a Glance
- Tabular directives
- 1 use-additional code
Category · FY2027A non-billable heading in the tabular list: report a more specific code beneath it.
What you need to know
Source: CMS/NCHS Official ICD-10-CM tabular notes, quoted. From the CMS/NCHS tabular list for the release in force. A note the category or block publishes applies to this code too; the Instructions section marks which is which.
- Use additional codeReport with this code when documented
- code(s) to identify all associated manifestations
Most relevant related codes MedCoder-derived
- Q87.0Congenital malformation syndromes predominantly affecting facial appearanceMore specific code
- Q87.1Congenital malformation syndromes predominantly associated with short statureMore specific code
- Q87.11Prader-Willi syndromeMore specific code
- Q87.19Other congenital malformation syndromes predominantly associated with short statureMore specific code
- Q87.2Congenital malformation syndromes predominantly involving limbsMore specific code
- Q87.3Congenital malformation syndromes involving early overgrowthMore specific code
Read off the official notes above and this code’s own position in the tabular list. Which to report is a documentation question; Compare shows the two side by side.
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q87 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2027Effective: October 1, 2026
Trace:FY2027 changesChange historyRelease, file and checksum
Use Additional Code
Supplementary codes the tabular list directs you to add.
- Use additional code(s) to identify all associated manifestations
Coder workflow for Q87
MedCoder structured workflow — derived from this code’s own official record
Before you code Q87
- Q87 is not reportable as written. Select the more specific code beneath it that the documentation supports. Codes are reported to the highest level of specificity the classification provides (Guidelines I.B.2).
ReviewQ87.0, Q87.1, Q87.2, Q87.3, Q87.4, Q87.5, Q87.8, Q87.A
See the relationships section · Guide: How to choose an ICD-10-CM code →
- “Other” (NEC) means the condition is specified in the record but no dedicated code captures it. Confirm the documented form is not one a sibling code names before settling on Q87; if the record states no specifics at all, the unspecified sibling applies instead. “Other” codes are for documented conditions the classification gives no specific code; “unspecified” codes are for records lacking the detail (Guidelines I.A.9.a, I.A.9.b).
See the relationships section · Guide: Other vs unspecified (NEC vs NOS) →
Choose the right path
- Does the documentation support one of the more specific codes beneath Q87?
Yes → Select that code and continue the checks below on its own page.
No → Q87 cannot be reported as written; query for the specificity its subcategory needs.ReviewQ87.0, Q87.1, Q87.2, Q87.3, Q87.4, Q87.5, Q87.8, Q87.A
Consider Q87. Then work the Use Additional Code note, and confirm the code is valid for the date of service in the Verify section.
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
- The conditions the Use Additional Code note names
- Reported with this code when documented; a conditional instruction (“if applicable”, “if known”) applies only when the record supports it.
- Any detail beyond this code’s title
- What the record states that a more specific sibling code would capture — or its absence, which itself supports the unspecified code.
Official instructions as workflow
Use Additional Code — after identifying Q87(1 note)
Coding workflow: Check whether the documentation supports the additional code(s) the note names, and report them with Q87 when it does. Where the instruction is conditional (“if applicable”, “if known”), it applies only when the record documents the condition.
See the official tabular notes · Guidelines I.A.13
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: A condition the Use Additional Code note names is documented.
Coding question: Is a second code reported with Q87?
Path: Review the Use Additional Code note and the code it names.
Reason: The additional code is reported when the record documents the condition; a conditional instruction applies only when its condition is met (Guidelines I.A.13).
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Coding context
Guidelines, coding notes, decision aids, relationships (with MS-DRG and CCSR classification), hierarchy, HCC, coverage and the context map: what a coder reaches for after the core. Each section names whether it is official source data, a MedCoder-derived relationship or MedCoder editorial.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Verify Before Coding
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder-derived relationships — computed from published CMS and AHRQ datasets
Other codes that name Q87 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.
Referenced by 1 Excludes1 note: Q89.7 — Multiple congenital malformations, not elsewhere classified.
These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.
Contextual Map
Every relationship of Q87 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Run Q87 with this related code in Claim Check
Hierarchy
- Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q80-Q89 — Other congenital malformations[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
Referenced by Excludes1 notes
- Q89.7 — Multiple congenital malformations, not elsewhere classified[Excludes1]: “congenital malformation syndromes affecting multiple systems (Q87.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
Nearest codes (25)
- Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q87.1 — Congenital malformation syndromes predominantly associated with short stature[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q87.11 — Prader-Willi syndrome[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q87.19 — Other congenital malformation syndromes predominantly associated with short stature[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q87.2 — Congenital malformation syndromes predominantly involving limbs[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q87.3 — Congenital malformation syndromes involving early overgrowth[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q87.4 — Marfan syndrome[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q87.40 — Marfan syndrome, unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- and 17 more
Change history
- FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016
Reference
Index terms and tables, published questions and FAQ, every source behind this page with its release and checksum, the date-of-service check and the complete change history.
Common coding questions
MedCoder editorial
Can Q87 be billed directly?
No. Q87 (Other specified congenital malformation syndromes affecting multiple systems) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder-derived relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder editorial explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Current data releases:ICD-10-CM FY2027 · ICD-10-PCS FY2027 · HCPCS October 2026 · MS-DRG v44 · Medicare Code Editor v44.0 · NCCI PTP Q4 2026 · MUE Q4 2026 · NCD code lists 2026-01 · LCD export September 28, 2026 · All releases and sources
Labels on this page: Official source data · MedCoder-derived relationship · MedCoder editorial explanation. How to read the labels · All data sources and release dates · CMS coding rules
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "Q87 — Other specified congenital malformation syndromes affecting multiple systems." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/q87-other-specified-congenital-malformation-syndromes-affecting-multiple-systems
Change history
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionOther specified congenital malformation syndromes affecting multiple systems
No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027, and none are recorded for this code. Note changes are tracked from FY2027 only.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q87 in its code family, with their registry titles.
- Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
- Q87.1 — Congenital malformation syndromes predominantly associated with short stature
- Q87.11 — Prader-Willi syndrome
- Q87.19 — Other congenital malformation syndromes predominantly associated with short stature
- Q87.2 — Congenital malformation syndromes predominantly involving limbs
- Q87.3 — Congenital malformation syndromes involving early overgrowth
- Q87.4 — Marfan syndrome
- Q87.40 — Marfan syndrome, unspecified
- Q87.41 — Marfan syndrome with cardiovascular manifestations
- Q87.410 — Marfan syndrome with aortic dilation
- Q87.418 — Marfan syndrome with other cardiovascular manifestations
- Q87.42 — Marfan syndrome with ocular manifestations
- Q87.43 — Marfan syndrome with skeletal manifestation
- Q87.5 — Other congenital malformation syndromes with other skeletal changes
- Q87.8 — Other specified congenital malformation syndromes, not elsewhere classified
- Q87.81 — Alport syndrome
- Q87.82 — Arterial tortuosity syndrome
- Q87.83 — Bardet-Biedl syndrome
- Q87.84 — Laurence-Moon syndrome
- Q87.85 — MED13L syndrome
- Q87.86 — Kleefstra syndrome
- Q87.87 — Hao-Fountain Syndrome
- Q87.88 — CTNNB1 syndrome
- Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified
- Q87.A — Loeys-Dietz syndrome