ICD-10/Q87.42

Q87.42 ICD 2026 Code: Marfan syndrome with ocular manifestations

Q87.42 is the authoritative medical code for Marfan syndrome with ocular manifestations. This classification is used in medical billing and clinical recording to specify the clinical criteria for marfan syndrome with ocular manifestations (ICD-10-CM Q87.42), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Marfan syndrome with ocular manifestations is a billable ICD-10-CM diagnosis code Q87.42. Use additional code: code(s) to identify all associated manifestations.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for Q87.42 in the official ICD-10-CM tabular list.

Use Additional Code

Supplementary codes the tabular list directs you to add.

  • code(s) to identify all associated manifestations

Frequently Asked Questions (FAQ) & Clinical Guidance

Is an additional code needed with Q87.42?

Use additional code(s) to specify: code(s) to identify all associated manifestations.

Codes in This Family (25)

Official ICD-10-CM classifications in the same code family as Q87.42, with their registry titles.

  • Q87 — Other specified congenital malformation syndromes affecting multiple systems
  • Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
  • Q87.1 — Congenital malformation syndromes predominantly associated with short stature
  • Q87.11 — Prader-Willi syndrome
  • Q87.19 — Other congenital malformation syndromes predominantly associated with short stature
  • Q87.2 — Congenital malformation syndromes predominantly involving limbs
  • Q87.3 — Congenital malformation syndromes involving early overgrowth
  • Q87.4 — Marfan syndrome
  • Q87.40 — Marfan syndrome, unspecified
  • Q87.41 — Marfan syndrome with cardiovascular manifestations
  • Q87.410 — Marfan syndrome with aortic dilation
  • Q87.418 — Marfan syndrome with other cardiovascular manifestations
  • Q87.43 — Marfan syndrome with skeletal manifestation
  • Q87.5 — Other congenital malformation syndromes with other skeletal changes
  • Q87.8 — Other specified congenital malformation syndromes, not elsewhere classified
  • Q87.81 — Alport syndrome
  • Q87.82 — Arterial tortuosity syndrome
  • Q87.83 — Bardet-Biedl syndrome
  • Q87.84 — Laurence-Moon syndrome
  • Q87.85 — MED13L syndrome
  • Q87.86 — Kleefstra syndrome
  • Q87.87 — Hao-Fountain Syndrome
  • Q87.88 — CTNNB1 syndrome
  • Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified
  • Q87.A — Loeys-Dietz syndrome

Indexed Clinical Terms (1)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Syndrome, Marfan, with, ocular manifestations

Related Codes & Numerical Sequence (Crawl Map)

Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:

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