Q87.1 is the authoritative medical code for Congenital malformation syndromes predominantly associated with short stature. This classification is used in medical billing and clinical recording to specify the clinical criteria for congenital malformation syndromes predominantly associated with short stature (ICD-10-CM Q87.1), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: NO. This is a clinician non-billable / parent hierarchy grouping in the ICD-10-CM system.
Official Registry Overview & Definition
Congenital malformation syndromes predominantly associated with short stature is a non-billable ICD-10-CM category code Q87.1. A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): Ellis-van Creveld syndrome Q77.6; Smith-Lemli-Opitz syndrome E78.72. Use additional code: code(s) to identify all associated manifestations.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for Q87.1 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- Ellis-van Creveld syndrome Q77.6
- Smith-Lemli-Opitz syndrome E78.72
Use Additional Code
Supplementary codes the tabular list directs you to add.
- code(s) to identify all associated manifestations
Frequently Asked Questions (FAQ) & Clinical Guidance
Can Q87.1 be billed directly?
No. Q87.1 (Congenital malformation syndromes predominantly associated with short stature) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.
What can't be coded together with Q87.1?
Per Excludes1 instructions, Q87.1 must not be reported with: Ellis-van Creveld syndrome (Q77.6); Smith-Lemli-Opitz syndrome (E78.72).
Is an additional code needed with Q87.1?
Use additional code(s) to specify: code(s) to identify all associated manifestations.
Codes in This Family (24)
Official ICD-10-CM classifications in the same code family as Q87.1, with their registry titles.
- Q87 — Other specified congenital malformation syndromes affecting multiple systems
- Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
- Q87.11 — Prader-Willi syndrome
- Q87.19 — Other congenital malformation syndromes predominantly associated with short stature
- Q87.2 — Congenital malformation syndromes predominantly involving limbs
- Q87.3 — Congenital malformation syndromes involving early overgrowth
- Q87.4 — Marfan syndrome
- Q87.40 — Marfan syndrome, unspecified
- Q87.41 — Marfan syndrome with cardiovascular manifestations
- Q87.410 — Marfan syndrome with aortic dilation
- Q87.418 — Marfan syndrome with other cardiovascular manifestations
- Q87.42 — Marfan syndrome with ocular manifestations
- Q87.43 — Marfan syndrome with skeletal manifestation
- Q87.5 — Other congenital malformation syndromes with other skeletal changes
- Q87.8 — Other specified congenital malformation syndromes, not elsewhere classified
- Q87.81 — Alport syndrome
- Q87.82 — Arterial tortuosity syndrome
- Q87.83 — Bardet-Biedl syndrome
- Q87.84 — Laurence-Moon syndrome
- Q87.85 — MED13L syndrome
- Q87.86 — Kleefstra syndrome
- Q87.87 — Hao-Fountain Syndrome
- Q87.88 — CTNNB1 syndrome
- Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:
ICD Code Q84.1
Congenital morphological disturbances of hair, not elsewhere classified
ICD Code Q92.1
Whole chromosome trisomy, mosaicism (mitotic nondisjunction)