Q87.2 is the authoritative medical code for Congenital malformation syndromes predominantly involving limbs. This classification is used in medical billing and clinical recording to specify the clinical criteria for congenital malformation syndromes predominantly involving limbs (ICD-10-CM Q87.2), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Congenital malformation syndromes predominantly involving limbs is a billable ICD-10-CM diagnosis code Q87.2. Inclusion terms: Holt-Oram syndrome; Klippel-Trenaunay-Weber syndrome; Nail patella syndrome; Rubinstein-Taybi syndrome; Sirenomelia syndrome; Thrombocytopenia with absent radius TAR syndrome; VATER syndrome. Use additional code: code(s) to identify all associated manifestations.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for Q87.2 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Holt-Oram syndrome
- Klippel-Trenaunay-Weber syndrome
- Nail patella syndrome
- Rubinstein-Taybi syndrome
- Sirenomelia syndrome
- Thrombocytopenia with absent radius TAR syndrome
- VATER syndrome
Use Additional Code
Supplementary codes the tabular list directs you to add.
- code(s) to identify all associated manifestations
Frequently Asked Questions (FAQ) & Clinical Guidance
Is an additional code needed with Q87.2?
Use additional code(s) to specify: code(s) to identify all associated manifestations.
What conditions are included under Q87.2?
Congenital malformation syndromes predominantly involving limbs includes: Holt-Oram syndrome; Klippel-Trenaunay-Weber syndrome; Nail patella syndrome; Rubinstein-Taybi syndrome; Sirenomelia syndrome.
Codes in This Family (9)
Official ICD-10-CM classifications in the same code family as Q87.2, with their registry titles.
- Q87 — Other specified congenital malformation syndromes affecting multiple systems
- Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
- Q87.1 — Congenital malformation syndromes predominantly associated with short stature
- Q87.3 — Congenital malformation syndromes involving early overgrowth
- Q87.4 — Marfan syndrome
- Q87.410 — Marfan syndrome with aortic dilation
- Q87.418 — Marfan syndrome with other cardiovascular manifestations
- Q87.5 — Other congenital malformation syndromes with other skeletal changes
- Q87.8 — Other specified congenital malformation syndromes, not elsewhere classified
Indexed Clinical Terms (23)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Fong's syndrome (hereditary osteo-onychodysplasia)
- Holt-Oram syndrome
- Klippel-Trenaunaysyndrome (-Weber)
- Mietens' syndrome
- Nail, patella syndrome
- Onycho-osteodysplasia
- Osteo-onycho-arthro-dysplasia
- Osteo-onychodysplasia, hereditary
- Österreicher-Turner syndrome
- Rubinstein-Taybi syndrome
- Sirenomelia (syndrome)
- Syndrome, Fong's
- Syndrome, nail patella
- Syndrome, Osterreicher-Turner
- Syndrome, sirenomelia
- Syndrome, TAR (thrombocytopenia with absent radius)
- Syndrome, thrombocytopenia with absent radius (TAR)
- Syndrome, VATER
- TARsyndrome (thrombocytopenia with absent radius)
- Taybi's syndrome
- Thrombocytopenia, thrombocytopenic, with absent radius (TAR)
- Turner-Kieser syndrome
- VATER syndrome
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: