ICD-10/Q87.40

Q87.40 ICD 2026 Code: Marfan syndrome, unspecified

Q87.40 is the authoritative medical code for Marfan syndrome, unspecified. This classification is used in medical billing and clinical recording to specify the clinical criteria for marfan syndrome, unspecified (ICD-10-CM Q87.40), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Marfan syndrome, unspecified is a billable ICD-10-CM diagnosis code Q87.40. Use additional code: code(s) to identify all associated manifestations.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for Q87.40 in the official ICD-10-CM tabular list.

Use Additional Code

Supplementary codes the tabular list directs you to add.

  • code(s) to identify all associated manifestations

Frequently Asked Questions (FAQ) & Clinical Guidance

Is an additional code needed with Q87.40?

Use additional code(s) to specify: code(s) to identify all associated manifestations.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q87.40 in its code family, with their registry titles.

  • Q87 — Other specified congenital malformation syndromes affecting multiple systems
  • Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
  • Q87.1 — Congenital malformation syndromes predominantly associated with short stature
  • Q87.11 — Prader-Willi syndrome
  • Q87.19 — Other congenital malformation syndromes predominantly associated with short stature
  • Q87.2 — Congenital malformation syndromes predominantly involving limbs
  • Q87.3 — Congenital malformation syndromes involving early overgrowth
  • Q87.4 — Marfan syndrome
  • Q87.41 — Marfan syndrome with cardiovascular manifestations
  • Q87.410 — Marfan syndrome with aortic dilation

View all 25 codes in the Q87 family

Indexed Clinical Terms (2)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Syndrome, Beals
  • Syndrome, Marfan