Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Inpatient Payment Groups (MS-DRG)

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0 (FY2026), Appendix B.

MS-DRG 564 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC (MDC 08)
MS-DRG 565 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC (MDC 08)
MS-DRG 566 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC (MDC 08)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Official Registry Overview & Definition

Other specified congenital malformation syndromes, not elsewhere classified is a billable ICD-10-CM diagnosis code (Q87.89).

Sequencing, inclusion, and exclusion notes published for Q87.89 in the official ICD-10-CM tabular list.

Conditions that can never be reported with this code; the two are mutually exclusive.

Supplementary codes the tabular list directs you to add.

Official ICD-10-CM classifications closest to Q87.89 in its code family, with their registry titles.

Q87.8 — Other specified congenital malformation syndromes, not elsewhere classified
Q87.81 — Alport syndrome
Q87.82 — Arterial tortuosity syndrome
Q87.83 — Bardet-Biedl syndrome
Q87.84 — Laurence-Moon syndrome
Q87.85 — MED13L syndrome
Q87.86 — Kleefstra syndrome
Q87.87 — Hao-Fountain Syndrome
Q87.88 — CTNNB1 syndrome
Q87.A — Loeys-Dietz syndrome

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.