Skip to main content

QA0.011 ICD-10-CM Code: Neurodevelopmental disorders, related to pathogenic variants in glutamate receptor genes

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
7 code-also instructions

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.

  • MS-DRG 564 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC (MDC 08)
  • MS-DRG 565 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC (MDC 08)
  • MS-DRG 566 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC (MDC 08)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for QA0.011 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on QA0.011 itself; “inherited from” names the category or block whose note applies here.

Code Also

Additional codes that may be required to fully describe the encounter.

  • Code also, if applicable, any associated conditions, such as:
  • attention-deficit hyperactivity disorders (F90.-)
  • autism spectrum disorder (F84.0)
  • developmental and epileptic encephalopathy (G93.45)
  • epilepsy, by specific type (G40.-)
  • intellectual disabilities (F70-F79)
  • pervasive developmental disorders (F84.-)

Source: inherited from QA0

Coder workflow for QA0.011

MedCoder structured workflow — derived from this code’s own official record

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).

Official instructions as workflow

  • Code Also — related condition(7 notes)

    Coding workflow: Review the related condition when both are documented and the instruction applies. A Code Also note does not fix sequencing; the order follows the circumstances of the encounter.

    ReviewF90, F84.0, G93.45, G40, F84

    See the official tabular notes · Guidelines I.A.17

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Code Overview

Neurodevelopmental disorders, related to pathogenic variants in glutamate receptor genes is a billable ICD-10-CM diagnosis code (QA0.011).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (10)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Verify Before Coding

  • CC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 39 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 3 MS-DRGs: DRG 564 (MDC 08), DRG 565 (MDC 08), DRG 566 (MDC 08).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Related Codes

Same clinical process (MS-DRG)

Acts as CC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

Q89.81 — Kabuki syndrome, Q89.89 — Other specified congenital malformations, Q99.2 — Fragile X chromosome, Q99.811 — Usher syndrome, type 1, Q99.812 — Usher syndrome, type 2, Q99.813 — Usher syndrome, type 3, Q99.818 — Other Usher syndrome, Q99.819 — Usher syndrome, unspecified, QA0.0101 — SCN2A-related neurodevelopmental disorder, QA0.0102 — CACNA1A-related neurodevelopmental disorder, QA0.0109 — Neurodevelopmental disorder related to pathogenic variant in other ion channel gene, QA0.012 — Neurodevelopmental disorders, related to pathogenic variants in other receptor genes, QA0.0131 — SLC6A1-related disorder, QA0.0139 — Neurodevelopmental disorder, related to pathogenic variant in other transporter or solute carrier gene, QA0.0141 — Syntaxin-binding protein 1-related disorder, QA0.0142 — DLG4-related synaptopathy, QA0.0149 — Neurodevelopmental disorder, related to pathogenic variant in other synapse related gene, QA0.0151 — FOXG1 syndrome, QA0.0159 — Neurodevelopmental disorder, related to other genes associated with transcription and gene expression, QA0.8 — Other neurodevelopmental disorders related to pathogenic variants in other specific genes, +18 more

Contextual Map

Every relationship of QA0.011 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Hierarchy

MS-DRG Grouper

MDC crossing

  • MDC 08 — Diseases and Disorders of the Musculoskeletal System and Connective Tissue[MDC crossing]: “Diseases and Disorders of the Musculoskeletal System and Connective Tissue — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 18,508 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries (10)

  • Disorder (of), neurodevelopmental, GRIA1-related[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Disorder (of), neurodevelopmental, GRIA2-related[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Disorder (of), neurodevelopmental, GRIA3-related[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Disorder (of), neurodevelopmental, GRIA4-related[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Disorder (of), neurodevelopmental, GRIK2-related[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Disorder (of), neurodevelopmental, GRIN1-related[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Disorder (of), neurodevelopmental, GRIN2A-related[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Disorder (of), neurodevelopmental, GRIN2B-related[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • and 2 more

Nearest codes (19)

Change history

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "QA0.011 — Neurodevelopmental disorders, related to pathogenic variants in glutamate receptor genes." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/qa0.011-neurodevelopmental-disorders-related-to-pathogenic-variants-in-glutamate-receptor-genes

Change history

  • FY2026 — October 1, 2025
    Added to the code set
    Neurodevelopmental disorders, related to pathogenic variants in glutamate receptor genes
    FY2026 changes

Nearest Codes in This Family

Official ICD-10-CM classifications closest to QA0.011 in its code family, with their registry titles.

View all codes in the QA0 family