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E70 vs G71.038

E70 (Disorders of aromatic amino-acid metabolism) compared with G71.038 (Other limb girdle muscular dystrophy), from the official CMS tabular data.

Current data releases:ICD-10-CM FY2027 · ICD-10-PCS FY2027 · HCPCS October 2026 · MS-DRG v44 · Medicare Code Editor v44.0 · NCCI PTP Q4 2026 · MUE Q4 2026 · NCD code lists 2026-01 · LCD export September 28, 2026 · All releases and sources

Summary

These codes can be reported together when both conditions are documented, because G71.038 lists E70 under Excludes2, which marks them as distinct conditions.

Official rule
What is different?

The conditions named, billing status and chapter.E70 is “Disorders of aromatic amino-acid metabolism”; G71.038 is “Other limb girdle muscular dystrophy”. E70 is a non-billable header; G71.038 is billable. E70 sits in E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89); G71.038 in G00-G99 — Diseases of the Nervous System (G00-G99).

Registry fact

Can these codes be reported together?

Yes, when both are documented.G71.038 lists E70 under Excludes2: “metabolic disorders (E70-E88)”. Excludes2 marks distinct conditions that may both be reported when both are documented.

Official ruleGuide: Excludes1 vs Excludes2

Is there an Excludes1 relationship?

None.Neither entry carries an Excludes1 note that names the other code. E70 carries 5 Excludes1 notes covering other codes; the side-by-side table quotes them.

Official rule

Is there an Excludes2 relationship?

Yes.G71.038’s tabular entry: “metabolic disorders (E70-E88)”. The note covers E70.

Official ruleGuide: Excludes1 vs Excludes2

Is one more specific?

Not comparable.The codes sit in different categories; specificity is only comparable within one category.

Is one a parent or header code?

One is a header.E70 is a non-billable header, but G71.038 is not one of its subdivisions.

Registry fact

Are there sequencing instructions?

None.Neither entry carries a Code First or Use Additional Code note that names the other.

Official rule

Are there other coding relationships?

None found.No laterality, encounter-phase, Table of Neoplasms, Table of Drugs and Chemicals, or history-versus-active-disease relationship links these codes.

MedCoder-derived

Official rule: a tabular instructional note or a section of the ICD-10-CM Official Guidelines, quoted as published. Registry fact: the codes’ own published attributes (titles, billable status, position in the hierarchy, code set). MedCoder-derived: a reading MedCoder computes from those facts; it is not itself a rule. How to read the labels

Can these codes be reported together?

Informational

Excludes2 relationship

G71.038
Other limb girdle muscular dystrophy
↔
E70
Disorders of aromatic amino-acid metabolism

What we found

Yes, when both are documented.G71.038 carries an Excludes2 note covering E70: “metabolic disorders (E70-E88)”

Excludes2 marks distinct conditions — both may be reported when both are documented.

What to review

Report both only when the documentation supports both conditions; otherwise report the one documented.

Guide: Excludes1 vs Excludes2Check these on a claim

Why it matters

An Excludes2 note means the excluded condition is not part of the code above it, but a patient can have both. Report both when both are documented.

Source / rule

CMS ICD-10-CM tabular instructional notes

Official guidance behind these answers

  • Section I.A.12.b — Excludes2 · applies to: Excludes2

    A type 2 Excludes note represents “Not included here.” An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

    ICD-10-CM Official Guidelines FY2027

Quoted from the ICD-10-CM Official Guidelines for Coding and Reporting in effect for the release shown. The tabular notes above are the code-level instruction; these sections are the convention that says how such a note is applied. Source document (CMS PDF) · Release and checksum

Side by side

Similar descriptions do not make codes interchangeable. The documentation and the official instructions decide which code applies.

Official descriptionDiffers
E70

Disorders of aromatic amino-acid metabolism

G71.038

Other limb girdle muscular dystrophy

StatusDiffers
E70
Non-billable header

A header is not reported on a claim; a code beneath it is.

Report instead: E70.0, E70.1, E70.20, E70.21, E70.29

G71.038
Billable
Excludes1Differs
E70
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
G71.038

None at this code

Excludes2Differs
E70
  • Ehlers-Danlos syndromes (Q79.6-)
G71.038
  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)
CategoryDiffers
E70

Is itself a category

G71.038

G71 Primary disorders of muscles

ChapterDiffers
E70

E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89)

G71.038

G00-G99 — Diseases of the Nervous System (G00-G99)

IncludesDiffers
E70

None at this code

G71.038
  • LGMD R22 collagen 6-related
  • Other autosomal recessive limb girdle muscular dystrophy

No Code first, Use additional code, Code also and 7th character note at either code.

Notes are the code’s own tabular entry, quoted as published. A note that names the other code is the one the verdict above rests on. In a row that differs, notes every code shares are dimmed.

Derived from the official CMS ICD-10-CM tabular data (FY2027). A coding-rule comparison, not billing advice: payer-specific edits and medical-necessity policy are outside its scope. All data sources