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G71.038 ICD-10-CM Code: Other limb girdle muscular dystrophy

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Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
2 inclusion terms · 3 Excludes2
Risk adjustment
CMS-HCC V28: 1 category · CMS-HCC V22 category 76

Billable · FY2027A valid, specific ICD-10-CM code, reportable for dates of service in FY2027.

What you need to know

Source: CMS/NCHS Official ICD-10-CM tabular notes, quoted. From the CMS/NCHS tabular list for the release in force. A note the category or block publishes applies to this code too; the Instructions section marks which is which.

Excludes2Not included here; may be reported together
  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)
IncludesWhat this code covers
  • LGMD R22 collagen 6-related
  • Other autosomal recessive limb girdle muscular dystrophy

Most relevant related codes MedCoder-derived

Read off the official notes above and this code’s own position in the tabular list. Which to report is a documentation question; Compare shows the two side by side.

CompareCheck ClaimView Related Codes

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v44, Appendix B.

  • MS-DRG 091 — OTHER DISORDERS OF NERVOUS SYSTEM WITH MCC (MDC 01)
  • MS-DRG 092 — OTHER DISORDERS OF NERVOUS SYSTEM WITH CC (MDC 01)
  • MS-DRG 093 — OTHER DISORDERS OF NERVOUS SYSTEM WITHOUT CC/MCC (MDC 01)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Risk Adjustment (CMS-HCC)

Payment categories this diagnosis maps to under CMS-HCC V28, payment year 2026.

  • HCC 197 — Muscular Dystrophy

Other models: CMS-HCC V22 HCC 76

Risk scores depend on the enrollee's full accepted diagnosis set and segment; a category mapping alone does not determine payment.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for G71.038 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2027Effective: October 1, 2026

Trace:FY2027 changesChange historyRelease, file and checksum

Notes without a marker are published on G71.038 itself; “inherited from” names the category or block whose note applies here.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • LGMD R22 collagen 6-related
  • Other autosomal recessive limb girdle muscular dystrophy

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

Source: inherited from G71

Coder workflow for G71.038

MedCoder structured workflow — derived from this code’s own official record

Before you code G71.038

  1. “Other” (NEC) means the condition is specified in the record but no dedicated code captures it. Confirm the documented form is not one a sibling code names before settling on G71.038; if the record states no specifics at all, the unspecified sibling applies instead. “Other” codes are for documented conditions the classification gives no specific code; “unspecified” codes are for records lacking the detail (Guidelines I.A.9.a, I.A.9.b).

    ReviewG71.031, G71.032, G71.033, G71.034, G71.035, G71.036

    See the relationships section · Guide: Other vs unspecified (NEC vs NOS) →

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
Any detail beyond this code’s title
What the record states that a more specific sibling code would capture — or its absence, which itself supports the unspecified code.

Official instructions as workflow

  • Excludes2 — not part of G71.038(3 notes)

    Coding workflow: The conditions named in this note are not included in G71.038. When the record documents both, both may be reported; the note is a boundary, not a prohibition.

    CompareQ74.3, M60

    See the official tabular notes · Guidelines I.A.12.b

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Don’t confuse G71.038 with…

MedCoder analysis — pairs from this code’s official notes, distinctions written by MedCoder

The codes most likely to be picked instead of G71.038 — named in its own official notes, or sharing its laterality or encounter family — with what separates them and which documentation moves the case. Each links to the full comparison.

  • G71.039— Specificity relationship (Review)

    Overlapping diagnoses in the same category.

    Overlapping codes in the same category — the documentation decides which is the more specific fit.

    What moves you there: A record that documents no more than “Limb girdle muscular dystrophy, unspecified” takes G71.039; specificity in the record moves it back here.

    Full comparison: G71.038 vs G71.039 →

  • Q74.3— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of arthrogryposis multiplex congenita adds Q74.3; it is not part of this code and both may be reported when both are documented.

    Full comparison: G71.038 vs Q74.3 →

  • E70— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of metabolic disorders adds E70; it is not part of this code and both may be reported when both are documented.

    Full comparison: G71.038 vs E70 →

  • E88— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of metabolic disorders adds E88; it is not part of this code and both may be reported when both are documented.

    Full comparison: G71.038 vs E88 →

  • M60— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of myositis adds M60; it is not part of this code and both may be reported when both are documented.

    Full comparison: G71.038 vs M60 →

Relationships are read from this code's own official notes, its laterality siblings and its encounter family; the wording of each distinction is MedCoder editorial, and the documentation named in each “what moves you there” line is the official note phrase or sibling title itself. Source: CMS ICD-10-CM tabular instructional notes; ICD-10-CM Official Guidelines, Section I.A.12.a.

Coding context

Guidelines, coding notes, decision aids, relationships (with MS-DRG and CCSR classification), hierarchy, HCC, coverage and the context map: what a coder reaches for after the core. Each section names whether it is official source data, a MedCoder-derived relationship or MedCoder editorial.

Code Overview

Other limb girdle muscular dystrophy is a billable ICD-10-CM diagnosis code (G71.038).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Verify Before Coding

  • No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder-derived relationships — computed from published CMS and AHRQ datasets

Other codes that name G71.038 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 5 Excludes2 notes: M60 — Myositis (via G71.-), M60-M63 — Disorders of muscles (M60-M63) (via G71.-), M61 — Calcification and ossification of muscle (via G71.-), M62 — Other disorders of muscle (via G71.-), M63 — Disorders of muscle in diseases classified elsewhere (via G71.-).

These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.

Referenced by 2 Code First instructions across 2 chapters: M62.84 — Sarcopenia (via G71.-), Z99.3 — Dependence on wheelchair (via G71.0.-).

Each of these codes carries a Code First note naming this condition — when that code is reported, THIS code is sequenced first, ahead of it.

MS-DRG Grouper Relationships (FY2027)

Potential MS-DRG participation — not a DRG assignment.

FY2027 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.

Named in the grouper logic of 3 MS-DRGs: DRG 091 (MDC 01), DRG 092 (MDC 01), DRG 093 (MDC 01).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):NVS018 — Myopathies (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same CMS-HCC risk category (V28)

CMS maps these diagnoses to the same Hierarchical Condition Category (Muscular Dystrophy) for risk-adjusted payment.

G71.00 — Muscular dystrophy, unspecified, G71.01 — Duchenne or Becker muscular dystrophy, G71.02 — Facioscapulohumeral muscular dystrophy, G71.031 — Autosomal dominant limb girdle muscular dystrophy, G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction, G71.033 — Limb girdle muscular dystrophy due to dysferlin dysfunction, G71.0340 — Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified, G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction, G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction, G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction, G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction, G71.036 — Limb girdle muscular dystrophy due to fukutin related protein dysfunction, G71.039 — Limb girdle muscular dystrophy, unspecified, G71.09 — Other specified muscular dystrophies, G71.11 — Myotonic muscular dystrophy, G71.20 — Congenital myopathy, unspecified, G71.21 — Nemaline myopathy, G71.220 — X-linked myotubular myopathy, G71.228 — Other centronuclear myopathy, G71.29 — Other congenital myopathy

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Myopathies).

G71.02 — Facioscapulohumeral muscular dystrophy, G71.031 — Autosomal dominant limb girdle muscular dystrophy, G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction, G71.033 — Limb girdle muscular dystrophy due to dysferlin dysfunction, G71.0340 — Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified, G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction, G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction, G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction, G71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction, G71.036 — Limb girdle muscular dystrophy due to fukutin related protein dysfunction, G71.039 — Limb girdle muscular dystrophy, unspecified, G71.09 — Other specified muscular dystrophies, G71.11 — Myotonic muscular dystrophy, G71.12 — Myotonia congenita, G71.13 — Myotonic chondrodystrophy, G71.14 — Drug induced myotonia, G71.19 — Other specified myotonic disorders, G71.2 — Congenital myopathies, G71.20 — Congenital myopathy, unspecified, G71.21 — Nemaline myopathy, +53 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main term “Dystrophy, dystrophia”; these codes share that main term but sit in a different category of the Tabular List.

E23.6 — Other disorders of pituitary gland (adiposogenital), E31.8 — Other polyglandular dysfunction (polyglandular), E45 — Retarded development following protein-calorie malnutrition (nutritional), E72.03 — Lowe's syndrome (oculocerebrorenal), E75.6 — Lipid storage disorder, unspecified (retinal, in, systemic lipidoses), G31.89 — Other specified degenerative diseases of nervous system (infantile neuraxonal), G60.0 — Hereditary motor and sensory neuropathy (muscular, progressive, Charcot-Marietype), G90.2 — Horner's syndrome (cervical sympathetic), H18.50 — Unspecified hereditary corneal dystrophies (cornea), H18.51 — Endothelial corneal dystrophy (Fuchs'), H18.52 — Epithelial (juvenile) corneal dystrophy (cornea, epithelial), H18.53 — Granular corneal dystrophy (cornea, granular), H18.54 — Lattice corneal dystrophy (cornea, lattice), H18.55 — Macular corneal dystrophy (cornea, macular), H18.59 — Other hereditary corneal dystrophies (cornea, specified type NEC), H31.20 — Hereditary choroidal dystrophy, unspecified (choroid), H31.21 — Choroideremia (choroid, choroideremia), H31.22 — Choroidal dystrophy (central areolar) (generalized) (peripapillary) (choroid, central areolar), H31.23 — Gyrate atrophy, choroid (choroid, gyrate atrophy), H31.29 — Other hereditary choroidal dystrophy (choroid, specified type NEC), +12 more

Contextual Map

Every relationship of G71.038 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run G71.038 with these 7 related codes in Claim Check

Hierarchy

Referenced by Excludes2 notes

Referenced by Code First instructions

  • M62.84 — Sarcopenia[Code First](via G71.-): “primary disorders of muscles (G71.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
  • Z99.3 — Dependence on wheelchair[Code First](via G71.0.-): “muscular dystrophy (G71.0-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027

Clinical classification (CCSR)

Risk adjustment (CMS-HCC)

  • HCC 197 — Muscular Dystrophy [CMS-HCC]— CMS-HCC V28 · 2026

MS-DRG Grouper

MDC crossing

  • MDC 01 — Diseases and Disorders of the Nervous System[MDC crossing]: “Diseases and Disorders of the Nervous System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 8,919 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2027

Index entries (34)

  • Dystrophy, dystrophia, Leyden-Möbius, meaning Limb girdle muscular dystrophy, specified type NEC[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
  • Dystrophy, dystrophia, muscular, limb-girdle, autosomal recessive NEC[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
  • Dystrophy, dystrophia, muscular, limb-girdle, collagen VI related, autosomal recessive[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
  • Dystrophy, dystrophia, muscular, limb-girdle, FKRP-related autosomal recessive[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
  • Dystrophy, dystrophia, muscular, limb-girdle, R10 (autosomal recessive)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
  • Dystrophy, dystrophia, muscular, limb-girdle, R11 (autosomal recessive)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
  • Dystrophy, dystrophia, muscular, limb-girdle, R13 (autosomal recessive)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
  • Dystrophy, dystrophia, muscular, limb-girdle, R14 (autosomal recessive)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
  • and 26 more

Nearest codes (34)

Change history

Reference

Index terms and tables, published questions and FAQ, every source behind this page with its release and checksum, the date-of-service check and the complete change history.

Indexed Clinical Terms (34)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v44 Release, file and checksum · Publisher’s page
Risk adjustment Official source data
2026 Mid-Year Final ICD-10 Mappings + Model Software (cms.gov/files/zip/2026-midyear-final-icd-10-mappings.zip, 2026-midyear-final-model-software.zip) — CMS-HCC V28, PY2026 mid-year final release Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder-derived relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder editorial explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Current data releases:ICD-10-CM FY2027 · ICD-10-PCS FY2027 · HCPCS October 2026 · MS-DRG v44 · Medicare Code Editor v44.0 · NCCI PTP Q4 2026 · MUE Q4 2026 · NCD code lists 2026-01 · LCD export September 28, 2026 · All releases and sources

Labels on this page: Official source data · MedCoder-derived relationship · MedCoder editorial explanation. How to read the labels · All data sources and release dates · CMS coding rules

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "G71.038 — Other limb girdle muscular dystrophy." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/g71.038-other-limb-girdle-muscular-dystrophy

Change history

  • FY2023 — October 1, 2022
    Added to the code set
    Other limb girdle muscular dystrophy
    FY2023 changes

Nearest Codes in This Family

Official ICD-10-CM classifications closest to G71.038 in its code family, with their registry titles.

View all codes in the G71 family