G31.89 ICD-10-CM Code: Other specified degenerative diseases of nervous system
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Coding at a Glance
- Tabular directives
- 1 Excludes2 · 7 use-additional codes
- Risk adjustment
- RxHCC V08 category 112
Inpatient Payment Groups (MS-DRG)
Potential MS-DRG participation — not a DRG assignment.
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v44, Appendix B.
- MS-DRG 056 — DEGENERATIVE NERVOUS SYSTEM DISORDERS WITH MCC (MDC 01)
- MS-DRG 057 — DEGENERATIVE NERVOUS SYSTEM DISORDERS WITHOUT MCC (MDC 01)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for G31.89 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2027Effective: October 1, 2026
Trace:FY2027 changesChange historyRelease, file and checksum
Notes without a marker are published on G31.89 itself; “inherited from” names the category or block whose note applies here.
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- Reye's syndrome (G93.7) Compare G31.89 vs G93.7 →
Source: inherited from G31
Use Additional Code
Supplementary codes the tabular list directs you to add.
- Use additional code, if applicable, for codes G31.0-G31.83, G31.85-G31.9, to identify:
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- mild neurocognitive disorder due to known physiological condition (F06.7-)
Source: inherited from G31
Coder workflow for G31.89
MedCoder structured workflow — derived from this code’s own official record
Before you code G31.89
- “Other” (NEC) means the condition is specified in the record but no dedicated code captures it. Confirm the documented form is not one a sibling code names before settling on G31.89; if the record states no specifics at all, the unspecified sibling applies instead. “Other” codes are for documented conditions the classification gives no specific code; “unspecified” codes are for records lacking the detail (Guidelines I.A.9.a, I.A.9.b).
ReviewG31.81, G31.82, G31.83, G31.84, G31.85, G31.86, G31.87
See the relationships section · Guide: Other vs unspecified (NEC vs NOS) →
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
- The conditions the Use Additional Code note names
- Reported with this code when documented; a conditional instruction (“if applicable”, “if known”) applies only when the record supports it.
- Any detail beyond this code’s title
- What the record states that a more specific sibling code would capture — or its absence, which itself supports the unspecified code.
Official instructions as workflow
Excludes2 — not part of G31.89(1 note)
Coding workflow: The conditions named in this note are not included in G31.89. When the record documents both, both may be reported; the note is a boundary, not a prohibition.
CompareG93.7
See the official tabular notes · Guidelines I.A.12.b
Use Additional Code — after identifying G31.89(7 notes)
Coding workflow: Check whether the documentation supports the additional code(s) the note names, and report them with G31.89 when it does. Where the instruction is conditional (“if applicable”, “if known”), it applies only when the record documents the condition.
ReviewF02.84, F02.A4, F02.B4, F02.C4, F02.81, F02.A1
See the official tabular notes · Guidelines I.A.13
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: A condition the Use Additional Code note names is documented.
Coding question: Is a second code reported with G31.89?
Path: Review the Use Additional Code note and the code it names.
Reason: The additional code is reported when the record documents the condition; a conditional instruction applies only when its condition is met (Guidelines I.A.13).
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Indexed Clinical Terms (11)
Official source data — entries quoted as published, in the Index’s own lookup phrasing
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.
- Degeneration, degenerative, brain (cortical) (progressive), childhood, specified NEC
- Degeneration, degenerative, brain (cortical) (progressive), cystic
- Degeneration, degenerative, cortical (cerebellar) (parenchymatous)
- Degeneration, degenerative, nervous system, fatty
- Degeneration, degenerative, nervous system, specified NEC
- Degeneration, degenerative, spinal (cord)
- Degeneration, degenerative, spinal (cord), familial NEC
- Degeneration, degenerative, spinal (cord), fatty
- Dystrophy, dystrophia, infantile neuraxonal
- Seitelberger's syndrome (infantile neuraxonal dystrophy)
- Syndrome, Seitelberger's
Verify Before Coding
- No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder structured relationships — computed from published CMS and AHRQ datasets
MS-DRG Grouper Relationships (FY2027)
Potential MS-DRG participation — not a DRG assignment.
FY2027 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.
Named in the grouper logic of 2 MS-DRGs: DRG 056 (MDC 01), DRG 057 (MDC 01).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Clinical classification (AHRQ CCSR):NVS006 — Other nervous system disorders (often hereditary or degenerative) (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Other nervous system disorders (often hereditary or degenerative)).
G25.9 — Extrapyramidal and movement disorder, unspecified, G26 — Extrapyramidal and movement disorders in diseases classified elsewhere, G31.2 — Degeneration of nervous system due to alcohol, G31.80 — Leukodystrophy, unspecified, G31.81 — Alpers disease, G31.82 — Leigh's disease, G31.84 — Mild cognitive impairment of uncertain or unknown etiology, G31.85 — Corticobasal degeneration, G31.86 — Alexander disease, G31.87 — Primary progressive apraxia of speech, G31.9 — Degenerative disease of nervous system, unspecified, G32.0 — Subacute combined degeneration of spinal cord in diseases classified elsewhere, G32.81 — Cerebellar ataxia in diseases classified elsewhere, G32.89 — Other specified degenerative disorders of nervous system in diseases classified elsewhere, G90.01 — Carotid sinus syncope, G90.09 — Other idiopathic peripheral autonomic neuropathy, G90.1 — Familial dysautonomia [Riley-Day], G90.3 — Multi-system degeneration of the autonomic nervous system, G90.4 — Autonomic dysreflexia, G90.B — LMNB1-related autosomal dominant leukodystrophy, +83 more
Same Index main term, other category
The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Degeneration, degenerative”, “Dystrophy, dystrophia”; these codes share that main term but sit in a different category of the Tabular List.
E85.4 — Organ-limited amyloidosis (skin, amyloid), E85.89 — Other amyloidosis (capillaries, amyloid), E85.9 — Amyloidosis, unspecified (amyloid), G11.9 — Hereditary ataxia, unspecified (cerebellar NOS, primary), G12.29 — Other motor neuron disease (anterior cornua, spinal cord), G23.0 — Hallervorden-Spatz disease (pallidal pigmentary), G23.2 — Striatonigral degeneration (striatonigral), G23.8 — Other specified degenerative diseases of basal ganglia (olivopontocerebellar), G23.9 — Degenerative disease of basal ganglia, unspecified (basal nuclei or ganglia), G25.9 — Extrapyramidal and movement disorder, unspecified (extrapyramidal), G37.9 — Demyelinating disease of central nervous system, unspecified (myelin, central nervous system), G54.0 — Brachial plexus disorders (brachial plexus), G54.2 — Cervical root disorders, not elsewhere classified (cervical plexus), G60.0 — Hereditary motor and sensory neuropathy (muscular, progressive, Charcot-Marietype), G71.00 — Muscular dystrophy, unspecified (muscular), G71.01 — Duchenne or Becker muscular dystrophy (Becker's type), G71.02 — Facioscapulohumeral muscular dystrophy (Erb's), G71.031 — Autosomal dominant limb girdle muscular dystrophy (muscular, limb-girdle, D2), G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction (muscular, limb-girdle, R1), G71.033 — Limb girdle muscular dystrophy due to dysferlin dysfunction (muscular, limb-girdle, R2), +155 more
Contextual Map
Every relationship of G31.89 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Hierarchy
- G00-G99 — Chapter 6: Diseases of the Nervous System (G00-G99) (G00-G99)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Clinical classification (CCSR)
- NVS006 — Other nervous system disorders (often hereditary or degenerative)[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
MS-DRG Grouper
- DRG 056 — DEGENERATIVE NERVOUS SYSTEM DISORDERS WITH MCC[MS-DRG]: “DEGENERATIVE NERVOUS SYSTEM DISORDERS WITH MCC (MDC 01)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2027
- DRG 057 — DEGENERATIVE NERVOUS SYSTEM DISORDERS WITHOUT MCC[MS-DRG]: “DEGENERATIVE NERVOUS SYSTEM DISORDERS WITHOUT MCC (MDC 01)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2027
MDC crossing
- MDC 01 — Diseases and Disorders of the Nervous System[MDC crossing]: “Diseases and Disorders of the Nervous System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 8,919 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2027
Index entries (11)
- Degeneration, degenerative, brain (cortical) (progressive), childhood, specified NEC[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Degeneration, degenerative, brain (cortical) (progressive), cystic[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Degeneration, degenerative, cortical (cerebellar) (parenchymatous)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Degeneration, degenerative, nervous system, fatty[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Degeneration, degenerative, nervous system, specified NEC[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Degeneration, degenerative, spinal (cord)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Degeneration, degenerative, spinal (cord), familial NEC[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Degeneration, degenerative, spinal (cord), fatty[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- and 3 more
Nearest codes (16)
- G31 — Other degenerative diseases of nervous system, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- G31.0 — Frontotemporal dementia[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- G31.01 — Pick's disease[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- G31.09 — Other frontotemporal neurocognitive disorder[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- G31.1 — Senile degeneration of brain, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- G31.2 — Degeneration of nervous system due to alcohol[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- G31.8 — Other specified degenerative diseases of nervous system[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- G31.80 — Leukodystrophy, unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- and 8 more
Change history
- FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
- Inpatient payment groups Official source data
- CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v44 Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder structured relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "G31.89 — Other specified degenerative diseases of nervous system." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/g31.89-other-specified-degenerative-diseases-of-nervous-system
Change history
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionOther specified degenerative diseases of nervous system
No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027, and none are recorded for this code. Note changes are tracked from FY2027 only.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to G31.89 in its code family, with their registry titles.
- G31.8 — Other specified degenerative diseases of nervous system
- G31.80 — Leukodystrophy, unspecified
- G31.81 — Alpers disease
- G31.82 — Leigh's disease
- G31.83 — Neurocognitive disorder with Lewy bodies
- G31.84 — Mild cognitive impairment of uncertain or unknown etiology
- G31.85 — Corticobasal degeneration
- G31.86 — Alexander disease
- G31.87 — Primary progressive apraxia of speech
- G31.9 — Degenerative disease of nervous system, unspecified