Other nervous system disorders (often hereditary or degenerative)

Code Families in This Category

• G25 Other extrapyramidal and movement disorders · 16
• E75 Disorders of sphingolipid metabolism and other lipid storage disorders · 14
• G11 Hereditary ataxia · 12
• G12 Spinal muscular atrophy and related syndromes · 11
• G24 Dystonia · 10
• G31 Other degenerative diseases of nervous system, not elsewhere classified · 10
• G21 Secondary parkinsonism · 8
• G23 Other degenerative diseases of basal ganglia · 6
• G90 Disorders of autonomic nervous system · 6
• G93 Other disorders of brain · 4
• G32 Other degenerative disorders of nervous system in diseases classified elsewhere · 3
• G99 Other disorders of nervous system in diseases classified elsewhere · 2
• G10 Huntington's disease · 1
• G26 Extrapyramidal and movement disorders in diseases classified elsewhere · 1

ICD-10-CM Codes in This Category (first 100 of 104)

• E75.00 — GM2 gangliosidosis, unspecified
• E75.01 — Sandhoff disease
• E75.02 — Tay-Sachs disease
• E75.09 — Other GM2 gangliosidosis
• E75.10 — Unspecified gangliosidosis
• E75.11 — Mucolipidosis IV
• E75.19 — Other gangliosidosis
• E75.23 — Krabbe disease
• E75.25 — Metachromatic leukodystrophy
• E75.26 — Sulfatase deficiency
• E75.27 — Pelizaeus-Merzbacher disease
• E75.28 — Canavan disease
• E75.29 — Other sphingolipidosis
• E75.4 — Neuronal ceroid lipofuscinosis
• G10 — Huntington's disease
• G11.0 — Congenital nonprogressive ataxia
• G11.1 — Early-onset cerebellar ataxia
• G11.10 — Early-onset cerebellar ataxia, unspecified
• G11.11 — Friedreich ataxia
• G11.19 — Other early-onset cerebellar ataxia
• G11.2 — Late-onset cerebellar ataxia
• G11.3 — Cerebellar ataxia with defective DNA repair
• G11.4 — Hereditary spastic paraplegia
• G11.5 — Hypomyelination - hypogonadotropic hypogonadism - hypodontia
• G11.6 — Leukodystrophy with vanishing white matter disease
• G11.8 — Other hereditary ataxias
• G11.9 — Hereditary ataxia, unspecified
• G12.0 — Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
• G12.1 — Other inherited spinal muscular atrophy
• G12.20 — Motor neuron disease, unspecified
• G12.21 — Amyotrophic lateral sclerosis
• G12.22 — Progressive bulbar palsy
• G12.23 — Primary lateral sclerosis
• G12.24 — Familial motor neuron disease
• G12.25 — Progressive spinal muscle atrophy
• G12.29 — Other motor neuron disease
• G12.8 — Other spinal muscular atrophies and related syndromes
• G12.9 — Spinal muscular atrophy, unspecified
• G21.0 — Malignant neuroleptic syndrome
• G21.11 — Neuroleptic induced parkinsonism
• G21.19 — Other drug induced secondary parkinsonism
• G21.2 — Secondary parkinsonism due to other external agents
• G21.3 — Postencephalitic parkinsonism
• G21.4 — Vascular parkinsonism
• G21.8 — Other secondary parkinsonism
• G21.9 — Secondary parkinsonism, unspecified
• G23.0 — Hallervorden-Spatz disease
• G23.1 — Progressive supranuclear ophthalmoplegia [Steele-Richardson-Olszewski]
• G23.2 — Striatonigral degeneration
• G23.3 — Hypomyelination with atrophy of the basal ganglia and cerebellum
• G23.8 — Other specified degenerative diseases of basal ganglia
• G23.9 — Degenerative disease of basal ganglia, unspecified
• G24.01 — Drug induced subacute dyskinesia
• G24.02 — Drug induced acute dystonia
• G24.09 — Other drug induced dystonia
• G24.1 — Genetic torsion dystonia
• G24.2 — Idiopathic nonfamilial dystonia
• G24.3 — Spasmodic torticollis
• G24.4 — Idiopathic orofacial dystonia
• G24.5 — Blepharospasm
• G24.8 — Other dystonia
• G24.9 — Dystonia, unspecified
• G25.0 — Essential tremor
• G25.1 — Drug-induced tremor
• G25.2 — Other specified forms of tremor
• G25.3 — Myoclonus
• G25.4 — Drug-induced chorea
• G25.5 — Other chorea
• G25.61 — Drug induced tics
• G25.69 — Other tics of organic origin
• G25.70 — Drug induced movement disorder, unspecified
• G25.71 — Drug induced akathisia
• G25.79 — Other drug induced movement disorders
• G25.81 — Restless legs syndrome
• G25.82 — Stiff-man syndrome
• G25.83 — Benign shuddering attacks
• G25.89 — Other specified extrapyramidal and movement disorders
• G25.9 — Extrapyramidal and movement disorder, unspecified
• G26 — Extrapyramidal and movement disorders in diseases classified elsewhere
• G31.2 — Degeneration of nervous system due to alcohol
• G31.80 — Leukodystrophy, unspecified
• G31.81 — Alpers disease
• G31.82 — Leigh's disease
• G31.84 — Mild cognitive impairment of uncertain or unknown etiology
• G31.85 — Corticobasal degeneration
• G31.86 — Alexander disease
• G31.87 — Primary progressive apraxia of speech
• G31.89 — Other specified degenerative diseases of nervous system
• G31.9 — Degenerative disease of nervous system, unspecified
• G32.0 — Subacute combined degeneration of spinal cord in diseases classified elsewhere
• G32.81 — Cerebellar ataxia in diseases classified elsewhere
• G32.89 — Other specified degenerative disorders of nervous system in diseases classified elsewhere
• G90.01 — Carotid sinus syncope
• G90.09 — Other idiopathic peripheral autonomic neuropathy
• G90.1 — Familial dysautonomia [Riley-Day]
• G90.3 — Multi-system degeneration of the autonomic nervous system
• G90.4 — Autonomic dysreflexia
• G90.B — LMNB1-related autosomal dominant leukodystrophy
• G93.42 — Megalencephalic leukoencephalopathy with subcortical cysts
• G93.43 — Leukoencephalopathy with calcifications and cysts

The remaining 4 codes are reachable through the code families above.