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G11.1 ICD-10-CM Code: Early-onset cerebellar ataxia

Compare with another code for G11.1Check this code on a claim

Billing Status: NO. This is a non-billable ICD-10-CM code: report a more specific billable code beneath it.

Coding at a Glance

Tabular directives
3 Excludes2

Not billable · FY2027A non-billable heading in the tabular list: report a more specific code beneath it.

What you need to know

Source: CMS/NCHS Official ICD-10-CM tabular notes, quoted. From the CMS/NCHS tabular list for the release in force. A note the category or block publishes applies to this code too, and is marked with where it comes from.

Excludes2from G11Not included here; may be reported together
  • cerebral palsy (G80.-)
  • hereditary and idiopathic neuropathy (G60.-)
  • metabolic disorders (E70-E88)

Where it sits Source: CMS/NCHS

Under:Chapter 6: Diseases of the Nervous SystemG10-G14 Systemic atrophies primarily affecting the central nervous systemG11 Hereditary ataxia

Codes under G11.1 (3)

  • G11.10Early-onset cerebellar ataxia, unspecifiedBillable
  • G11.11Friedreich ataxiaBillable
  • G11.19Other early-onset cerebellar ataxiaBillable

Most relevant related codes MedCoder-derived

Read off the official notes above and this code’s own position in the tabular list. Which to report is a documentation question; Compare shows the two side by side.

CompareCheck ClaimView Related Codes

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for G11.1 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2027Effective: October 1, 2026

Trace:FY2027 changesChange historyRelease, file and checksum

Notes without a marker are published on G11.1 itself; “inherited from” names the category or block whose note applies here.

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

Source: inherited from G11

Coder workflow for G11.1

MedCoder structured workflow — derived from this code’s own official record

Before you code G11.1

  1. G11.1 is not reportable as written. Select the more specific code beneath it that the documentation supports. Codes are reported to the highest level of specificity the classification provides (Guidelines I.B.2).

    ReviewG11.10, G11.11, G11.19

    See the relationships section · Guide: How to choose an ICD-10-CM code →

Choose the right path

  1. Does the documentation support one of the more specific codes beneath G11.1?
    Yes → Select that code and continue the checks below on its own page.
    No → G11.1 cannot be reported as written. Where the codes beneath it include an unspecified code, that code applies when the record goes no further; otherwise query for the missing detail.

    ReviewG11.10, G11.11, G11.19

Report the code beneath G11.1 that the documentation supports, not G11.1 itself. Then confirm that code is valid for the date of service on its own page.

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
The associated condition or complication
Whether the associated condition the title names is documented; the “with” convention presumes some links, and a provider statement that the conditions are unrelated defeats it (Guidelines I.A.15).

Official instructions as workflow

  • Excludes2 — not part of G11.1(3 notes)

    Coding workflow: The conditions named in this note are not included in G11.1. When the record documents both, both may be reported; the note is a boundary, not a prohibition.

    CompareG80, G60

    See the official tabular notes · Guidelines I.A.12.b

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Don’t confuse G11.1 with…

MedCoder analysis — pairs from this code’s official notes, distinctions written by MedCoder

The codes most likely to be picked instead of G11.1 — named in its own official notes, or sharing its laterality or encounter family — with what separates them and which documentation moves the case. Each links to the full comparison.

  • G11.9— Specificity relationship (Review)

    Overlapping diagnoses in the same category.

    Overlapping codes in the same category — the documentation decides which is the more specific fit.

    What moves you there: A record that documents no more than “Hereditary ataxia, unspecified” takes G11.9; specificity in the record moves it back here.

    Full comparison: G11.1 vs G11.9 →

  • G80— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of cerebral palsy adds G80; it is not part of this code and both may be reported when both are documented.

    Full comparison: G11.1 vs G80 →

  • G60— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of hereditary and idiopathic neuropathy adds G60; it is not part of this code and both may be reported when both are documented.

    Full comparison: G11.1 vs G60 →

  • E70— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of metabolic disorders adds E70; it is not part of this code and both may be reported when both are documented.

    Full comparison: G11.1 vs E70 →

  • E88— Excludes2 relationship (Informational)

    Distinct conditions — both may be reported.

    A distinct condition — both may be reported when both are documented.

    What moves you there: Documentation of metabolic disorders adds E88; it is not part of this code and both may be reported when both are documented.

    Full comparison: G11.1 vs E88 →

Relationships are read from this code's own official notes, its laterality siblings and its encounter family; the wording of each distinction is MedCoder editorial, and the documentation named in each “what moves you there” line is the official note phrase or sibling title itself. Source: CMS ICD-10-CM tabular instructional notes; ICD-10-CM Official Guidelines, Section I.A.12.a.

Coding context

Guidelines, coding notes, decision aids, relationships (with MS-DRG and CCSR classification), hierarchy, HCC, coverage and the context map: what a coder reaches for after the core. Each section names whether it is official source data, a MedCoder-derived relationship or MedCoder editorial.

Code Overview

Early-onset cerebellar ataxia is a non-billable ICD-10-CM category code (G11.1). A more specific billable subcode must be selected for claims submission.

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Verify Before Coding

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder-derived relationships — computed from published CMS and AHRQ datasets

Other codes that name G11.1 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 2 Excludes1 notes: R26 — Abnormalities of gait and mobility (via G11.-), R27 — Other lack of coordination (via G11.-).

These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.

Clinical classification (AHRQ CCSR):NVS006 — Other nervous system disorders (often hereditary or degenerative) (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Other nervous system disorders (often hereditary or degenerative)).

E75.19 — Other gangliosidosis, E75.23 — Krabbe disease, E75.25 — Metachromatic leukodystrophy, E75.26 — Sulfatase deficiency, E75.27 — Pelizaeus-Merzbacher disease, E75.28 — Canavan disease, E75.29 — Other sphingolipidosis, E75.4 — Neuronal ceroid lipofuscinosis, G10 — Huntington's disease, G11.0 — Congenital nonprogressive ataxia, G11.10 — Early-onset cerebellar ataxia, unspecified, G11.11 — Friedreich ataxia, G11.19 — Other early-onset cerebellar ataxia, G11.2 — Late-onset cerebellar ataxia, G11.3 — Cerebellar ataxia with defective DNA repair, G11.4 — Hereditary spastic paraplegia, G11.5 — Hypomyelination - hypogonadotropic hypogonadism - hypodontia, G11.6 — Leukodystrophy with vanishing white matter disease, G11.8 — Other hereditary ataxias, G11.9 — Hereditary ataxia, unspecified, +83 more

Contextual Map

Every relationship of G11.1 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run G11.1 with these 2 related codes in Claim Check

Hierarchy

Referenced by Excludes1 notes

Clinical classification (CCSR)

Nearest codes (12)

Change history (2)

Reference

Index terms and tables, published questions and FAQ, every source behind this page with its release and checksum, the date-of-service check and the complete change history.

Common coding questions

MedCoder editorial

Can G11.1 be billed directly?

No. G11.1 (Early-onset cerebellar ataxia) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder-derived relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder editorial explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Current data releases:ICD-10-CM FY2027 · ICD-10-PCS FY2027 · HCPCS October 2026 · MS-DRG v44 · Medicare Code Editor v44.0 · NCCI PTP Q4 2026 · MUE Q4 2026 · NCD code lists 2026-01 · LCD export September 28, 2026 · All releases and sources

Labels on this page: Official source data · MedCoder-derived relationship · MedCoder editorial explanation. How to read the labels · All data sources and release dates · CMS coding rules

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "G11.1 — Early-onset cerebellar ataxia." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/g11.1-early-onset-cerebellar-ataxia

Change history

  • FY2021 — October 1, 2020
    Became a non-billable header
    FY2021 changes
  • FY2016 — October 1, 2015
    In the code set at ICD-10-CM adoption
    Early-onset cerebellar ataxia

Nearest Codes in This Family

Official ICD-10-CM classifications closest to G11.1 in its code family, with their registry titles.

View all codes in the G11 family