G11.11 ICD-10-CM Code: Friedreich ataxia
G11.11 is the authoritative medical code for Friedreich ataxia. This classification is used in medical billing and clinical recording to specify the clinical criteria for friedreich ataxia (ICD-10-CM G11.11), ensuring healthcare documentation aligns with current federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Inpatient Payment Groups (MS-DRG)
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0 (FY2026), Appendix B.
- MS-DRG 058 — MULTIPLE SCLEROSIS AND CEREBELLAR ATAXIA WITH MCC (MDC 01)
- MS-DRG 059 — MULTIPLE SCLEROSIS AND CEREBELLAR ATAXIA WITH CC (MDC 01)
- MS-DRG 060 — MULTIPLE SCLEROSIS AND CEREBELLAR ATAXIA WITHOUT CC/MCC (MDC 01)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Code Set: Valid FY2026 and FY2027. FY2026 took effect October 1, 2025.
Official Registry Overview & Definition
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for G11.11 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Autosomal recessive Friedreich ataxia
- Friedreich ataxia with retained reflexes
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- cerebral palsy (G80.-)
- hereditary and idiopathic neuropathy (G60.-)
- metabolic disorders (E70-E88)
Frequently Asked Questions (FAQ) & Clinical Guidance
Can G11.11 be reported alongside related conditions?
Per official ICD-10-CM Excludes2 instructions, G11.11 and the following are not considered part of each other and may both be reported when both conditions are present: cerebral palsy (G80.-); hereditary and idiopathic neuropathy (G60.-); metabolic disorders (E70-E88).
What conditions are included under G11.11?
Friedreich ataxia includes: Autosomal recessive Friedreich ataxia; Friedreich ataxia with retained reflexes.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to G11.11 in its code family, with their registry titles.
- G11 — Hereditary ataxia
- G11.0 — Congenital nonprogressive ataxia
- G11.1 — Early-onset cerebellar ataxia
- G11.10 — Early-onset cerebellar ataxia, unspecified
- G11.19 — Other early-onset cerebellar ataxia
- G11.2 — Late-onset cerebellar ataxia
- G11.3 — Cerebellar ataxia with defective DNA repair
- G11.4 — Hereditary spastic paraplegia
- G11.5 — Hypomyelination - hypogonadotropic hypogonadism - hypodontia
- G11.6 — Leukodystrophy with vanishing white matter disease
Indexed Clinical Terms (13)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Ataxia, ataxy, ataxic, autosomal recessive Friedreich
- Ataxia, ataxy, ataxic, Friedreich's (heredofamilial) (cerebellar) (spinal) (with retained reflexes)
- Ataxia, ataxy, ataxic, hereditary, spinal (Friedreich's)
- Ataxia, ataxy, ataxic, spinal, hereditary (Friedreich's)
- Cardiomyopathy (familial) (idiopathic), due to, Friedreich's ataxia
- Disease, diseased, Friedreich's, combined systemic or ataxia
- Friedreich's, ataxia
- Friedreich's, combined systemic disease
- Friedreich's, sclerosis (cerebellum) (spinal cord)
- Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic), in (due to), Friedreich's ataxia
- Sclerosis, sclerotic, Friedreich's (spinal cord)
- Sclerosis, sclerotic, hereditary, spinal (Friedreich's ataxia)
- Sclerosis, sclerotic, spinal (cord) (progressive), hereditary (Friedreich's) (mixed form)