E70-E88 ICD-10-CM Code: Metabolic disorders

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for E70-E88 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Don’t confuse E70-E88 with…

MedCoder analysis — pairs from this code’s official notes, distinctions written by MedCoder

The codes most likely to be picked instead of E70-E88 — named in its own official notes, or sharing its laterality or encounter family — with what separates them and which documentation moves the case. Each links to the full comparison.

• E34.5— Excludes1 conflict (Excludes1 — generally not reported together)

  Not coded here — the tabular list excludes this pair for the same encounter.

  Not reported together with this code, except where the two conditions are documented as unrelated.

  What moves you there: Documentation of androgen insensitivity syndrome moves the case to E34.5; the two are not reported together unless documented as unrelated.

  Full comparison: E70-E88 vs E34.5 →

• E25.0— Excludes1 conflict (Excludes1 — generally not reported together)

  Not coded here — the tabular list excludes this pair for the same encounter.

  Not reported together with this code, except where the two conditions are documented as unrelated.

  What moves you there: Documentation of congenital adrenal hyperplasia moves the case to E25.0; the two are not reported together unless documented as unrelated.

  Full comparison: E70-E88 vs E25.0 →

• D55— Excludes1 conflict (Excludes1 — generally not reported together)

  Not coded here — the tabular list excludes this pair for the same encounter.

  Not reported together with this code, except where the two conditions are documented as unrelated.

  What moves you there: Documentation of hemolytic anemias attributable to enzyme disorders moves the case to D55; the two are not reported together unless documented as unrelated.

  Full comparison: E70-E88 vs D55 →

• Q87.4— Excludes1 conflict (Excludes1 — generally not reported together)

  Not coded here — the tabular list excludes this pair for the same encounter.

  Not reported together with this code, except where the two conditions are documented as unrelated.

  What moves you there: Documentation of Marfan syndrome moves the case to Q87.4; the two are not reported together unless documented as unrelated.

  Full comparison: E70-E88 vs Q87.4 →

• E29.1— Excludes1 conflict (Excludes1 — generally not reported together)

  Not coded here — the tabular list excludes this pair for the same encounter.

  Not reported together with this code, except where the two conditions are documented as unrelated.

  What moves you there: Documentation of 5-alpha-reductase deficiency moves the case to E29.1; the two are not reported together unless documented as unrelated.

  Full comparison: E70-E88 vs E29.1 →

• Q79.6— Excludes2 relationship (Informational)

  Distinct conditions — both may be reported.

  A distinct condition — both may be reported when both are documented.

  What moves you there: Documentation of Ehlers-Danlos syndromes adds Q79.6; it is not part of this code and both may be reported when both are documented.

  Full comparison: E70-E88 vs Q79.6 →

Relationships are read from this code's own official notes, its laterality siblings and its encounter family; the wording of each distinction is MedCoder editorial, and the documentation named in each “what moves you there” line is the official note phrase or sibling title itself. Source: CMS ICD-10-CM tabular instructional notes; ICD-10-CM Official Guidelines, Section I.A.12.a.

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data

CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page

Change history and date-of-service validity Official source data

CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page

Comparisons, relationships and the contextual map MedCoder structured relationship

Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears

Summary and FAQ answers MedCoder explanation

Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Nearest Codes in This Family

Official ICD-10-CM classifications closest to E70-E88 in its code family, with their registry titles.

• E70 — Disorders of aromatic amino-acid metabolism
• E71 — Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
• E72 — Other disorders of amino-acid metabolism
• E73 — Lactose intolerance
• E74 — Other disorders of carbohydrate metabolism
• E75 — Disorders of sphingolipid metabolism and other lipid storage disorders
• E76 — Disorders of glycosaminoglycan metabolism
• E77 — Disorders of glycoprotein metabolism
• E78 — Disorders of lipoprotein metabolism and other lipidemias
• E79 — Disorders of purine and pyrimidine metabolism
• E80 — Disorders of porphyrin and bilirubin metabolism
• E83 — Disorders of mineral metabolism
• E84 — Cystic fibrosis
• E85 — Amyloidosis
• E86 — Volume depletion
• E87 — Other disorders of fluid, electrolyte and acid-base balance
• E88 — Other and unspecified metabolic disorders