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Compare/E80 vs Q87.4

E80 vs Q87.4

E80 (Disorders of porphyrin and bilirubin metabolism) compared with Q87.4 (Marfan syndrome), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.

Can these codes be reported together?

No — do not report together. E80 carries an Excludes1 note covering Q87.4: “Marfan syndrome (Q87.4-)”

Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Side by side

E80Disorders of porphyrin and bilirubin metabolismQ87.4Marfan syndrome
Billing statusNon-billable header

Report instead: E80.0, E80.1, E80.20, E80.21, E80.29

Non-billable header

Report instead: Q87.40, Q87.410, Q87.418, Q87.42, Q87.43

ClassificationE00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89)Q00-Q99 — Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99)
DefinitionDisorders of porphyrin and bilirubin metabolism is a non-billable ICD-10-CM category code (E80).Marfan syndrome is a non-billable ICD-10-CM category code (Q87.4).
Includes
defects of catalase and peroxidase
Use additional code
code(s) to identify all associated manifestations

Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources