D18.00 ICD-10-CM Code: Hemangioma unspecified site

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for D18.00 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on D18.00 itself; “inherited from” names the category or block whose note applies here.

Coder workflow for D18.00

MedCoder structured workflow — derived from this code’s own official record

Before you code D18.00

1. Unspecified does not mean incorrect. When the record gives no greater specificity, D18.00 may be the appropriate code. Check the record for detail that supports a more specific sibling. An unspecified code is for records that do not provide the detail a more specific code needs; a query, not an assumption, is the route to specificity (Guidelines I.A.9.b, I.B.18).

   ReviewD18.01, D18.02, D18.03, D18.09

   See the relationships section · Guide: Other vs unspecified (NEC vs NOS) →

2. Confirm the documented site and behavior (this code’s block classifies benign neoplasms), whether the site is primary or secondary, and whether the malignancy is current or a personal history: a previously excised malignancy with no further treatment and no evidence of disease is history, not current disease. Verify the site against the Table of Neoplasms. Neoplasm chapter guidelines (Guidelines I.C.2.a, I.C.2.d, I.C.2.m).

   See the Table of Neoplasms entries · Guide: Active cancer vs history of cancer →

Choose the right path

1. Does the record document the detail a more specific sibling code needs?
   Yes → Review the specific siblings in this subcategory.
   No → Continue — D18.00 is appropriate when the documentation goes no further.

   ReviewD18.01, D18.02, D18.03, D18.09

Consider D18.00. Then confirm the code is valid for the date of service in the Verify section.

Documentation check

The provider’s diagnostic statement

Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).

Anatomical site

At the most specific level the record states; a site the classification separates cannot be assumed from a procedure or a measurement.

Behavior and current-versus-history status

Malignant, in situ, benign or uncertain; primary or secondary; current disease or personal history (Guidelines I.C.2.m).

Any detail beyond this code’s title

What the record states that a more specific sibling code would capture — or its absence, which itself supports the unspecified code.

Official instructions as workflow

• Excludes2 — not part of D18.00(4 notes)

  Coding workflow: The conditions named in this note are not included in D18.00. When the record documents both, both may be reported; the note is a boundary, not a prohibition.

  CompareD35.6, D22, Q82.5

  See the official tabular notes · Guidelines I.A.12.b

Coding decision scenarios

Pattern scenarios for this code’s structure — decision rules, not clinical cases

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Indexed Clinical Terms (24)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

• Angioendothelioma, benign
• Angioma, plexiform
• Cyst (colloid) (mucous) (simple) (retention), hemangiomatous
• Glomangioma
• Glomangiomyoma
• Hemangioendothelioma, benign
• Hemangioma
• Hemangioma, arteriovenous
• Hemangioma, cavernous
• Hemangioma, epithelioid
• Hemangioma, histiocytoid
• Hemangioma, infantile
• Hemangioma, intramuscular
• Hemangioma, juvenile
• Hemangioma, plexiform
• Hemangioma, racemose
• Hemangioma, simplex
• Hemangioma, venous
• Hemangioma, verrucous keratotic
• Nevus, capillary
• Nevus, cavernous
• Nevus, hemangiomatous
• Nevus, meaning hemangioma
• Tumor, glomus

Don’t confuse D18.00 with…

MedCoder analysis — pairs from this code’s official notes, distinctions written by MedCoder

The codes most likely to be picked instead of D18.00 — named in its own official notes, or sharing its laterality or encounter family — with what separates them and which documentation moves the case. Each links to the full comparison.

• D35.6— Excludes2 relationship (Informational)

  Distinct conditions — both may be reported.

  A distinct condition — both may be reported when both are documented.

  What moves you there: Documentation of benign neoplasm of glomus jugulare adds D35.6; it is not part of this code and both may be reported when both are documented.

  Full comparison: D18.00 vs D35.6 →

• D22— Excludes2 relationship (Informational)

  Distinct conditions — both may be reported.

  A distinct condition — both may be reported when both are documented.

  What moves you there: Documentation of blue or pigmented nevus adds D22; it is not part of this code and both may be reported when both are documented.

  Full comparison: D18.00 vs D22 →

• Q82.5— Excludes2 relationship (Informational)

  Distinct conditions — both may be reported.

  A distinct condition — both may be reported when both are documented.

  What moves you there: Documentation of vascular nevus adds Q82.5; it is not part of this code and both may be reported when both are documented.

  Full comparison: D18.00 vs Q82.5 →

Relationships are read from this code's own official notes, its laterality siblings and its encounter family; the wording of each distinction is MedCoder editorial, and the documentation named in each “what moves you there” line is the official note phrase or sibling title itself. Source: CMS ICD-10-CM tabular instructional notes; ICD-10-CM Official Guidelines, Section I.A.12.a.

Verify Before Coding

• No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name D18.00 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 3 Excludes1 notes: D21 — Other benign neoplasms of connective and other soft tissue (via D18.-), D21 — Other benign neoplasms of connective and other soft tissue (via D18.0.-), D33 — Benign neoplasm of brain and other parts of central nervous system (via D18.0.-).

These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.

Referenced by 1 Excludes2 note: Q27 — Other congenital malformations of peripheral vascular system (via D18.-).

These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.

Named in the grouper logic of 6 MS-DRGs: DRG 011 (MDC PRE), DRG 012 (MDC PRE), DRG 013 (MDC PRE), DRG 314 (MDC 05), DRG 315 (MDC 05), DRG 316 (MDC 05).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):NEO073 — Benign neoplasms (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Benign neoplasms).

D17.24 — Benign lipomatous neoplasm of skin and subcutaneous tissue of left leg, D17.30 — Benign lipomatous neoplasm of skin and subcutaneous tissue of unspecified sites, D17.39 — Benign lipomatous neoplasm of skin and subcutaneous tissue of other sites, D17.4 — Benign lipomatous neoplasm of intrathoracic organs, D17.5 — Benign lipomatous neoplasm of intra-abdominal organs, D17.6 — Benign lipomatous neoplasm of spermatic cord, D17.71 — Benign lipomatous neoplasm of kidney, D17.72 — Benign lipomatous neoplasm of other genitourinary organ, D17.79 — Benign lipomatous neoplasm of other sites, D17.9 — Benign lipomatous neoplasm, unspecified, D18.01 — Hemangioma of skin and subcutaneous tissue, D18.02 — Hemangioma of intracranial structures, D18.03 — Hemangioma of intra-abdominal structures, D18.09 — Hemangioma of other sites, D18.1 — Lymphangioma, any site, D19.0 — Benign neoplasm of mesothelial tissue of pleura, D19.1 — Benign neoplasm of mesothelial tissue of peritoneum, D19.7 — Benign neoplasm of mesothelial tissue of other sites, D19.9 — Benign neoplasm of mesothelial tissue, unspecified, D20.0 — Benign neoplasm of soft tissue of retroperitoneum, +252 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Tumor”, “Nevus”, “Cyst”; these codes share that main term but sit in a different category of the Tabular List.

C7B.03 — Secondary carcinoid tumors of bone (carcinoid, secondary, bone), C7B.04 — Secondary carcinoid tumors of peritoneum (carcinoid, mesentery metastasis), C7B.09 — Secondary carcinoid tumors of other sites (secondary, carcinoid, specified NEC), C7B.8 — Other secondary neuroendocrine tumors (neuroendocrine, secondary NEC), C80.1 — Malignant (primary) neoplasm, unspecified (malignant), D10.30 — Benign neoplasm of unspecified part of mouth (mouth), D10.39 — Benign neoplasm of other parts of mouth (mouth, specified site NEC), D13.7 — Benign neoplasm of endocrine pancreas (beta-cell, pancreas), D16.4 — Benign neoplasm of bones of skull and face (calcifying odontogenic, upper jaw), D16.5 — Benign neoplasm of lower jaw bone (calcifying odontogenic), D21.4 — Benign neoplasm of connective and other soft tissue of abdomen (stromal, stomach, benign), D22.0 — Melanocytic nevi of lip (skin, lip), D22.1 — Melanocytic nevi of eyelid, including canthus (skin, eyelid), D22.2 — Melanocytic nevi of ear and external auricular canal (skin, ear), D22.30 — Melanocytic nevi of unspecified part of face (skin, face), D22.39 — Melanocytic nevi of other parts of face (skin, jaw), D22.4 — Melanocytic nevi of scalp and neck (skin, neck), D22.5 — Melanocytic nevi of trunk (skin, back), D22.6 — Melanocytic nevi of upper limb, including shoulder (skin, arm), D22.7 — Melanocytic nevi of lower limb, including hip (skin, toe), +330 more

Lab tests where this diagnosis supports Medicare coverage (NCD)

Medicare's National Coverage Determination (NCD) program lists this diagnosis as medical justification for these lab tests.

Iron Panel

Contextual Map

Every relationship of D18.00 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run D18.00 with these 3 related codes in Claim Check

Hierarchy

• C00-D49 — Chapter 2: Neoplasms (C00-D49) (C00-D49)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026

Referenced by Excludes1 notes

• D21 — Other benign neoplasms of connective and other soft tissue[Excludes1](via D18.-): “benign neoplasm of vascular tissue (D18.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
• D21 — Other benign neoplasms of connective and other soft tissue[Excludes1](via D18.0.-): “hemangioma (D18.0-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
• D33 — Benign neoplasm of brain and other parts of central nervous system[Excludes1](via D18.0.-): “angioma (D18.0-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026

Referenced by Excludes2 notes

• Q27 — Other congenital malformations of peripheral vascular system[Excludes2](via D18.-): “hemangioma and lymphangioma (D18.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026

Clinical classification (CCSR)

• NEO073 — Benign neoplasms[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)

MS-DRG Grouper

• DRG 011 — TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITH MCC[MS-DRG]: “TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITH MCC (MDC PRE)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
• DRG 012 — TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITH CC[MS-DRG]: “TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITH CC (MDC PRE)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
• DRG 013 — TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITHOUT CC/MCC[MS-DRG]: “TRACHEOSTOMY FOR FACE, MOUTH AND NECK DIAGNOSES OR LARYNGECTOMY WITHOUT CC/MCC (MDC PRE)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
• DRG 314 — OTHER CIRCULATORY SYSTEM DIAGNOSES WITH MCC[MS-DRG]: “OTHER CIRCULATORY SYSTEM DIAGNOSES WITH MCC (MDC 05)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
• DRG 315 — OTHER CIRCULATORY SYSTEM DIAGNOSES WITH CC[MS-DRG]: “OTHER CIRCULATORY SYSTEM DIAGNOSES WITH CC (MDC 05)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
• DRG 316 — OTHER CIRCULATORY SYSTEM DIAGNOSES WITHOUT CC/MCC[MS-DRG]: “OTHER CIRCULATORY SYSTEM DIAGNOSES WITHOUT CC/MCC (MDC 05)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026

MDC crossing

• Pre-MDC[MDC crossing]: “Pre-MDC — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 153 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026
• MDC 05 — Diseases and Disorders of the Circulatory System[MDC crossing]: “Diseases and Disorders of the Circulatory System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 17,209 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries (24)

• Angioendothelioma, benign[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Angioma, plexiform[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Cyst (colloid) (mucous) (simple) (retention), hemangiomatous[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Glomangioma[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Glomangiomyoma[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Hemangioendothelioma, benign[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Hemangioma[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• Hemangioma, arteriovenous[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
• and 16 more

Nearest codes

• D18 — Hemangioma and lymphangioma, any site[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• D18.0 — Hemangioma[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• D18.01 — Hemangioma of skin and subcutaneous tissue[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• D18.02 — Hemangioma of intracranial structures[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• D18.03 — Hemangioma of intra-abdominal structures[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• D18.09 — Hemangioma of other sites[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
• D18.1 — Lymphangioma, any site[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026

Change history

• FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data

CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page

Claim edits Official source data

CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page

Inpatient payment groups Official source data

CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page

Change history and date-of-service validity Official source data

CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page

Comparisons, relationships and the contextual map MedCoder structured relationship

Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears

Summary and FAQ answers MedCoder explanation

Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Nearest Codes in This Family

Official ICD-10-CM classifications closest to D18.00 in its code family, with their registry titles.

• D18 — Hemangioma and lymphangioma, any site
• D18.0 — Hemangioma
• D18.01 — Hemangioma of skin and subcutaneous tissue
• D18.02 — Hemangioma of intracranial structures
• D18.03 — Hemangioma of intra-abdominal structures
• D18.09 — Hemangioma of other sites
• D18.1 — Lymphangioma, any site

View all codes in the D18 family