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M30.0 ICD-10-CM Code: Polyarteritis nodosa

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
4 inclusion terms · 2 Excludes1
Risk adjustment
CMS-HCC V28: 1 category · CMS-HCC V22 category 40 · RxHCC V08 category 84

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.

  • MS-DRG 545 — CONNECTIVE TISSUE DISORDERS WITH MCC (MDC 08)
  • MS-DRG 546 — CONNECTIVE TISSUE DISORDERS WITH CC (MDC 08)
  • MS-DRG 547 — CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC (MDC 08)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Risk Adjustment (CMS-HCC)

Payment categories this diagnosis maps to under CMS-HCC V28, payment year 2026.

  • HCC 94 — Systemic Lupus Erythematosus and Other Specified Systemic Connective Tissue Disorders

Other models: CMS-HCC V22 HCC 40 · RxHCC V08 HCC 84

Risk scores depend on the enrollee's full accepted diagnosis set and segment; a category mapping alone does not determine payment.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for M30.0 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on M30.0 itself; “inherited from” names the category or block whose note applies here.

Includes

Conditions the official ICD-10-CM tabular list includes under this code.

  • autoimmune disease NOS
  • collagen (vascular) disease NOS
  • systemic autoimmune disease
  • systemic collagen (vascular) disease

Source: inherited from M30-M36

Excludes1 — Not Coded Here

Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

  • microscopic polyarteritis (M31.7) inherited from M30Compare M30.0 vs M31.7 →
  • autoimmune disease, single organ or single cell-type -code to relevant condition category inherited from M30-M36

Coder workflow for M30.0

MedCoder structured workflow — derived from this code’s own official record

Before you code M30.0

  1. Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with M30.0. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).

    See the official tabular notes

Choose the right path

  1. Does the documentation support a condition named in M30.0’s Excludes1 note?
    Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
    No → Continue.

    ReviewM31.7

Consider M30.0. Then confirm the code is valid for the date of service in the Verify section.

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).

Official instructions as workflow

  • Excludes1 — check before selecting M30.0(2 notes)

    Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with M30.0: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.

    CompareM31.7

    See the official tabular notes · Guidelines I.A.12.a

Coding decision scenarios

Pattern scenarios for this code’s structure — decision rules, not clinical cases

Documentation: Both the condition M30.0 describes and a condition named in its Excludes1 note are documented for the same encounter.

Coding question: Can both codes be reported?

Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.

Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).

ReviewM31.7

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Code Overview

Polyarteritis nodosa is a billable ICD-10-CM diagnosis code (M30.0).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (11)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Verify Before Coding

  • CC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

Other codes that name M30.0 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

Referenced by 8 Excludes1 notes across 2 chapters: L94 — Other localized connective tissue disorders (via M30.-), L95 — Vasculitis limited to skin, not elsewhere classified, M31.7 — Microscopic polyangiitis, M60 — Myositis, M60-M63 — Disorders of muscles (M60-M63), M61 — Calcification and ossification of muscle, M62 — Other disorders of muscle, M63 — Disorders of muscle in diseases classified elsewhere.

These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.

Referenced by 2 Excludes2 notes across 2 chapters: I77 — Other disorders of arteries and arterioles (via M30.-), J82 — Pulmonary eosinophilia, not elsewhere classified (via M30.-).

These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.

Referenced by 2 Code First instructions across 2 chapters: F02 — Dementia in other diseases classified elsewhere, J84.170 — Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere (via M30.-).

Each of these codes carries a Code First note naming this condition — when that code is reported, THIS code is sequenced first, ahead of it.

Referenced by 1 Code Also instruction: D81.32 — Adenosine deaminase 2 deficiency.

These codes suggest coding this condition alongside when both are present.

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 74 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 3 MS-DRGs: DRG 545 (MDC 08), DRG 546 (MDC 08), DRG 547 (MDC 08).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MUS024 — Systemic lupus erythematosus and connective tissue disorders (default); CIR037 — Vasculitis.

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical process (MS-DRG)

Acts as CC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

E13.65 — Other specified diabetes mellitus with hyperglycemia, E13.69 — Other specified diabetes mellitus with other specified complication, E13.8 — Other specified diabetes mellitus with unspecified complications, I27.841 — Fontan-associated lymphatic dysfunction, I27.848 — Other Fontan-associated condition, I27.849 — Fontan related circulation, unspecified, I87.8 — Other specified disorders of veins, I87.9 — Disorder of vein, unspecified, I99.8 — Other disorder of circulatory system, I99.9 — Unspecified disorder of circulatory system, M30.1 — Polyarteritis with lung involvement [Churg-Strauss], M30.2 — Juvenile polyarteritis, M30.3 — Mucocutaneous lymph node syndrome [Kawasaki], M30.8 — Other conditions related to polyarteritis nodosa, M31.0 — Hypersensitivity angiitis, M31.2 — Lethal midline granuloma, M31.30 — Wegener's granulomatosis without renal involvement, M31.31 — Wegener's granulomatosis with renal involvement, M31.4 — Aortic arch syndrome [Takayasu], M31.5 — Giant cell arteritis with polymyalgia rheumatica, +53 more

Same CMS-HCC risk category (V28)

CMS maps these diagnoses to the same Hierarchical Condition Category (Systemic Lupus Erythematosus and Other Specified Systemic Connective Tissue Disorders) for risk-adjusted payment.

M12.052 — Chronic postrheumatic arthropathy [Jaccoud], left hip, M12.059 — Chronic postrheumatic arthropathy [Jaccoud], unspecified hip, M12.061 — Chronic postrheumatic arthropathy [Jaccoud], right knee, M12.062 — Chronic postrheumatic arthropathy [Jaccoud], left knee, M12.069 — Chronic postrheumatic arthropathy [Jaccoud], unspecified knee, M12.071 — Chronic postrheumatic arthropathy [Jaccoud], right ankle and foot, M12.072 — Chronic postrheumatic arthropathy [Jaccoud], left ankle and foot, M12.079 — Chronic postrheumatic arthropathy [Jaccoud], unspecified ankle and foot, M12.08 — Chronic postrheumatic arthropathy [Jaccoud], other specified site, M12.09 — Chronic postrheumatic arthropathy [Jaccoud], multiple sites, M30.2 — Juvenile polyarteritis, M30.8 — Other conditions related to polyarteritis nodosa, M31.5 — Giant cell arteritis with polymyalgia rheumatica, M31.6 — Other giant cell arteritis, M31.7 — Microscopic polyangiitis, M31.8 — Other specified necrotizing vasculopathies, M31.9 — Necrotizing vasculopathy, unspecified, M32.10 — Systemic lupus erythematosus, organ or system involvement unspecified, M32.11 — Endocarditis in systemic lupus erythematosus, M32.12 — Pericarditis in systemic lupus erythematosus, +50 more

Related risk categories

These categories interact through CMS's HCC hierarchy — one can suppress the other's risk-adjustment weight when both are present on a claim.

Rheumatoid Arthritis and Other Specified Inflammatory Rheumatic Disorders

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical categories (Systemic lupus erythematosus and connective tissue disorders, Vasculitis).

M05.251 — Rheumatoid vasculitis with rheumatoid arthritis of right hip, M05.252 — Rheumatoid vasculitis with rheumatoid arthritis of left hip, M05.259 — Rheumatoid vasculitis with rheumatoid arthritis of unspecified hip, M05.261 — Rheumatoid vasculitis with rheumatoid arthritis of right knee, M05.262 — Rheumatoid vasculitis with rheumatoid arthritis of left knee, M05.269 — Rheumatoid vasculitis with rheumatoid arthritis of unspecified knee, M05.271 — Rheumatoid vasculitis with rheumatoid arthritis of right ankle and foot, M05.272 — Rheumatoid vasculitis with rheumatoid arthritis of left ankle and foot, M05.279 — Rheumatoid vasculitis with rheumatoid arthritis of unspecified ankle and foot, M05.29 — Rheumatoid vasculitis with rheumatoid arthritis of multiple sites, M30.1 — Polyarteritis with lung involvement [Churg-Strauss], M30.2 — Juvenile polyarteritis, M30.3 — Mucocutaneous lymph node syndrome [Kawasaki], M30.8 — Other conditions related to polyarteritis nodosa, M31.0 — Hypersensitivity angiitis, M31.1 — Thrombotic microangiopathy, M31.10 — Thrombotic microangiopathy, unspecified, M31.11 — Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA], M31.19 — Other thrombotic microangiopathy, M31.2 — Lethal midline granuloma, +101 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Arteritis”, “Polyangiitis”, “Myopathy”, …; these codes share that main term but sit in a different category of the Tabular List.

G72.9 — Myopathy, unspecified, H05.82 — Myopathy of extraocular muscles (extraocular muscles), I01.8 — Other acute rheumatic heart disease (coronary, rheumatic), I09.89 — Other specified rheumatic heart diseases (coronary, rheumatic, chronic), I25.89 — Other forms of chronic ischemic heart disease (coronary), I28.8 — Other diseases of pulmonary vessels (pulmonary), I67.7 — Cerebral arteritis, not elsewhere classified (brain), I68.2 — Cerebral arteritis in other diseases classified elsewhere (cerebral, in, diseases classified elsewhere), I77.2 — Rupture of artery (suppurative), I77.6 — Arteritis, unspecified, M31.0 — Hypersensitivity angiitis (allergic), M31.4 — Aortic arch syndrome [Takayasu] (aortic arch), M31.5 — Giant cell arteritis with polymyalgia rheumatica (giant cell NEC, with polymyalgia rheumatica), M31.6 — Other giant cell arteritis (giant cell NEC), M31.7 — Microscopic polyangiitis (microscopic), M31.8 — Other specified necrotizing vasculopathies (necrosing or necrotizing, specified NEC), M31.9 — Necrotizing vasculopathy, unspecified (necrosing or necrotizing), M32.19 — Other organ or system involvement in systemic lupus erythematosus (in, systemic lupus erythematosus), M34.82 — Systemic sclerosis with myopathy (in, scleroderma), M35.03 — Sjögren syndrome with myopathy (in, sicca syndrome), +182 more

Contextual Map

Every relationship of M30.0 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Run M30.0 with these 13 related codes in Claim Check

Hierarchy

Index manifestation

Referenced by Excludes1 notes

Referenced by Excludes2 notes

Referenced by Code First instructions

Referenced by Code Also instructions

Clinical classification (CCSR)

Risk adjustment (CMS-HCC)

  • HCC 94 — Systemic Lupus Erythematosus and Other Specified Systemic Connective Tissue Disorders [CMS-HCC]— CMS-HCC V28 · 2026

MS-DRG Grouper

MDC crossing

  • MDC 08 — Diseases and Disorders of the Musculoskeletal System and Connective Tissue[MDC crossing]: “Diseases and Disorders of the Musculoskeletal System and Connective Tissue — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 18,508 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries (11)

  • Arteritis, nodosa[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety), in (due to), polyarteritis nodosa[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety), in (due to), polyarteritis nodosa, with behavioral disturbance[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Kussmaul's, disease[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Myopathy, in (due to), polyarteritis nodosa[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Panangiitis[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Panarteritis nodosa[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Periarteritis nodosa (disseminated) (infectious) (necrotizing)[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • and 3 more

Nearest codes

Change history

  • FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
Risk adjustment Official source data
2026 Mid-Year Final ICD-10 Mappings + Model Software (cms.gov/files/zip/2026-midyear-final-icd-10-mappings.zip, 2026-midyear-final-model-software.zip) — CMS-HCC V28, PY2026 mid-year final release Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "M30.0 — Polyarteritis nodosa." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/m30.0-polyarteritis-nodosa

Change history

  • FY2016 — October 1, 2015
    In the code set at ICD-10-CM adoption
    Polyarteritis nodosa

No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027 (effective October 1, 2026), and none are recorded for this code. Note changes are tracked from FY2027 only.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to M30.0 in its code family, with their registry titles.

View all codes in the M30 family