Skip to main content

M35.0 ICD-10-CM Code: Sjögren syndrome

Billing Status: NO. This is a clinician non-billable / parent hierarchy grouping in the ICD-10-CM system.

Official Registry Overview & Definition

Sjögren syndrome is a non-billable ICD-10-CM category code (M35.0). A more specific billable subcode must be selected for claims submission.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for M35.0 in the official ICD-10-CM tabular list.

Includes

Conditions the official ICD-10-CM tabular list includes under this code.

  • autoimmune disease NOS
  • collagen (vascular) disease NOS
  • systemic autoimmune disease
  • systemic collagen (vascular) disease

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Sicca syndrome

Excludes1 — Not Coded Here

Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Use Additional Code

Supplementary codes the tabular list directs you to add.

  • Use additional code to identify associated manifestations

Frequently Compared Codes

The official Excludes notes on M35.0 name these codes. Each comparison page covers when the two can — or must not — be reported together.

Change history

  • FY2022 — 2021-10-01
    Description revised
    Sicca syndrome [Sjogren] → Sjogren syndrome
    FY2022 changes
  • FY2022 — 2021-10-01
    Short description revised
    Sicca syndrome [Sjogren] → Sjogren syndrome
    FY2022 changes

Verify Before Coding

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim.

Contextual Map

Every relationship of M35.0 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Hierarchy

  • M00-M99 — Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue (M00-M99) (M00-M99) [Hierarchy]
  • M30-M36 — Systemic connective tissue disorders [Hierarchy]

Excludes1

  • R68.2 — Dry mouth, unspecified [Excludes1]: “dry mouth, unspecified (R68.2)” · check together

Referenced by Excludes1 notes

  • K11.8 — Other diseases of salivary glands [Excludes1]: “Sjögren syndrome (M35.0-)” · check together
  • R68.2 — Dry mouth, unspecified [Excludes1]: “dry mouth due to Sjögren syndrome (M35.0-)” · check together

Referenced by Code Also instructions

  • I27.21 — Secondary pulmonary arterial hypertension [Code Also]: “Sjögren syndrome (M35.0-)” · check together

Nearest codes (25)

  • M35 — Other systemic involvement of connective tissue [Sibling]
  • M35.00 — Sjögren syndrome, unspecified [Sibling]
  • M35.01 — Sjögren syndrome with keratoconjunctivitis [Sibling]
  • M35.02 — Sjögren syndrome with lung involvement [Sibling]
  • M35.03 — Sjögren syndrome with myopathy [Sibling]
  • M35.04 — Sjögren syndrome with tubulo-interstitial nephropathy [Sibling]
  • M35.05 — Sjögren syndrome with inflammatory arthritis [Sibling]
  • M35.06 — Sjögren syndrome with peripheral nervous system involvement [Sibling]
  • and 17 more

Change history (2)

  • FY2022 — Description revised [Change history]
  • and 1 more

Referenced by Other Codes

Official ICD-10-CM tabular notes on other codes that name M35.0 or its code family.

2 Excludes1 notes across 2 chapters: K11.8, R68.2.

1 Code Also instructions: I27.21.

Frequently Asked Questions (FAQ) & Clinical Guidance

Can M35.0 be billed directly?

No. M35.0 (Sjögren syndrome) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to M35.0 in its code family, with their registry titles.

  • M35 — Other systemic involvement of connective tissue
  • M35.00 — Sjögren syndrome, unspecified
  • M35.01 — Sjögren syndrome with keratoconjunctivitis
  • M35.02 — Sjögren syndrome with lung involvement
  • M35.03 — Sjögren syndrome with myopathy
  • M35.04 — Sjögren syndrome with tubulo-interstitial nephropathy
  • M35.05 — Sjögren syndrome with inflammatory arthritis
  • M35.06 — Sjögren syndrome with peripheral nervous system involvement
  • M35.07 — Sjögren syndrome with central nervous system involvement
  • M35.08 — Sjögren syndrome with gastrointestinal involvement

View all codes in the M35 family