Skip to main content
ICD-10/Q25.49

Q25.49 ICD-10-CM Code: Other congenital malformations of aorta

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Inpatient Payment Groups (MS-DRG)

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0 (FY2026), Appendix B.

  • MS-DRG 306 — CARDIAC CONGENITAL AND VALVULAR DISORDERS WITH MCC (MDC 05)
  • MS-DRG 307 — CARDIAC CONGENITAL AND VALVULAR DISORDERS WITHOUT MCC (MDC 05)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Code Set: Valid FY2026 and FY2027. FY2026 took effect October 1, 2025.

Official Registry Overview & Definition

Other congenital malformations of aorta is a billable ICD-10-CM diagnosis code (Q25.49).

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for Q25.49 in the official ICD-10-CM tabular list.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Aortic arch
  • Bovine arch

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4)

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q25.49 in its code family, with their registry titles.

  • Q25.44 — Congenital dilation of aorta
  • Q25.45 — Double aortic arch
  • Q25.46 — Tortuous aortic arch
  • Q25.47 — Right aortic arch
  • Q25.48 — Anomalous origin of subclavian artery
  • Q25.5 — Atresia of pulmonary artery
  • Q25.6 — Stenosis of pulmonary artery
  • Q25.7 — Other congenital malformations of pulmonary artery
  • Q25.71 — Coarctation of pulmonary artery
  • Q25.72 — Congenital pulmonary arteriovenous malformation

View all codes in the Q25 family

Indexed Clinical Terms (11)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Absence (of) (organ or part) (complete or partial), transverse aortic arch, congenital
  • Anomaly, anomalous (congenital) (unspecified type), sinus of Valsalva
  • Arch, aortic
  • Arch, bovine
  • Congenital, aortic septum
  • Deformity, transverse aortic arch (congenital)
  • Malformation (congenital), aorta, specified type NEC
  • Malposition, congenital, aorta
  • Overriding, aorta
  • Persistence, persistent (congenital), left, root with right arch of aorta
  • Pseudotruncus arteriosus