ICD-10/Q25.45

Q25.45 ICD 2026 Code: Double aortic arch

Q25.45 is the authoritative medical code for Double aortic arch. This classification is used in medical billing and clinical recording to specify the clinical criteria for double aortic arch (ICD-10-CM Q25.45), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Double aortic arch is a billable ICD-10-CM diagnosis code Q25.45. Inclusion terms: Vascular ring of aorta. Excludes1 (not coded here): hypoplasia of aorta in hypoplastic left heart syndrome Q23.4.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for Q25.45 in the official ICD-10-CM tabular list.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Vascular ring of aorta

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • hypoplasia of aorta in hypoplastic left heart syndrome Q23.4

Frequently Asked Questions (FAQ) & Clinical Guidance

What can't be coded together with Q25.45?

Per official ICD-10-CM Excludes1 instructions, Q25.45 must not be reported together with: hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4).

What conditions are included under Q25.45?

Double aortic arch includes: Vascular ring of aorta.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q25.45 in its code family, with their registry titles.

  • Q25 — Congenital malformations of great arteries
  • Q25.0 — Patent ductus arteriosus
  • Q25.1 — Coarctation of aorta
  • Q25.2 — Atresia of aorta
  • Q25.21 — Interruption of aortic arch
  • Q25.29 — Other atresia of aorta
  • Q25.3 — Supravalvular aortic stenosis
  • Q25.4 — Other congenital malformations of aorta
  • Q25.40 — Congenital malformation of aorta unspecified
  • Q25.41 — Absence and aplasia of aorta

View all 25 codes in the Q25 family

Indexed Clinical Terms (5)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Anomaly, anomalous (congenital) (unspecified type), vascular, ring
  • Double, aortic arch
  • Persistence, persistent (congenital), double aortic arch
  • Ring (s), aorta (vascular)
  • Ring (s), vascular (congenital), aorta