Q25.46 is the authoritative medical code for Tortuous aortic arch. This classification is used in medical billing and clinical recording to specify the clinical criteria for tortuous aortic arch (ICD-10-CM Q25.46), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Tortuous aortic arch is a billable ICD-10-CM diagnosis code Q25.46. Inclusion terms: Persistent convolutions of aortic arch. Excludes1 (not coded here): hypoplasia of aorta in hypoplastic left heart syndrome Q23.4.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for Q25.46 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Persistent convolutions of aortic arch
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- hypoplasia of aorta in hypoplastic left heart syndrome Q23.4
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with Q25.46?
Per Excludes1 instructions, Q25.46 must not be reported with: hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4).
What conditions are included under Q25.46?
Tortuous aortic arch includes: Persistent convolutions of aortic arch.
Codes in This Family (25)
Official ICD-10-CM classifications in the same code family as Q25.46, with their registry titles.
- Q25 — Congenital malformations of great arteries
- Q25.0 — Patent ductus arteriosus
- Q25.1 — Coarctation of aorta
- Q25.2 — Atresia of aorta
- Q25.21 — Interruption of aortic arch
- Q25.29 — Other atresia of aorta
- Q25.3 — Supravalvular aortic stenosis
- Q25.4 — Other congenital malformations of aorta
- Q25.40 — Congenital malformation of aorta unspecified
- Q25.41 — Absence and aplasia of aorta
- Q25.42 — Hypoplasia of aorta
- Q25.43 — Congenital aneurysm of aorta
- Q25.44 — Congenital dilation of aorta
- Q25.45 — Double aortic arch
- Q25.47 — Right aortic arch
- Q25.48 — Anomalous origin of subclavian artery
- Q25.49 — Other congenital malformations of aorta
- Q25.5 — Atresia of pulmonary artery
- Q25.6 — Stenosis of pulmonary artery
- Q25.7 — Other congenital malformations of pulmonary artery
- Q25.71 — Coarctation of pulmonary artery
- Q25.72 — Congenital pulmonary arteriovenous malformation
- Q25.79 — Other congenital malformations of pulmonary artery
- Q25.8 — Other congenital malformations of other great arteries
- Q25.9 — Congenital malformation of great arteries, unspecified
Indexed Clinical Terms (2)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Persistence, persistent (congenital), convolutions, aortic arch
- Tortuous, aortic arch
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: