Q27.39 ICD-10-CM Code: Arteriovenous malformation, other site
Compare with another codeCheck this code on a claim
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Coding at a Glance
- Tabular directives
- 1 Excludes1 · 7 Excludes2
Billable · FY2027A valid, specific ICD-10-CM code, reportable for dates of service in FY2027.
What you need to know
Source: CMS/NCHS Official ICD-10-CM tabular notes, quoted. From the CMS/NCHS tabular list for the release in force. A note the category or block publishes applies to this code too; the Instructions section marks which is which.
- Excludes1Never report with this code
- acquired arteriovenous aneurysm (I77.0)
Most relevant related codes MedCoder-derived
Read off the official notes above and this code’s own position in the tabular list. Which to report is a documentation question; Compare shows the two side by side.
Inpatient Payment Groups (MS-DRG)
Potential MS-DRG participation — not a DRG assignment.
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v44, Appendix B.
- MS-DRG 299 — PERIPHERAL VASCULAR DISORDERS WITH MCC (MDC 05)
- MS-DRG 300 — PERIPHERAL VASCULAR DISORDERS WITH CC (MDC 05)
- MS-DRG 301 — PERIPHERAL VASCULAR DISORDERS WITHOUT CC/MCC (MDC 05)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q27.39 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2027Effective: October 1, 2026
Trace:FY2027 changesChange historyRelease, file and checksum
Notes without a marker are published on Q27.39 itself; “inherited from” names the category or block whose note applies here.
Excludes1 — Not Coded Here
Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
- acquired arteriovenous aneurysm (I77.0) Compare Q27.39 vs I77.0 →
Source: inherited from Q27.3
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- arteriovenous malformation of cerebral vessels (Q28.2) inherited from Q27.3Compare Q27.39 vs Q28.2 →
- arteriovenous malformation of precerebral vessels (Q28.0) inherited from Q27.3Compare Q27.39 vs Q28.0 →
- anomalies of cerebral and precerebral vessels (Q28.0-Q28.3) inherited from Q27Compare Q27.39 vs Q28.0 →
- anomalies of coronary vessels (Q24.5) inherited from Q27Compare Q27.39 vs Q24.5 →
- anomalies of pulmonary artery (Q25.5-Q25.7) inherited from Q27Compare Q27.39 vs Q25.5 →
- congenital retinal aneurysm (Q14.1) inherited from Q27Compare Q27.39 vs Q14.1 →
- hemangioma and lymphangioma (D18.-) inherited from Q27Compare Q27.39 vs D18 →
Coder workflow for Q27.39
MedCoder structured workflow — derived from this code’s own official record
Before you code Q27.39
- Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with Q27.39. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).
Choose the right path
- Does the documentation support a condition named in Q27.39’s Excludes1 note?
Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
No → Continue.ReviewI77.0
Consider Q27.39. Then confirm the code is valid for the date of service in the Verify section.
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
Official instructions as workflow
Excludes1 — check before selecting Q27.39(1 note)
Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with Q27.39: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.
CompareI77.0
See the official tabular notes · Guidelines I.A.12.a
Excludes2 — not part of Q27.39(7 notes)
Coding workflow: The conditions named in this note are not included in Q27.39. When the record documents both, both may be reported; the note is a boundary, not a prohibition.
CompareQ28.2, Q28.0, Q24.5, Q14.1, D18
See the official tabular notes · Guidelines I.A.12.b
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: Both the condition Q27.39 describes and a condition named in its Excludes1 note are documented for the same encounter.
Coding question: Can both codes be reported?
Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.
Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).
ReviewI77.0
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Coding context
Guidelines, coding notes, decision aids, relationships (with MS-DRG and CCSR classification), hierarchy, HCC, coverage and the context map: what a coder reaches for after the core. Each section names whether it is official source data, a MedCoder-derived relationship or MedCoder editorial.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Verify Before Coding
- No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder-derived relationships — computed from published CMS and AHRQ datasets
Other codes that name Q27.39 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.
Referenced by 2 Excludes1 notes across 2 chapters: I77.0 — Arteriovenous fistula, acquired (via Q27.3.-), Q27.8 — Other specified congenital malformations of peripheral vascular system (via Q27.3.-).
These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.
Referenced by 2 Excludes2 notes across 2 chapters: I72 — Other aneurysm (via Q27.3.-), P29 — Cardiovascular disorders originating in the perinatal period (via Q27.-).
These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.
Referenced by 2 Code Also instructions across 2 chapters: I27.21 — Secondary pulmonary arterial hypertension (via Q27.-), Z71.87 — Encounter for pediatric-to-adult transition counseling (via Q27.-).
These codes suggest coding this condition alongside when both are present.
MS-DRG Grouper Relationships (FY2027)
Potential MS-DRG participation — not a DRG assignment.
FY2027 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.
Named in the grouper logic of 3 MS-DRGs: DRG 299 (MDC 05), DRG 300 (MDC 05), DRG 301 (MDC 05).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Clinical classification (AHRQ CCSR):MAL001 — Cardiac and circulatory congenital anomalies (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Cardiac and circulatory congenital anomalies).
Q26.6 — Portal vein-hepatic artery fistula, Q26.8 — Other congenital malformations of great veins, Q26.9 — Congenital malformation of great vein, unspecified, Q27.0 — Congenital absence and hypoplasia of umbilical artery, Q27.1 — Congenital renal artery stenosis, Q27.2 — Other congenital malformations of renal artery, Q27.30 — Arteriovenous malformation, site unspecified, Q27.31 — Arteriovenous malformation of vessel of upper limb, Q27.32 — Arteriovenous malformation of vessel of lower limb, Q27.33 — Arteriovenous malformation of digestive system vessel, Q27.34 — Arteriovenous malformation of renal vessel, Q27.4 — Congenital phlebectasia, Q27.8 — Other specified congenital malformations of peripheral vascular system, Q27.9 — Congenital malformation of peripheral vascular system, unspecified, Q28.0 — Arteriovenous malformation of precerebral vessels, Q28.1 — Other malformations of precerebral vessels, Q28.2 — Arteriovenous malformation of cerebral vessels, Q28.3 — Other malformations of cerebral vessels, Q28.8 — Other specified congenital malformations of circulatory system, Q28.9 — Congenital malformation of circulatory system, unspecified, +87 more
Same Index main term, other category
The ICD-10-CM Index to Diseases and Injuries files this code under the main term “Malformation”; these codes share that main term but sit in a different category of the Tabular List.
Q25.9 — Congenital malformation of great arteries, unspecified (great, artery), Q26.0 — Congenital stenosis of vena cava (great, vein, vena cava stenosis, congenital), Q26.1 — Persistent left superior vena cava (great, vein, persistent left superior vena cava), Q26.2 — Total anomalous pulmonary venous connection (great, vein, anomalous, pulmonary venous connection, total), Q26.3 — Partial anomalous pulmonary venous connection (great, vein, anomalous, pulmonary venous connection, partial), Q26.4 — Anomalous pulmonary venous connection, unspecified (great, vein, anomalous, pulmonary venous connection), Q26.5 — Anomalous portal venous connection (great, vein, anomalous, portal venous connection), Q26.6 — Portal vein-hepatic artery fistula (great, vein, portal vein-hepatic artery fistula), Q26.8 — Other congenital malformations of great veins (great, vein, specified type NEC), Q26.9 — Congenital malformation of great vein, unspecified (great, vein), Q28.0 — Arteriovenous malformation of precerebral vessels (arteriovenous, aneurysmatic, precerebral vessels), Q28.1 — Other malformations of precerebral vessels (precerebral vessels), Q28.2 — Arteriovenous malformation of cerebral vessels (brain, arteriovenous), Q28.3 — Other malformations of cerebral vessels (cerebral, vessels), Q28.9 — Congenital malformation of circulatory system, unspecified (circulatory system), Q30.8 — Other congenital malformations of nose (nose, specified type NEC), Q30.9 — Congenital malformation of nose, unspecified (nose), Q32.1 — Other congenital malformations of trachea (trachea), Q32.4 — Other congenital malformations of bronchus (bronchus), Q33.9 — Congenital malformation of lung, unspecified (lung), +156 more
Contextual Map
Every relationship of Q27.39 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Run Q27.39 with these 6 related codes in Claim Check
Hierarchy
- Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
Referenced by Excludes1 notes
- I77.0 — Arteriovenous fistula, acquired[Excludes1](via Q27.3.-): “arteriovenous aneurysm NOS (Q27.3-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
- Q27.8 — Other specified congenital malformations of peripheral vascular system[Excludes1](via Q27.3.-): “arteriovenous malformation (Q27.3-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
Referenced by Excludes2 notes
- I72 — Other aneurysm[Excludes2](via Q27.3.-): “aneurysm (of) arteriovenous NOS (Q27.3-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
- P29 — Cardiovascular disorders originating in the perinatal period[Excludes2](via Q27.-): “congenital malformations of the circulatory system (Q20-Q28)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
Referenced by Code Also instructions
- I27.21 — Secondary pulmonary arterial hypertension[Code Also](via Q27.-): “congenital heart disease (Q20-Q28)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
- Z71.87 — Encounter for pediatric-to-adult transition counseling[Code Also](via Q27.-): “congenital malformations of the circulatory system (Q20-Q28)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
Clinical classification (CCSR)
- MAL001 — Cardiac and circulatory congenital anomalies[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
MS-DRG Grouper
- DRG 299 — PERIPHERAL VASCULAR DISORDERS WITH MCC[MS-DRG]: “PERIPHERAL VASCULAR DISORDERS WITH MCC (MDC 05)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2027
- DRG 300 — PERIPHERAL VASCULAR DISORDERS WITH CC[MS-DRG]: “PERIPHERAL VASCULAR DISORDERS WITH CC (MDC 05)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2027
- DRG 301 — PERIPHERAL VASCULAR DISORDERS WITHOUT CC/MCC[MS-DRG]: “PERIPHERAL VASCULAR DISORDERS WITHOUT CC/MCC (MDC 05)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2027
MDC crossing
- MDC 05 — Diseases and Disorders of the Circulatory System[MDC crossing]: “Diseases and Disorders of the Circulatory System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 15,708 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2027
Index entries
- Malformation (congenital), arteriovenous, aneurysmatic (congenital), peripheral, other specified site[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2027
Nearest codes (13)
- Q27 — Other congenital malformations of peripheral vascular system[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q27.0 — Congenital absence and hypoplasia of umbilical artery[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q27.1 — Congenital renal artery stenosis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q27.2 — Other congenital malformations of renal artery[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q27.3 — Arteriovenous malformation (peripheral)[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q27.30 — Arteriovenous malformation, site unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q27.31 — Arteriovenous malformation of vessel of upper limb[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- Q27.32 — Arteriovenous malformation of vessel of lower limb[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- and 5 more
Change history
- FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016
Reference
Index terms and tables, published questions and FAQ, every source behind this page with its release and checksum, the date-of-service check and the complete change history.
Indexed Clinical Terms (1)
Official source data — entries quoted as published, in the Index’s own lookup phrasing
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
- Inpatient payment groups Official source data
- CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v44 Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder-derived relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder editorial explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Current data releases:ICD-10-CM FY2027 · ICD-10-PCS FY2027 · HCPCS October 2026 · MS-DRG v44 · Medicare Code Editor v44.0 · NCCI PTP Q4 2026 · MUE Q4 2026 · NCD code lists 2026-01 · LCD export September 20, 2026 · All releases and sources
Labels on this page: Official source data · MedCoder-derived relationship · MedCoder editorial explanation. How to read the labels · All data sources and release dates · CMS coding rules
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "Q27.39 — Arteriovenous malformation, other site." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/q27.39-arteriovenous-malformation-other-site
Change history
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionArteriovenous malformation, other site
No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027, and none are recorded for this code. Note changes are tracked from FY2027 only.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q27.39 in its code family, with their registry titles.
- Q27.2 — Other congenital malformations of renal artery
- Q27.3 — Arteriovenous malformation (peripheral)
- Q27.30 — Arteriovenous malformation, site unspecified
- Q27.31 — Arteriovenous malformation of vessel of upper limb
- Q27.32 — Arteriovenous malformation of vessel of lower limb
- Q27.33 — Arteriovenous malformation of digestive system vessel
- Q27.34 — Arteriovenous malformation of renal vessel
- Q27.4 — Congenital phlebectasia
- Q27.8 — Other specified congenital malformations of peripheral vascular system
- Q27.9 — Congenital malformation of peripheral vascular system, unspecified