Q75.0 ICD-10-CM Code: Craniosynostosis
Billing Status: NO. This is a clinician non-billable / parent hierarchy grouping in the ICD-10-CM system.
Coding at a Glance
- Tabular directives
- 9 Excludes1
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q75.0 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025
Notes without a marker are published on Q75.0 itself; “inherited from” names the category or block whose note applies here.
Excludes1 — Not Coded Here
Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
- congenital malformation of face NOS (Q18.-) inherited from Q75Compare Q75.0 vs Q18 →
- congenital malformation syndromes classified to Q87.- inherited from Q75
- dentofacial anomalies including malocclusion
- musculoskeletal deformities of head and face (Q67.0-Q67.4) inherited from Q75Compare Q75.0 vs Q67.0 →
- skull defects associated with congenital anomalies of brain such as:
- anencephaly (Q00.0) inherited from Q75Compare Q75.0 vs Q00.0 →
- encephalocele (Q01.-) inherited from Q75Compare Q75.0 vs Q01 →
- hydrocephalus (Q03.-) inherited from Q75Compare Q75.0 vs Q03 →
- microcephaly (Q02) inherited from Q75Compare Q75.0 vs Q02 →
Coder workflow for Q75.0
MedCoder structured workflow — derived from this code’s own official record
Before you code Q75.0
- Q75.0 is not reportable as written. Select the more specific code beneath it that the documentation supports. Codes are reported to the highest level of specificity the classification provides (Guidelines I.B.2).
ReviewQ75.00, Q75.01, Q75.02, Q75.03, Q75.04, Q75.05, Q75.08
See the relationships section · Guide: How to choose an ICD-10-CM code →
- Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with Q75.0. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).
Choose the right path
- Does the documentation support one of the more specific codes beneath Q75.0?
Yes → Select that code and continue the checks below on its own page.
No → Q75.0 cannot be reported as written; query for the specificity its subcategory needs.ReviewQ75.00, Q75.01, Q75.02, Q75.03, Q75.04, Q75.05, Q75.08
- Does the documentation support a condition named in Q75.0’s Excludes1 note?
Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
No → Continue.
Consider Q75.0. Then confirm the code is valid for the date of service in the Verify section.
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
Official instructions as workflow
Excludes1 — check before selecting Q75.0(9 notes)
Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with Q75.0: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.
CompareQ18, Q87, Q00.0, Q01, Q03, Q02
See the official tabular notes · Guidelines I.A.12.a
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: Both the condition Q75.0 describes and a condition named in its Excludes1 note are documented for the same encounter.
Coding question: Can both codes be reported?
Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.
Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Verify Before Coding
- Not billable as written — a more specific code is required: Q75.001, Q75.002, Q75.009, Q75.01, Q75.021.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder structured relationships — computed from published CMS and AHRQ datasets
Other codes that name Q75.0 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.
Referenced by 2 Excludes1 notes across 2 chapters: M24.3 — Pathological dislocation of joint, not elsewhere classified (via Q75.-), Q18 — Other congenital malformations of face and neck (via Q75.-).
These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.
Referenced by 1 Excludes2 note: M95 — Other acquired deformities of musculoskeletal system and connective tissue (via Q75.-).
These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.
Clinical classification (AHRQ CCSR):MAL008 — Musculoskeletal congenital conditions (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Musculoskeletal congenital conditions).
Q72.93 — Unspecified reduction defect of lower limb, bilateral, Q73.0 — Congenital absence of unspecified limb(s), Q73.1 — Phocomelia, unspecified limb(s), Q73.8 — Other reduction defects of unspecified limb(s), Q74.0 — Other congenital malformations of upper limb(s), including shoulder girdle, Q74.1 — Congenital malformation of knee, Q74.2 — Other congenital malformations of lower limb(s), including pelvic girdle, Q74.3 — Arthrogryposis multiplex congenita, Q74.8 — Other specified congenital malformations of limb(s), Q74.9 — Unspecified congenital malformation of limb(s), Q75.001 — Craniosynostosis, unspecified type, unilateral, Q75.002 — Craniosynostosis, unspecified type, bilateral, Q75.009 — Craniosynostosis, unspecified, Q75.01 — Sagittal craniosynostosis, Q75.021 — Coronal craniosynostosis, unilateral, Q75.022 — Coronal craniosynostosis, bilateral, Q75.029 — Coronal craniosynostosis, unspecified, Q75.03 — Metopic craniosynostosis, Q75.041 — Lambdoid craniosynostosis, unilateral, Q75.042 — Lambdoid craniosynostosis, bilateral, +245 more
Contextual Map
Every relationship of Q75.0 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Run Q75.0 with these 3 related codes in Claim Check
Hierarchy
- Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q65-Q79 — Congenital malformations and deformations of the musculoskeletal system[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Referenced by Excludes1 notes
- M24.3 — Pathological dislocation of joint, not elsewhere classified[Excludes1](via Q75.-): “congenital dislocation or displacement of joint- see congenital malformations and deformations of the musculoskeletal system (Q65-Q79)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- Q18 — Other congenital malformations of face and neck[Excludes1](via Q75.-): “congenital malformations of skull and face bones (Q75.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Referenced by Excludes2 notes
- M95 — Other acquired deformities of musculoskeletal system and connective tissue[Excludes2](via Q75.-): “congenital malformations and deformations of the musculoskeletal system (Q65-Q79)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Clinical classification (CCSR)
- MAL008 — Musculoskeletal congenital conditions[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
Nearest codes (27)
- Q75 — Other congenital malformations of skull and face bones[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q75.00 — Craniosynostosis, unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q75.001 — Craniosynostosis, unspecified type, unilateral[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q75.002 — Craniosynostosis, unspecified type, bilateral[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q75.009 — Craniosynostosis, unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q75.01 — Sagittal craniosynostosis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q75.02 — Coronal craniosynostosis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q75.021 — Coronal craniosynostosis, unilateral[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- and 19 more
Change history (2)
- FY2024 — Became a non-billable header[Change history]— CMS release files (code change ledger) · icd10cm-fy2024
- and 1 more
Common coding questions
Can Q75.0 be billed directly?
No. Q75.0 (Craniosynostosis) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder structured relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "Q75.0 — Craniosynostosis." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/q75.0-craniosynostosis
Change history
- FY2024 — October 1, 2023Became a non-billable headerFY2024 changes
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionCraniosynostosis
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q75.0 in its code family, with their registry titles.
- Q75 — Other congenital malformations of skull and face bones
- Q75.00 — Craniosynostosis, unspecified
- Q75.001 — Craniosynostosis, unspecified type, unilateral
- Q75.002 — Craniosynostosis, unspecified type, bilateral
- Q75.009 — Craniosynostosis, unspecified
- Q75.01 — Sagittal craniosynostosis
- Q75.02 — Coronal craniosynostosis
- Q75.021 — Coronal craniosynostosis, unilateral
- Q75.022 — Coronal craniosynostosis, bilateral
- Q75.029 — Coronal craniosynostosis, unspecified