Q99.89 ICD-10-CM Code: Other specified chromosome abnormalities
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Coding at a Glance
- Tabular directives
- 1 Excludes2
Inpatient Payment Groups (MS-DRG)
Potential MS-DRG participation — not a DRG assignment.
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.
- MS-DRG 729 — OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITH CC/MCC (MDC 12)
- MS-DRG 730 — OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITHOUT CC/MCC (MDC 12)
- MS-DRG 742 — UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITH CC/MCC (MDC 13)
- MS-DRG 743 — UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITHOUT CC/MCC (MDC 13)
- MS-DRG 760 — MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITH CC/MCC (MDC 13)
- MS-DRG 761 — MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITHOUT CC/MCC (MDC 13)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for Q99.89 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025
Notes without a marker are published on Q99.89 itself; “inherited from” names the category or block whose note applies here.
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- mitochondrial metabolic disorders (E88.4-) Compare Q99.89 vs E88.4 →
Source: inherited from Q90-Q99
Coder workflow for Q99.89
MedCoder structured workflow — derived from this code’s own official record
Before you code Q99.89
- “Other” (NEC) means the condition is specified in the record but no dedicated code captures it. Confirm the documented form is not one a sibling code names before settling on Q99.89; if the record states no specifics at all, the unspecified sibling applies instead. “Other” codes are for documented conditions the classification gives no specific code; “unspecified” codes are for records lacking the detail (Guidelines I.A.9.a, I.A.9.b).
ReviewQ99.81
See the relationships section · Guide: Other vs unspecified (NEC vs NOS) →
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
- Any detail beyond this code’s title
- What the record states that a more specific sibling code would capture — or its absence, which itself supports the unspecified code.
Official instructions as workflow
Excludes2 — not part of Q99.89(1 note)
Coding workflow: The conditions named in this note are not included in Q99.89. When the record documents both, both may be reported; the note is a boundary, not a prohibition.
CompareE88.4
See the official tabular notes · Guidelines I.A.12.b
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Verify Before Coding
- No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder structured relationships — computed from published CMS and AHRQ datasets
Other codes that name Q99.89 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.
Referenced by 10 Excludes1 notes across 3 chapters: E25 — Adrenogenital disorders (via Q99.-), Q50 — Congenital malformations of ovaries, fallopian tubes and broad ligaments (via Q99.-), Q50-Q56 — Congenital malformations of genital organs (Q50-Q56) (via Q99.-), Q51 — Congenital malformations of uterus and cervix (via Q99.-), Q52 — Other congenital malformations of female genitalia (via Q99.-), Q53 — Undescended and ectopic testicle (via Q99.-), Q54 — Hypospadias (via Q99.-), Q55 — Other congenital malformations of male genital organs (via Q99.-), Q56 — Indeterminate sex and pseudohermaphroditism (via Q99.-), Z15 — Genetic susceptibility to disease (via Q99.-).
These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.
Referenced by 1 Code First instruction: D84.81 — Immunodeficiency due to conditions classified elsewhere (via Q99.-).
Each of these codes carries a Code First note naming this condition — when that code is reported, THIS code is sequenced first, ahead of it.
MS-DRG Grouper Relationships (FY2026)
Potential MS-DRG participation — not a DRG assignment.
FY2026 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.
Named in the grouper logic of 6 MS-DRGs: DRG 729 (MDC 12), DRG 730 (MDC 12), DRG 742 (MDC 13), DRG 743 (MDC 13), DRG 760 (MDC 13), DRG 761 (MDC 13).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Clinical classification (AHRQ CCSR):MAL009 — Chromosomal abnormalities (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Chromosomal abnormalities).
Q97.9 — Sex chromosome abnormality, female phenotype, unspecified, Q98.0 — Klinefelter syndrome karyotype 47, XXY, Q98.1 — Klinefelter syndrome, male with more than two X chromosomes, Q98.3 — Other male with 46, XX karyotype, Q98.4 — Klinefelter syndrome, unspecified, Q98.5 — Karyotype 47, XYY, Q98.6 — Male with structurally abnormal sex chromosome, Q98.7 — Male with sex chromosome mosaicism, Q98.8 — Other specified sex chromosome abnormalities, male phenotype, Q98.9 — Sex chromosome abnormality, male phenotype, unspecified, Q99.0 — Chimera 46, XX/46, XY, Q99.1 — 46, XX true hermaphrodite, Q99.2 — Fragile X chromosome, Q99.8 — Other specified chromosome abnormalities, Q99.811 — Usher syndrome, type 1, Q99.812 — Usher syndrome, type 2, Q99.813 — Usher syndrome, type 3, Q99.818 — Other Usher syndrome, Q99.819 — Usher syndrome, unspecified, Q99.9 — Chromosomal abnormality, unspecified, +56 more
Contextual Map
Every relationship of Q99.89 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Run Q99.89 with these 9 related codes in Claim Check
Hierarchy
- Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Referenced by Excludes1 notes (10)
- E25 — Adrenogenital disorders[Excludes1](via Q99.-): “chromosomal abnormalities (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- Q50 — Congenital malformations of ovaries, fallopian tubes and broad ligaments[Excludes1](via Q99.-): “syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- Q50-Q56 — Congenital malformations of genital organs (Q50-Q56)[Excludes1](via Q99.-): “syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- Q51 — Congenital malformations of uterus and cervix[Excludes1](via Q99.-): “syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- Q52 — Other congenital malformations of female genitalia[Excludes1](via Q99.-): “syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- Q53 — Undescended and ectopic testicle[Excludes1](via Q99.-): “syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- Q54 — Hypospadias[Excludes1](via Q99.-): “syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- Q55 — Other congenital malformations of male genital organs[Excludes1](via Q99.-): “syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- and 2 more
Referenced by Code First instructions
- D84.81 — Immunodeficiency due to conditions classified elsewhere[Code First](via Q99.-): “chromosomal abnormalities (Q90-Q99)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Clinical classification (CCSR)
- MAL009 — Chromosomal abnormalities[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
MS-DRG Grouper
- DRG 729 — OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITH CC/MCC[MS-DRG]: “OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITH CC/MCC (MDC 12)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 730 — OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITHOUT CC/MCC[MS-DRG]: “OTHER MALE REPRODUCTIVE SYSTEM DIAGNOSES WITHOUT CC/MCC (MDC 12)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 742 — UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITH CC/MCC[MS-DRG]: “UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITH CC/MCC (MDC 13)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 743 — UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITHOUT CC/MCC[MS-DRG]: “UTERINE AND ADNEXA PROCEDURES FOR NON-MALIGNANCY WITHOUT CC/MCC (MDC 13)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 760 — MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITH CC/MCC[MS-DRG]: “MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITH CC/MCC (MDC 13)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 761 — MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITHOUT CC/MCC[MS-DRG]: “MENSTRUAL AND OTHER FEMALE REPRODUCTIVE SYSTEM DISORDERS WITHOUT CC/MCC (MDC 13)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
MDC crossing
- MDC 12 — Diseases and Disorders of the Male Reproductive System[MDC crossing]: “Diseases and Disorders of the Male Reproductive System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 1,964 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026
- MDC 13 — Diseases and Disorders of the Female Reproductive System[MDC crossing]: “Diseases and Disorders of the Female Reproductive System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 2,232 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026
Nearest codes (12)
- Q99 — Other chromosome abnormalities, not elsewhere classified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q99.0 — Chimera 46, XX/46, XY[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q99.1 — 46, XX true hermaphrodite[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q99.2 — Fragile X chromosome[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q99.8 — Other specified chromosome abnormalities[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q99.81 — Usher syndrome[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q99.811 — Usher syndrome, type 1[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q99.812 — Usher syndrome, type 2[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- and 4 more
Change history
- FY2026 — Added to the code set[Change history]— CMS release files (code change ledger) · icd10cm-fy2026
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
- Inpatient payment groups Official source data
- CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder structured relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "Q99.89 — Other specified chromosome abnormalities." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/q99.89-other-specified-chromosome-abnormalities
Change history
- FY2026 — October 1, 2025Added to the code setOther specified chromosome abnormalitiesFY2026 changes
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q99.89 in its code family, with their registry titles.
- Q99.1 — 46, XX true hermaphrodite
- Q99.2 — Fragile X chromosome
- Q99.8 — Other specified chromosome abnormalities
- Q99.81 — Usher syndrome
- Q99.811 — Usher syndrome, type 1
- Q99.812 — Usher syndrome, type 2
- Q99.813 — Usher syndrome, type 3
- Q99.818 — Other Usher syndrome
- Q99.819 — Usher syndrome, unspecified
- Q99.9 — Chromosomal abnormality, unspecified