Skip to main content
Clinical Concepts/MUS024

Systemic lupus erythematosus and connective tissue disorders

CCSR category MUS024 · 93 ICD-10-CM codes

Code Families in This Category

  • M35 Other systemic involvement of connective tissue · 24
  • M33 Dermatopolymyositis · 19
  • M31 Other necrotizing vasculopathies · 14
  • M32 Systemic lupus erythematosus (SLE) · 10
  • M34 Systemic sclerosis [scleroderma] · 8
  • H01 Other inflammation of eyelid · 7
  • M30 Polyarteritis nodosa and related conditions · 5
  • L93 Lupus erythematosus · 3
  • M36 Systemic disorders of connective tissue in diseases classified elsewhere · 2
  • E83 Disorders of mineral metabolism · 1

ICD-10-CM Codes in This Category (93)

  • E83.824 — ABCC6 deficiency causing pseudoxanthoma elasticum
  • H01.121 — Discoid lupus erythematosus of right upper eyelid
  • H01.122 — Discoid lupus erythematosus of right lower eyelid
  • H01.123 — Discoid lupus erythematosus of right eye, unspecified eyelid
  • H01.124 — Discoid lupus erythematosus of left upper eyelid
  • H01.125 — Discoid lupus erythematosus of left lower eyelid
  • H01.126 — Discoid lupus erythematosus of left eye, unspecified eyelid
  • H01.129 — Discoid lupus erythematosus of unspecified eye, unspecified eyelid
  • L93.0 — Discoid lupus erythematosus
  • L93.1 — Subacute cutaneous lupus erythematosus
  • L93.2 — Other local lupus erythematosus
  • M30.0 — Polyarteritis nodosa
  • M30.1 — Polyarteritis with lung involvement [Churg-Strauss]
  • M30.2 — Juvenile polyarteritis
  • M30.3 — Mucocutaneous lymph node syndrome [Kawasaki]
  • M30.8 — Other conditions related to polyarteritis nodosa
  • M31.0 — Hypersensitivity angiitis
  • M31.1 — Thrombotic microangiopathy
  • M31.10 — Thrombotic microangiopathy, unspecified
  • M31.11 — Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]
  • M31.19 — Other thrombotic microangiopathy
  • M31.2 — Lethal midline granuloma
  • M31.30 — Wegener's granulomatosis without renal involvement
  • M31.31 — Wegener's granulomatosis with renal involvement
  • M31.4 — Aortic arch syndrome [Takayasu]
  • M31.5 — Giant cell arteritis with polymyalgia rheumatica
  • M31.6 — Other giant cell arteritis
  • M31.7 — Microscopic polyangiitis
  • M31.8 — Other specified necrotizing vasculopathies
  • M31.9 — Necrotizing vasculopathy, unspecified
  • M32.0 — Drug-induced systemic lupus erythematosus
  • M32.10 — Systemic lupus erythematosus, organ or system involvement unspecified
  • M32.11 — Endocarditis in systemic lupus erythematosus
  • M32.12 — Pericarditis in systemic lupus erythematosus
  • M32.13 — Lung involvement in systemic lupus erythematosus
  • M32.14 — Glomerular disease in systemic lupus erythematosus
  • M32.15 — Tubulo-interstitial nephropathy in systemic lupus erythematosus
  • M32.19 — Other organ or system involvement in systemic lupus erythematosus
  • M32.8 — Other forms of systemic lupus erythematosus
  • M32.9 — Systemic lupus erythematosus, unspecified
  • M33.00 — Juvenile dermatomyositis, organ involvement unspecified
  • M33.01 — Juvenile dermatomyositis with respiratory involvement
  • M33.02 — Juvenile dermatomyositis with myopathy
  • M33.03 — Juvenile dermatomyositis without myopathy
  • M33.09 — Juvenile dermatomyositis with other organ involvement
  • M33.10 — Other dermatomyositis, organ involvement unspecified
  • M33.11 — Other dermatomyositis with respiratory involvement
  • M33.12 — Other dermatomyositis with myopathy
  • M33.13 — Other dermatomyositis without myopathy
  • M33.19 — Other dermatomyositis with other organ involvement
  • M33.20 — Polymyositis, organ involvement unspecified
  • M33.21 — Polymyositis with respiratory involvement
  • M33.22 — Polymyositis with myopathy
  • M33.29 — Polymyositis with other organ involvement
  • M33.90 — Dermatopolymyositis, unspecified, organ involvement unspecified
  • M33.91 — Dermatopolymyositis, unspecified with respiratory involvement
  • M33.92 — Dermatopolymyositis, unspecified with myopathy
  • M33.93 — Dermatopolymyositis, unspecified without myopathy
  • M33.99 — Dermatopolymyositis, unspecified with other organ involvement
  • M34.0 — Progressive systemic sclerosis
  • M34.1 — CR(E)ST syndrome
  • M34.2 — Systemic sclerosis induced by drug and chemical
  • M34.81 — Systemic sclerosis with lung involvement
  • M34.82 — Systemic sclerosis with myopathy
  • M34.83 — Systemic sclerosis with polyneuropathy
  • M34.89 — Other systemic sclerosis
  • M34.9 — Systemic sclerosis, unspecified
  • M35.00 — Sjögren syndrome, unspecified
  • M35.01 — Sjögren syndrome with keratoconjunctivitis
  • M35.02 — Sjögren syndrome with lung involvement
  • M35.03 — Sjögren syndrome with myopathy
  • M35.04 — Sjögren syndrome with tubulo-interstitial nephropathy
  • M35.05 — Sjögren syndrome with inflammatory arthritis
  • M35.06 — Sjögren syndrome with peripheral nervous system involvement
  • M35.07 — Sjögren syndrome with central nervous system involvement
  • M35.08 — Sjögren syndrome with gastrointestinal involvement
  • M35.09 — Sjögren syndrome with other organ involvement
  • M35.0A — Sjögren syndrome with glomerular disease
  • M35.0B — Sjögren syndrome with vasculitis
  • M35.0C — Sjögren syndrome with dental involvement
  • M35.1 — Other overlap syndromes
  • M35.2 — Behçet's disease
  • M35.3 — Polymyalgia rheumatica
  • M35.4 — Diffuse (eosinophilic) fasciitis
  • M35.5 — Multifocal fibrosclerosis
  • M35.6 — Relapsing panniculitis [Weber-Christian]
  • M35.7 — Hypermobility syndrome
  • M35.8 — Other specified systemic involvement of connective tissue
  • M35.81 — Multisystem inflammatory syndrome
  • M35.89 — Other specified systemic involvement of connective tissue
  • M35.9 — Systemic involvement of connective tissue, unspecified
  • M36.0 — Dermato(poly)myositis in neoplastic disease
  • M36.8 — Systemic disorders of connective tissue in other diseases classified elsewhere

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, Rockville, MD. All data sources.