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M35.2 ICD-10-CM Code: Behçet's disease

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Inpatient Payment Groups (MS-DRG)

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0, Appendix B.

  • MS-DRG 545 — CONNECTIVE TISSUE DISORDERS WITH MCC (MDC 08)
  • MS-DRG 546 — CONNECTIVE TISSUE DISORDERS WITH CC (MDC 08)
  • MS-DRG 547 — CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC (MDC 08)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Risk Adjustment (CMS-HCC)

Payment categories this diagnosis maps to under CMS-HCC V28, payment year 2026.

  • HCC 94 — Systemic Lupus Erythematosus and Other Specified Systemic Connective Tissue Disorders

Other models: CMS-HCC V22 HCC 40 · RxHCC V08 HCC 83

Risk scores depend on the enrollee's full accepted diagnosis set and segment; a category mapping alone does not determine payment.

Official Registry Overview & Definition

Behçet's disease is a billable ICD-10-CM diagnosis code (M35.2).

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for M35.2 in the official ICD-10-CM tabular list.

Includes

Conditions the official ICD-10-CM tabular list includes under this code.

  • autoimmune disease NOS
  • collagen (vascular) disease NOS
  • systemic autoimmune disease
  • systemic collagen (vascular) disease

Excludes1 — Not Coded Here

Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

  • reactive perforating collagenosis (L87.1) Compare M35.2 vs L87.1 →
  • autoimmune disease, single organ or single cell-type -code to relevant condition category

Indexed Clinical Terms (4)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute), in (due to), Behçet's syndrome
  • Behçet's disease or syndrome
  • Ulcer, ulcerated, ulcerating, ulceration, ulcerative, vagina, in Behçet's disease
  • Ulcer, ulcerated, ulcerating, ulceration, ulcerative, vulva (acute) (infectional), in (due to), Behçet's disease

Frequently Compared Codes

The official Excludes notes on M35.2 name these codes. Each comparison page covers when the two can — or must not — be reported together.

Change history

No changes recorded for this code — unchanged since the FY2016 baseline of the change ledger.

Verify Before Coding

  • CC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim.

Relationships & Classification

Official ICD-10-CM tabular notes on other codes that name M35.2 or its code family.

1 Excludes1 notes: M02.

1 Excludes2 notes: M45.

1 Code First instructions: N77.0.

Potential MS-DRG Relationships (FY2026)

CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 942 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 3 MS-DRGs: DRG 545 (MDC 08), DRG 546 (MDC 08), DRG 547 (MDC 08).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MUS024 — Systemic lupus erythematosus and connective tissue disorders (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Contextual Map

Every relationship of M35.2 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Hierarchy

  • M00-M99 — Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue (M00-M99) (M00-M99) [Hierarchy]
  • M30-M36 — Systemic connective tissue disorders [Hierarchy]

Referenced by Excludes1 notes

  • M02 — Postinfective and reactive arthropathies [Excludes1]: “Behçet's disease (M35.2)” · check together

Referenced by Excludes2 notes

  • M45 — Ankylosing spondylitis [Excludes2]: “Behçet's disease (M35.2)” · check together

Referenced by Code First instructions

  • N77.0 — Ulceration of vulva in diseases classified elsewhere [Code First]: “Behçet's disease (M35.2)” · check together

Clinical classification (CCSR)

  • MUS024 — Systemic lupus erythematosus and connective tissue disorders [CCSR]

Risk adjustment (CMS-HCC)

  • HCC 94 — Systemic Lupus Erythematosus and Other Specified Systemic Connective Tissue Disorders [CMS-HCC]

Potential MS-DRG

  • CC — Complication or Comorbidity [MS-DRG severity]: “As a secondary diagnosis this code can raise the stay's MS-DRG severity tier (CC).”
  • DRG 545 — CONNECTIVE TISSUE DISORDERS WITH MCC [MS-DRG]: “CONNECTIVE TISSUE DISORDERS WITH MCC (MDC 08)”
  • DRG 546 — CONNECTIVE TISSUE DISORDERS WITH CC [MS-DRG]: “CONNECTIVE TISSUE DISORDERS WITH CC (MDC 08)”
  • DRG 547 — CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC [MS-DRG]: “CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC (MDC 08)”

MDC crossing · procedures (18508)

  • MDC 08 — Diseases and Disorders of the Musculoskeletal System and Connective Tissue [MDC crossing]: “Diseases and Disorders of the Musculoskeletal System and Connective Tissue — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs.”
  • 005T0ZZ — Destruction of Spinal Meninges, Open Approach [Same-MDC procedure]: “Destruction of Spinal Meninges, Open Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • 005T3ZZ — Destruction of Spinal Meninges, Percutaneous Approach [Same-MDC procedure]: “Destruction of Spinal Meninges, Percutaneous Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • 005T4ZZ — Destruction of Spinal Meninges, Percutaneous Endoscopic Approach [Same-MDC procedure]: “Destruction of Spinal Meninges, Percutaneous Endoscopic Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • 005W0Z3 — Destruction of Cervical Spinal Cord using Laser Interstitial Thermal Therapy, Open Approach [Same-MDC procedure]: “Destruction of Cervical Spinal Cord using Laser Interstitial Thermal Therapy, Open Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • 005W0ZZ — Destruction of Cervical Spinal Cord, Open Approach [Same-MDC procedure]: “Destruction of Cervical Spinal Cord, Open Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • and 18503 more

Index entries

  • Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute), in (due to), Behçet's syndrome[Index term]
  • Behçet's disease or syndrome[Index term]
  • Ulcer, ulcerated, ulcerating, ulceration, ulcerative, vagina, in Behçet's disease[Index term]
  • Ulcer, ulcerated, ulcerating, ulceration, ulcerative, vulva (acute) (infectional), in (due to), Behçet's disease[Index term]

Nearest codes (25)

  • M35 — Other systemic involvement of connective tissue [Sibling]
  • M35.0 — Sjögren syndrome [Sibling]
  • M35.00 — Sjögren syndrome, unspecified [Sibling]
  • M35.01 — Sjögren syndrome with keratoconjunctivitis [Sibling]
  • M35.02 — Sjögren syndrome with lung involvement [Sibling]
  • M35.03 — Sjögren syndrome with myopathy [Sibling]
  • M35.04 — Sjögren syndrome with tubulo-interstitial nephropathy [Sibling]
  • M35.05 — Sjögren syndrome with inflammatory arthritis [Sibling]
  • and 17 more

Nearest Codes in This Family

Official ICD-10-CM classifications closest to M35.2 in its code family, with their registry titles.

  • M35.09 — Sjögren syndrome with other organ involvement
  • M35.0A — Sjögren syndrome with glomerular disease
  • M35.0B — Sjögren syndrome with vasculitis
  • M35.0C — Sjögren syndrome with dental involvement
  • M35.1 — Other overlap syndromes
  • M35.3 — Polymyalgia rheumatica
  • M35.4 — Diffuse (eosinophilic) fasciitis
  • M35.5 — Multifocal fibrosclerosis
  • M35.6 — Relapsing panniculitis [Weber-Christian]
  • M35.7 — Hypermobility syndrome

View all codes in the M35 family