Nervous system congenital anomalies
CCSR category MAL004 · 50 ICD-10-CM codes
Code Families in This Category
- Q05 Spina bifida · 10
- Q04 Other congenital malformations of brain · 9
- Q06 Other congenital malformations of spinal cord · 7
- Q07 Other congenital malformations of nervous system · 6
- Q01 Encephalocele · 5
- Q85 Phakomatoses, not elsewhere classified · 5
- Q03 Congenital hydrocephalus · 4
- Q00 Anencephaly and similar malformations · 3
- Q02 Microcephaly · 1
ICD-10-CM Codes in This Category (50)
- Q00.0 — Anencephaly
- Q00.1 — Craniorachischisis
- Q00.2 — Iniencephaly
- Q01.0 — Frontal encephalocele
- Q01.1 — Nasofrontal encephalocele
- Q01.2 — Occipital encephalocele
- Q01.8 — Encephalocele of other sites
- Q01.9 — Encephalocele, unspecified
- Q02 — Microcephaly
- Q03.0 — Malformations of aqueduct of Sylvius
- Q03.1 — Atresia of foramina of Magendie and Luschka
- Q03.8 — Other congenital hydrocephalus
- Q03.9 — Congenital hydrocephalus, unspecified
- Q04.0 — Congenital malformations of corpus callosum
- Q04.1 — Arhinencephaly
- Q04.2 — Holoprosencephaly
- Q04.3 — Other reduction deformities of brain
- Q04.4 — Septo-optic dysplasia of brain
- Q04.5 — Megalencephaly
- Q04.6 — Congenital cerebral cysts
- Q04.8 — Other specified congenital malformations of brain
- Q04.9 — Congenital malformation of brain, unspecified
- Q05.0 — Cervical spina bifida with hydrocephalus
- Q05.1 — Thoracic spina bifida with hydrocephalus
- Q05.2 — Lumbar spina bifida with hydrocephalus
- Q05.3 — Sacral spina bifida with hydrocephalus
- Q05.4 — Unspecified spina bifida with hydrocephalus
- Q05.5 — Cervical spina bifida without hydrocephalus
- Q05.6 — Thoracic spina bifida without hydrocephalus
- Q05.7 — Lumbar spina bifida without hydrocephalus
- Q05.8 — Sacral spina bifida without hydrocephalus
- Q05.9 — Spina bifida, unspecified
- Q06.0 — Amyelia
- Q06.1 — Hypoplasia and dysplasia of spinal cord
- Q06.2 — Diastematomyelia
- Q06.3 — Other congenital cauda equina malformations
- Q06.4 — Hydromyelia
- Q06.8 — Other specified congenital malformations of spinal cord
- Q06.9 — Congenital malformation of spinal cord, unspecified
- Q07.00 — Arnold-Chiari syndrome without spina bifida or hydrocephalus
- Q07.01 — Arnold-Chiari syndrome with spina bifida
- Q07.02 — Arnold-Chiari syndrome with hydrocephalus
- Q07.03 — Arnold-Chiari syndrome with spina bifida and hydrocephalus
- Q07.8 — Other specified congenital malformations of nervous system
- Q07.9 — Congenital malformation of nervous system, unspecified
- Q85.00 — Neurofibromatosis, unspecified
- Q85.01 — Neurofibromatosis, type 1
- Q85.02 — Neurofibromatosis, type 2
- Q85.03 — Schwannomatosis
- Q85.09 — Other neurofibromatosis
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, Rockville, MD. All data sources.