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Nervous system congenital anomalies

CCSR category MAL004 · 50 ICD-10-CM codes

Code Families in This Category

  • Q05 Spina bifida · 10
  • Q04 Other congenital malformations of brain · 9
  • Q06 Other congenital malformations of spinal cord · 7
  • Q07 Other congenital malformations of nervous system · 6
  • Q01 Encephalocele · 5
  • Q85 Phakomatoses, not elsewhere classified · 5
  • Q03 Congenital hydrocephalus · 4
  • Q00 Anencephaly and similar malformations · 3
  • Q02 Microcephaly · 1

ICD-10-CM Codes in This Category (50)

  • Q00.0 — Anencephaly
  • Q00.1 — Craniorachischisis
  • Q00.2 — Iniencephaly
  • Q01.0 — Frontal encephalocele
  • Q01.1 — Nasofrontal encephalocele
  • Q01.2 — Occipital encephalocele
  • Q01.8 — Encephalocele of other sites
  • Q01.9 — Encephalocele, unspecified
  • Q02 — Microcephaly
  • Q03.0 — Malformations of aqueduct of Sylvius
  • Q03.1 — Atresia of foramina of Magendie and Luschka
  • Q03.8 — Other congenital hydrocephalus
  • Q03.9 — Congenital hydrocephalus, unspecified
  • Q04.0 — Congenital malformations of corpus callosum
  • Q04.1 — Arhinencephaly
  • Q04.2 — Holoprosencephaly
  • Q04.3 — Other reduction deformities of brain
  • Q04.4 — Septo-optic dysplasia of brain
  • Q04.5 — Megalencephaly
  • Q04.6 — Congenital cerebral cysts
  • Q04.8 — Other specified congenital malformations of brain
  • Q04.9 — Congenital malformation of brain, unspecified
  • Q05.0 — Cervical spina bifida with hydrocephalus
  • Q05.1 — Thoracic spina bifida with hydrocephalus
  • Q05.2 — Lumbar spina bifida with hydrocephalus
  • Q05.3 — Sacral spina bifida with hydrocephalus
  • Q05.4 — Unspecified spina bifida with hydrocephalus
  • Q05.5 — Cervical spina bifida without hydrocephalus
  • Q05.6 — Thoracic spina bifida without hydrocephalus
  • Q05.7 — Lumbar spina bifida without hydrocephalus
  • Q05.8 — Sacral spina bifida without hydrocephalus
  • Q05.9 — Spina bifida, unspecified
  • Q06.0 — Amyelia
  • Q06.1 — Hypoplasia and dysplasia of spinal cord
  • Q06.2 — Diastematomyelia
  • Q06.3 — Other congenital cauda equina malformations
  • Q06.4 — Hydromyelia
  • Q06.8 — Other specified congenital malformations of spinal cord
  • Q06.9 — Congenital malformation of spinal cord, unspecified
  • Q07.00 — Arnold-Chiari syndrome without spina bifida or hydrocephalus
  • Q07.01 — Arnold-Chiari syndrome with spina bifida
  • Q07.02 — Arnold-Chiari syndrome with hydrocephalus
  • Q07.03 — Arnold-Chiari syndrome with spina bifida and hydrocephalus
  • Q07.8 — Other specified congenital malformations of nervous system
  • Q07.9 — Congenital malformation of nervous system, unspecified
  • Q85.00 — Neurofibromatosis, unspecified
  • Q85.01 — Neurofibromatosis, type 1
  • Q85.02 — Neurofibromatosis, type 2
  • Q85.03 — Schwannomatosis
  • Q85.09 — Other neurofibromatosis

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, Rockville, MD. All data sources.