Q06.0 ICD-10-CM Code: Amyelia
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Coding at a Glance
Inpatient Payment Groups (MS-DRG)
Potential MS-DRG participation — not a DRG assignment.
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.
- MS-DRG 091 — OTHER DISORDERS OF NERVOUS SYSTEM WITH MCC (MDC 01)
- MS-DRG 092 — OTHER DISORDERS OF NERVOUS SYSTEM WITH CC (MDC 01)
- MS-DRG 093 — OTHER DISORDERS OF NERVOUS SYSTEM WITHOUT CC/MCC (MDC 01)
- MS-DRG 791 — PREMATURITY WITH MAJOR PROBLEMS (MDC 15)
- MS-DRG 793 — FULL TERM NEONATE WITH MAJOR PROBLEMS (MDC 15)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Risk Adjustment (CMS-HCC)
Payment categories this diagnosis maps to under CMS-HCC V28, payment year 2026.
- HCC 182 — Spinal Cord Disorders/Injuries
Other models: CMS-HCC V22 HCC 72 · RxHCC V08 HCC 155
Risk scores depend on the enrollee's full accepted diagnosis set and segment; a category mapping alone does not determine payment.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Indexed Clinical Terms (2)
Official source data — entries quoted as published, in the Index’s own lookup phrasing
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.
Verify Before Coding
- No Medicare Code Editor or MS-DRG Definitions Manual restrictions apply to this code.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder structured relationships — computed from published CMS and AHRQ datasets
MS-DRG Grouper Relationships (FY2026)
Potential MS-DRG participation — not a DRG assignment.
FY2026 MS-DRG: not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity for that release.
Named in the grouper logic of 5 MS-DRGs: DRG 091 (MDC 01), DRG 092 (MDC 01), DRG 093 (MDC 01), DRG 791 (MDC 15), DRG 793 (MDC 15).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Clinical classification (AHRQ CCSR):MAL004 — Nervous system congenital anomalies (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same CMS-HCC risk category (V28)
CMS maps these diagnoses to the same Hierarchical Condition Category (Spinal Cord Disorders/Injuries) for risk-adjusted payment.
Q05.0 — Cervical spina bifida with hydrocephalus, Q05.1 — Thoracic spina bifida with hydrocephalus, Q05.2 — Lumbar spina bifida with hydrocephalus, Q05.3 — Sacral spina bifida with hydrocephalus, Q05.4 — Unspecified spina bifida with hydrocephalus, Q05.5 — Cervical spina bifida without hydrocephalus, Q05.6 — Thoracic spina bifida without hydrocephalus, Q05.7 — Lumbar spina bifida without hydrocephalus, Q05.8 — Sacral spina bifida without hydrocephalus, Q05.9 — Spina bifida, unspecified, Q06.1 — Hypoplasia and dysplasia of spinal cord, Q06.2 — Diastematomyelia, Q06.3 — Other congenital cauda equina malformations, Q06.4 — Hydromyelia, Q06.8 — Other specified congenital malformations of spinal cord, Q06.9 — Congenital malformation of spinal cord, unspecified, Q07.00 — Arnold-Chiari syndrome without spina bifida or hydrocephalus, Q07.01 — Arnold-Chiari syndrome with spina bifida, Q07.02 — Arnold-Chiari syndrome with hydrocephalus, Q07.03 — Arnold-Chiari syndrome with spina bifida and hydrocephalus, +230 more
Related risk categories
These categories interact through CMS's HCC hierarchy — one can suppress the other's risk-adjustment weight when both are present on a claim.
Quadriplegia, Paraplegia
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Nervous system congenital anomalies).
Q05.0 — Cervical spina bifida with hydrocephalus, Q05.1 — Thoracic spina bifida with hydrocephalus, Q05.2 — Lumbar spina bifida with hydrocephalus, Q05.3 — Sacral spina bifida with hydrocephalus, Q05.4 — Unspecified spina bifida with hydrocephalus, Q05.5 — Cervical spina bifida without hydrocephalus, Q05.6 — Thoracic spina bifida without hydrocephalus, Q05.7 — Lumbar spina bifida without hydrocephalus, Q05.8 — Sacral spina bifida without hydrocephalus, Q05.9 — Spina bifida, unspecified, Q06.1 — Hypoplasia and dysplasia of spinal cord, Q06.2 — Diastematomyelia, Q06.3 — Other congenital cauda equina malformations, Q06.4 — Hydromyelia, Q06.8 — Other specified congenital malformations of spinal cord, Q06.9 — Congenital malformation of spinal cord, unspecified, Q07.00 — Arnold-Chiari syndrome without spina bifida or hydrocephalus, Q07.01 — Arnold-Chiari syndrome with spina bifida, Q07.02 — Arnold-Chiari syndrome with hydrocephalus, Q07.03 — Arnold-Chiari syndrome with spina bifida and hydrocephalus, +29 more
Same Index main term, other category
The ICD-10-CM Index to Diseases and Injuries files this code under the main term “Agenesis”; these codes share that main term but sit in a different category of the Tabular List.
E03.1 — Congenital hypothyroidism without goiter (thyroid), M26.09 — Other specified anomalies of jaw size (jaw), Q00.0 — Anencephaly (brain), Q02 — Microcephaly (skull, with, microcephaly), Q03.9 — Congenital hydrocephalus, unspecified (skull, with, hydrocephalus), Q04.0 — Congenital malformations of corpus callosum (corpus callosum), Q04.3 — Other reduction deformities of brain (cerebellum), Q07.8 — Other specified congenital malformations of nervous system (nerve), Q10.3 — Other congenital malformations of eyelid (cilia), Q10.4 — Absence and agenesis of lacrimal apparatus (punctum lacrimale), Q11.1 — Other anophthalmos (eye), Q12.3 — Congenital aphakia (lens), Q13.1 — Absence of iris (iris), Q15.8 — Other specified congenital malformations of eye (eye, adnexa), Q16.0 — Congenital absence of (ear) auricle (auricle), Q16.1 — Congenital absence, atresia and stricture of auditory canal (external) (auditory), Q16.2 — Absence of eustachian tube (eustachian tube), Q16.3 — Congenital malformation of ear ossicles (incus), Q16.5 — Congenital malformation of inner ear (organ, of Corti), Q16.9 — Congenital malformation of ear causing impairment of hearing, unspecified (ear), +94 more
Contextual Map
Every relationship of Q06.0 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Hierarchy
- Q00-QA1 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-QA1) (Q00-QA1)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q00-Q07 — Congenital malformations of the nervous system[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Clinical classification (CCSR)
- MAL004 — Nervous system congenital anomalies[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
Risk adjustment (CMS-HCC)
- HCC 182 — Spinal Cord Disorders/Injuries [CMS-HCC]— CMS-HCC V28 · 2026
MS-DRG Grouper
- DRG 091 — OTHER DISORDERS OF NERVOUS SYSTEM WITH MCC[MS-DRG]: “OTHER DISORDERS OF NERVOUS SYSTEM WITH MCC (MDC 01)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 092 — OTHER DISORDERS OF NERVOUS SYSTEM WITH CC[MS-DRG]: “OTHER DISORDERS OF NERVOUS SYSTEM WITH CC (MDC 01)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 093 — OTHER DISORDERS OF NERVOUS SYSTEM WITHOUT CC/MCC[MS-DRG]: “OTHER DISORDERS OF NERVOUS SYSTEM WITHOUT CC/MCC (MDC 01)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 791 — PREMATURITY WITH MAJOR PROBLEMS[MS-DRG]: “PREMATURITY WITH MAJOR PROBLEMS (MDC 15)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
- DRG 793 — FULL TERM NEONATE WITH MAJOR PROBLEMS[MS-DRG]: “FULL TERM NEONATE WITH MAJOR PROBLEMS (MDC 15)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
MDC crossing
- MDC 01 — Diseases and Disorders of the Nervous System[MDC crossing]: “Diseases and Disorders of the Nervous System — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 8,892 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026
- MDC 15 — Newborns and Other Neonates with Conditions Originating in Perinatal Period[MDC crossing]: “Newborns and Other Neonates with Conditions Originating in Perinatal Period — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs.”— CMS MS-DRG Definitions Manual · FY2026
Index entries
- Agenesis, spinal cord[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
- Amyelia[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
Nearest codes
- Q06 — Other congenital malformations of spinal cord[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q06.1 — Hypoplasia and dysplasia of spinal cord[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q06.2 — Diastematomyelia[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q06.3 — Other congenital cauda equina malformations[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q06.4 — Hydromyelia[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q06.8 — Other specified congenital malformations of spinal cord[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- Q06.9 — Congenital malformation of spinal cord, unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Change history
- FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
- Inpatient payment groups Official source data
- CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
- Risk adjustment Official source data
- 2026 Mid-Year Final ICD-10 Mappings + Model Software (cms.gov/files/zip/2026-midyear-final-icd-10-mappings.zip, 2026-midyear-final-model-software.zip) — CMS-HCC V28, PY2026 mid-year final release Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder structured relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "Q06.0 — Amyelia." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/q06.0-amyelia
Change history
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionAmyelia
No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027 (effective October 1, 2026), and none are recorded for this code. Note changes are tracked from FY2027 only.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q06.0 in its code family, with their registry titles.
- Q06 — Other congenital malformations of spinal cord
- Q06.1 — Hypoplasia and dysplasia of spinal cord
- Q06.2 — Diastematomyelia
- Q06.3 — Other congenital cauda equina malformations
- Q06.4 — Hydromyelia
- Q06.8 — Other specified congenital malformations of spinal cord
- Q06.9 — Congenital malformation of spinal cord, unspecified