Immunity disorders
CCSR category BLD008 · 85 ICD-10-CM codes
Code Families in This Category
- D89 Other disorders involving the immune mechanism, not elsewhere classified · 24
- D81 Combined immunodeficiencies · 18
- D86 Sarcoidosis · 13
- D80 Immunodeficiency with predominantly antibody defects · 10
- D84 Other immunodeficiencies · 8
- D82 Immunodeficiency associated with other major defects · 7
- D83 Common variable immunodeficiency · 5
ICD-10-CM Codes in This Category (85)
- D80.0 — Hereditary hypogammaglobulinemia
- D80.1 — Nonfamilial hypogammaglobulinemia
- D80.2 — Selective deficiency of immunoglobulin A [IgA]
- D80.3 — Selective deficiency of immunoglobulin G [IgG] subclasses
- D80.4 — Selective deficiency of immunoglobulin M [IgM]
- D80.5 — Immunodeficiency with increased immunoglobulin M [IgM]
- D80.6 — Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
- D80.7 — Transient hypogammaglobulinemia of infancy
- D80.8 — Other immunodeficiencies with predominantly antibody defects
- D80.9 — Immunodeficiency with predominantly antibody defects, unspecified
- D81.0 — Severe combined immunodeficiency [SCID] with reticular dysgenesis
- D81.1 — Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
- D81.2 — Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
- D81.3 — Adenosine deaminase [ADA] deficiency
- D81.30 — Adenosine deaminase deficiency, unspecified
- D81.31 — Severe combined immunodeficiency due to adenosine deaminase deficiency
- D81.32 — Adenosine deaminase 2 deficiency
- D81.39 — Other adenosine deaminase deficiency
- D81.4 — Nezelof's syndrome
- D81.5 — Purine nucleoside phosphorylase [PNP] deficiency
- D81.6 — Major histocompatibility complex class I deficiency
- D81.7 — Major histocompatibility complex class II deficiency
- D81.810 — Biotinidase deficiency
- D81.818 — Other biotin-dependent carboxylase deficiency
- D81.819 — Biotin-dependent carboxylase deficiency, unspecified
- D81.82 — Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
- D81.89 — Other combined immunodeficiencies
- D81.9 — Combined immunodeficiency, unspecified
- D82.0 — Wiskott-Aldrich syndrome
- D82.1 — Di George's syndrome
- D82.2 — Immunodeficiency with short-limbed stature
- D82.3 — Immunodeficiency following hereditary defective response to Epstein-Barr virus
- D82.4 — Hyperimmunoglobulin E [IgE] syndrome
- D82.8 — Immunodeficiency associated with other specified major defects
- D82.9 — Immunodeficiency associated with major defect, unspecified
- D83.0 — Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function
- D83.1 — Common variable immunodeficiency with predominant immunoregulatory T-cell disorders
- D83.2 — Common variable immunodeficiency with autoantibodies to B- or T-cells
- D83.8 — Other common variable immunodeficiencies
- D83.9 — Common variable immunodeficiency, unspecified
- D84.0 — Lymphocyte function antigen-1 [LFA-1] defect
- D84.1 — Defects in the complement system
- D84.8 — Other specified immunodeficiencies
- D84.81 — Immunodeficiency due to conditions classified elsewhere
- D84.821 — Immunodeficiency due to drugs
- D84.822 — Immunodeficiency due to external causes
- D84.89 — Other immunodeficiencies
- D84.9 — Immunodeficiency, unspecified
- D86.0 — Sarcoidosis of lung
- D86.1 — Sarcoidosis of lymph nodes
- D86.2 — Sarcoidosis of lung with sarcoidosis of lymph nodes
- D86.3 — Sarcoidosis of skin
- D86.81 — Sarcoid meningitis
- D86.82 — Multiple cranial nerve palsies in sarcoidosis
- D86.83 — Sarcoid iridocyclitis
- D86.84 — Sarcoid pyelonephritis
- D86.85 — Sarcoid myocarditis
- D86.86 — Sarcoid arthropathy
- D86.87 — Sarcoid myositis
- D86.89 — Sarcoidosis of other sites
- D86.9 — Sarcoidosis, unspecified
- D89.0 — Polyclonal hypergammaglobulinemia
- D89.1 — Cryoglobulinemia
- D89.2 — Hypergammaglobulinemia, unspecified
- D89.3 — Immune reconstitution syndrome
- D89.40 — Mast cell activation, unspecified
- D89.41 — Monoclonal mast cell activation syndrome
- D89.42 — Idiopathic mast cell activation syndrome
- D89.43 — Secondary mast cell activation
- D89.44 — Hereditary alpha tryptasemia
- D89.49 — Other mast cell activation disorder
- D89.810 — Acute graft-versus-host disease
- D89.811 — Chronic graft-versus-host disease
- D89.812 — Acute on chronic graft-versus-host disease
- D89.813 — Graft-versus-host disease, unspecified
- D89.82 — Autoimmune lymphoproliferative syndrome [ALPS]
- D89.831 — Cytokine release syndrome, grade 1
- D89.832 — Cytokine release syndrome, grade 2
- D89.833 — Cytokine release syndrome, grade 3
- D89.834 — Cytokine release syndrome, grade 4
- D89.835 — Cytokine release syndrome, grade 5
- D89.839 — Cytokine release syndrome, grade unspecified
- D89.84 — IgG4-related disease
- D89.89 — Other specified disorders involving the immune mechanism, not elsewhere classified
- D89.9 — Disorder involving the immune mechanism, unspecified
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, Rockville, MD. All data sources.