Q22.1 ICD-10-CM Code: Congenital pulmonary valve stenosis
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Inpatient Payment Groups (MS-DRG)
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0 (FY2026), Appendix B.
- MS-DRG 306 — CARDIAC CONGENITAL AND VALVULAR DISORDERS WITH MCC (MDC 05)
- MS-DRG 307 — CARDIAC CONGENITAL AND VALVULAR DISORDERS WITHOUT MCC (MDC 05)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Code Set: Valid FY2026 and FY2027. FY2026 took effect October 1, 2025.
Official Registry Overview & Definition
Congenital pulmonary valve stenosis is a billable ICD-10-CM diagnosis code (Q22.1).
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q22.1 in its code family, with their registry titles.
- Q22 — Congenital malformations of pulmonary and tricuspid valves
- Q22.0 — Pulmonary valve atresia
- Q22.2 — Congenital pulmonary valve insufficiency
- Q22.3 — Other congenital malformations of pulmonary valve
- Q22.4 — Congenital tricuspid stenosis
- Q22.5 — Ebstein's anomaly
- Q22.6 — Hypoplastic right heart syndrome
- Q22.8 — Other congenital malformations of tricuspid valve
- Q22.9 — Congenital malformation of tricuspid valve, unspecified
Indexed Clinical Terms (10)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Anomaly, anomalous (congenital) (unspecified type), heart, valve NEC, pulmonary, stenosis
- Anomaly, anomalous (congenital) (unspecified type), pulmonary, valve, stenosis
- Fusion, fused (congenital), cusps, heart valve NEC, pulmonary
- Fusion, fused (congenital), pulmonic cusps
- Stenosis, stenotic (cicatricial), pulmonary (artery) (congenital), valve, congenital
- Stenosis, stenotic (cicatricial), pulmonic (congenital)
- Stenosis, stenotic (cicatricial), valve (cardiac) (heart), congenital, pulmonary
- Stricture, heart, valve, pulmonary
- Stricture, pulmonary, pulmonic, valve, congenital
- Stricture, valve (cardiac) (heart), congenital, pulmonary