E74.00 is the authoritative medical code for Glycogen storage disease, unspecified. This classification is used in medical billing and clinical recording to specify the clinical criteria for glycogen storage disease, unspecified (ICD-10-CM E74.00), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Glycogen storage disease, unspecified is a billable ICD-10-CM diagnosis code E74.00. Excludes1 (not coded here): diabetes mellitus E08-E13; hypoglycemia NOS E16.2; increased secretion of glucagon E16.3; mucopolysaccharidosis E76.0-E76.3; androgen insensitivity syndrome E34.5-; congenital adrenal hyperplasia E25.0; hemolytic anemias attributable to enzyme disorders D55.-; Marfan syndrome Q87.4-; 5-alpha-reductase deficiency E29.1. Excludes2 (not included here): Ehlers-Danlos syndromes Q79.6-.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for E74.00 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- diabetes mellitus E08-E13
- hypoglycemia NOS E16.2
- increased secretion of glucagon E16.3
- mucopolysaccharidosis E76.0-E76.3
- androgen insensitivity syndrome E34.5-
- congenital adrenal hyperplasia E25.0
- hemolytic anemias attributable to enzyme disorders D55.-
- Marfan syndrome Q87.4-
- 5-alpha-reductase deficiency E29.1
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- Ehlers-Danlos syndromes Q79.6-
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with E74.00?
Per official ICD-10-CM Excludes1 instructions, E74.00 must not be reported together with: diabetes mellitus (E08-E13); hypoglycemia NOS (E16.2); increased secretion of glucagon (E16.3); mucopolysaccharidosis (E76.0-E76.3).
Can E74.00 be reported alongside related conditions?
Per official ICD-10-CM Excludes2 instructions, E74.00 and the following are not considered part of each other and may both be reported when both conditions are present: Ehlers-Danlos syndromes (Q79.6-).
Nearest Codes in This Family
Official ICD-10-CM classifications closest to E74.00 in its code family, with their registry titles.
- E74 — Other disorders of carbohydrate metabolism
- E74.0 — Glycogen storage disease
- E74.01 — von Gierke disease
- E74.02 — Pompe disease
- E74.03 — Cori disease
- E74.04 — McArdle disease
- E74.05 — Lysosome-associated membrane protein 2 [LAMP2] deficiency
- E74.09 — Other glycogen storage disease
- E74.1 — Disorders of fructose metabolism
- E74.10 — Disorder of fructose metabolism, unspecified
View all 31 codes in the E74 family
Indexed Clinical Terms (6)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Aglycogenosis
- Disease, diseased, glycogen storage
- Disease, diseased, glycogen storage, generalized
- Disorder (of), tubulo-interstitial (in), glycogen storage disease
- Myopathy, in (due to), glycogen storage disease
- Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic), tubulo-interstitial (in), due to, glycogen storage disease